Structural interplay of KV7.1 and KCNE1 is essential for normal repolarization and is compromised in short QT syndrome 2 (KV7.1-A287T).

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Published in HeartRhythm Case Rep on September 12, 2016

Authors

Ina Rothenberg1, Ilaria Piccini1, Eva Wrobel1, Birgit Stallmeyer1, Jovanca Müller1, Boris Greber2,3, Nathalie Strutz-Seebohm1, Eric Schulze-Bahr1,4, Nicole Schmitt5, Guiscard Seebohm1,4

Author Affiliations

1: Institute for Genetics of Heart Diseases (IfGH), Department of Cardiovascular Medicine, University Hospital Münster, Münster, Germany.
2: Human Stem Cell Pluripotency Laboratory, Max Planck Institute for Molecular Biomedicine, Münster, Germany.
3: Chemical Genomics Centre of the Max Planck Society, Dortmund, Germany.
4: Interdisziplinäres Zentrum für Klinische Forschung Münster (IZKF Münster) and Innovative Medizinische Forschung (IMF Münster), Faculty of Medicine, University of Münster, Münster, Germany.
5: Danish National Research Foundation Centre for Cardiac Arrhythmia, Department of Biomedical Sciences, University of Copenhagen, Copenhagen, Denmark.

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