Published in Lancet on November 09, 1985
The sclera, the prion, and the ophthalmologist. Br J Ophthalmol (2002) 1.72
Creutzfeldt-Jakob disease and blood transfusion. BMJ (1991) 1.61
Bovine spongiform encephalopathy and Creutzfeldt-Jakob disease: implications for physicians. CMAJ (1996) 1.57
Follicular dendritic cells and dissemination of Creutzfeldt-Jakob disease. J Virol (2000) 1.32
Is Creutzfeldt-Jakob disease transmitted in blood? Emerg Infect Dis (1997) 1.19
Virus-like interference in the latency and prevention of Creutzfeldt-Jakob disease. Proc Natl Acad Sci U S A (2003) 1.02
Neuroinvasion by a Creutzfeldt-Jakob disease agent in the absence of B cells and follicular dendritic cells. Proc Natl Acad Sci U S A (2001) 0.99
Re-assessment of PrP(Sc) distribution in sporadic and variant CJD. PLoS One (2013) 0.92
Retention of corneal epithelial cells following Goldmann tonometry: implications for CJD risk. Br J Ophthalmol (2003) 0.87
Variant CJD and tonometry. Br J Ophthalmol (2004) 0.77
Formic acid pretreatment enhances immunostaining of cerebral and systemic amyloids. Lab Invest (1987) 4.98
Beta-protein amyloid is widely distributed in the central nervous system of patients with Alzheimer's disease. Am J Pathol (1989) 2.61
Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome. Biochem Biophys Res Commun (1989) 2.35
Transmission of chronic spongiform encephalopathy with kuru plaques from humans to small rodents. Ann Neurol (1979) 2.01
Vascular variant of prion protein cerebral amyloidosis with tau-positive neurofibrillary tangles: the phenotype of the stop codon 145 mutation in PRNP. Proc Natl Acad Sci U S A (1996) 1.94
Abnormal isoform of prion protein accumulates in follicular dendritic cells in mice with Creutzfeldt-Jakob disease. J Virol (1991) 1.90
Abnormal isoform of prion proteins accumulates in the synaptic structures of the central nervous system in patients with Creutzfeldt-Jakob disease. Am J Pathol (1992) 1.86
Amyloid plaques in Creutzfeldt-Jakob disease stain with prion protein antibodies. Ann Neurol (1986) 1.85
Typing prion isoforms. Nature (1997) 1.82
Hydrated autoclave pretreatment enhances tau immunoreactivity in formalin-fixed normal and Alzheimer's disease brain tissues. Lab Invest (1991) 1.78
Diagnostic criteria for sporadic Creutzfeldt-Jakob disease. Arch Neurol (1996) 1.66
The sequential development of abnormal prion protein accumulation in mice with Creutzfeldt-Jakob disease. Am J Pathol (1992) 1.66
An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques. Biochem Biophys Res Commun (1993) 1.63
Creutzfeldt-Jakob disease with florid plaques after cadaveric dural graft in a Japanese woman. Lancet (1997) 1.60
Morphometric comparison of the vulnerability of peripheral motor and sensory neurons in amyotrophic lateral sclerosis. J Neuropathol Exp Neurol (1981) 1.59
Immunohistochemical confirmation of Creutzfeldt-Jakob disease with a long clinical course with amyloid plaque core antibodies. Am J Pathol (1988) 1.52
Accumulation of alpha B-crystallin in central nervous system glia and neurons in pathologic conditions. Am J Pathol (1992) 1.46
Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome. Biochem Biophys Res Commun (1993) 1.43
Rosenthal fibers share epitopes with alpha B-crystallin, glial fibrillary acidic protein, and ubiquitin, but not with vimentin. Immunoelectron microscopy with colloidal gold. Am J Pathol (1991) 1.42
Sequence heterogeneity of HTLV-I proviral DNA in the central nervous system of patients with HTLV-I-associated myelopathy. Ann Neurol (1994) 1.38
Codon 219 Lys allele of PRNP is not found in sporadic Creutzfeldt-Jakob disease. Ann Neurol (1998) 1.37
Experimental transmission of human subacute spongiform encephalopathy to small rodents. I. Clinical and histological observations. Acta Neuropathol (1980) 1.31
Formalin fixed brains are useful for magnetic resonance imaging (MRI) study. J Neurol Sci (1987) 1.29
Organ distribution of proteinase-resistant prion protein in humans and mice with Creutzfeldt-Jakob disease. J Gen Virol (1989) 1.24
Amyloid plaques in the brains of mice with Creutzfeldt-Jakob disease. Ann Neurol (1984) 1.23
N-terminal sequence of prion protein is also integrated into kuru plaques in patients with Gerstmann-Sträussler syndrome. Brain Res (1991) 1.23
Immunoblotting of Creutzfeldt-Jakob disease prion proteins: host species-specific epitopes. Ann Neurol (1987) 1.22
Mitochondrial encephalomyopathy with lactate-pyruvate elevation and brain infarctions. Neurology (1984) 1.21
Human prion diseases with variant prion protein. Philos Trans R Soc Lond B Biol Sci (1994) 1.21
The original Gerstmann-Sträussler-Scheinker family of Austria: divergent clinicopathological phenotypes but constant PrP genotype. Brain Pathol (1995) 1.19
Presence of HTLV-I proviral DNA in central nervous system of patients with HTLV-I-associated myelopathy. Ann Neurol (1992) 1.18
Increased tau accumulation in senile plaques as a hallmark in Alzheimer's disease. Am J Pathol (1989) 1.16
CJD discrepancy. Nature (1991) 1.16
Ferritin immunohistochemistry as a marker for microglia. Acta Neuropathol (1989) 1.15
Alpha B-crystallin and 27-kd heat shock protein are regulated by stress conditions in the central nervous system and accumulate in Rosenthal fibers. Am J Pathol (1993) 1.14
A new inherited prion disease (PrP-P105L mutation) showing spastic paraparesis. Ann Neurol (1993) 1.10
Protective prion protein polymorphisms against sporadic Creutzfeldt-Jakob disease. Lancet (1998) 1.09
Experimental transmission of human subacute spongiform encephalopathy to small rodents. III. Further transmission from three patients and distribution patterns of lesions in mice. Acta Neuropathol (1981) 1.09
Neuronal autophagy in experimental Creutzfeldt-Jakob's disease. Acta Neuropathol (1989) 1.05
Alzheimer's amyloid precursor protein accumulates within axonal swellings in human brain lesions. Neurosci Lett (1992) 1.05
Distinctive immunohistochemical profiles of small heat shock proteins (heat shock protein 27 and alpha B-crystallin) in human brain tumors. Cancer (1996) 1.01
Increased senile plaques without microglia in Alzheimer's disease. Acta Neuropathol (1991) 1.00
Creutzfeldt-Jakob disease patients with congophilic kuru plaques have the missense variant prion protein common to Gerstmann-Sträussler syndrome. Ann Neurol (1990) 1.00
Aging and cerebral amyloid: early detection of amyloid in the human brain using biochemical extraction and immunostain. J Gerontol (1988) 0.99
New variant prion protein in a Japanese family with Gerstmann-Sträussler syndrome. Brain Res Mol Brain Res (1995) 0.99
A new method to classify amyloid fibril proteins. Acta Neuropathol (1985) 0.98
A prion protein missense variant is integrated in kuru plaque cores in patients with Gerstmann-Sträussler syndrome. Neurology (1991) 0.97
Spinal cord multiple sclerosis lesions in Japanese patients: Schwann cell remyelination occurs in areas that lack glial fibrillary acidic protein (GFAP). Acta Neuropathol (1985) 0.96
Humanized prion protein knock-in by Cre-induced site-specific recombination in the mouse. Biochem Biophys Res Commun (1996) 0.96
Positive transmission of Creutzfeldt-Jakob disease verified by murine kuru plaques. Lab Invest (1989) 0.96
Colocalization of prion protein and beta protein in the same amyloid plaques in patients with Gerstmann-Sträussler syndrome. Acta Neuropathol (1992) 0.96
Sense and antisense modification of glial alpha B-crystallin production results in alterations of stress fiber formation and thermoresistance. J Cell Biol (1994) 0.95
Properties of the transmissible agent derived from chronic spongiform encephalopathy. Ann Neurol (1980) 0.95
The primary structure of the prion protein influences the distribution of abnormal prion protein in the central nervous system. Am J Pathol (1992) 0.94
Accumulation of alpha B-crystallin in brains of patients with Alexander's disease is not due to an abnormality of the 5'-flanking and coding sequence of the genomic DNA. Neurosci Lett (1992) 0.94
Japanese family with Creutzfeldt-Jakob disease with codon 200 point mutation of the prion protein gene. Neurology (1994) 0.94
Immunohistochemical demonstration of alphaB-crystallin in hamartomas of tuberous sclerosis. Am J Pathol (1991) 0.93
Accumulation of abnormal prion protein in mice infected with Creutzfeldt-Jakob disease via intraperitoneal route: a sequential study. Am J Pathol (1993) 0.92
Chordoma in early childhood: a clinicopathological study. Neurosurgery (1991) 0.92
Morphogenesis of amyloid plaques in mice with Creutzfeldt-Jakob disease. Acta Neuropathol (1985) 0.92
MIB1 staining index and scoring of histologic features in meningioma. Indicators for the prediction of biologic potential and postoperative management. Cancer (1994) 0.92
Expression of neurofibromatosis 2 protein in human brain tumors: an immunohistochemical study. Acta Neuropathol (1997) 0.91
[Atypical Alzheimer's disease--an autopsy case]. No To Shinkei (1976) 0.91
Experimental transmission of human subacute spongiform encephalopathy to small rodents. II. Ultrastructural study of spongy state in the gray and white matter. Acta Neuropathol (1980) 0.91
Host genetic control of incubation periods of Creutzfeldt-Jakob disease in mice. J Gen Virol (1989) 0.91
[The pathology of the peripheral nervous system in two autopsy cases of osteosclerotic myeloma associated with polyneuropathy, skin hyperpigmentation, hypertrichosis and edema (author's transl)]. Rinsho Shinkeigaku (1980) 0.91
Prion disease with 144 base pair insertion in a Japanese family line. Acta Neuropathol (1995) 0.90
A comparative immunohistochemical study of Kuru and senile plaques with a special reference to glial reactions at various stages of amyloid plaque formation. Am J Pathol (1991) 0.90
Parvalbumin-immunoreactive neurons in the human central nervous system are decreased in Alzheimer's disease. Acta Neuropathol (1991) 0.90
A morphometric study of myelinated fibers in the fifth lumbar ventral roots in patients with cerebrovascular diseases. Clin Neuropathol (1988) 0.90
Successful transmission of Creutzfeldt-Jakob disease from human to mouse verified by prion protein accumulation in mouse brains. Brain Res (1992) 0.90
Creutzfeldt-Jakob disease with codon 129 polymorphism (valine): a comparative study of patients with codon 102 point mutation or without mutations. Acta Neuropathol (1992) 0.90
Clinical course of patients with coronary ectasia. Cardiology (1999) 0.90
Adrenoleukodystrophy with olivopontocerebellar atrophy-like lesions. Clin Neuropathol (1986) 0.89
Amyloid beta-protein (Abeta) 1-40 but not Abeta1-42 contributes to the experimental formation of Alzheimer disease amyloid fibrils in rat brain. J Neurosci (1997) 0.89
The presence of complements in amyloid plaques of Creutzfeldt-Jakob disease and Gerstmann-Straussler-Scheinker disease. Appl Pathol (1984) 0.87
Ventricular and subarachnoid seeding of intracranial tumors of neuroectodermal origin--a study of 26 consecutive autopsy cases with reference to focal ependymal defect. Clin Neuropathol (1982) 0.86
Hemangiopericytoma of the meninges: a clinicopathologic and immunohistochemical study. Clin Neuropathol (1989) 0.86
Massive accumulation of modified tau and severe depletion of normal tau characterize the cerebral cortex and white matter of Alzheimer's disease. Demonstration using the hydrated autoclaving method. Am J Pathol (1992) 0.86
Lack of effect of thymus and spleen on the incubation period of Creutzfeldt-Jakob disease in mice. J Gen Virol (1987) 0.85
A missense mutation at codon 105 with codon 129 polymorphism of the prion protein gene in a new variant of Gerstmann-Sträussler-Scheinker disease. Neurology (1993) 0.85
Radial component of central myelin in shiverer mouse. Brain Res (1983) 0.85
Scrapie-associated fibrils (SAF) purification method yields amyloid proteins from systemic and cerebral amyloidosis. Biosci Rep (1986) 0.85
[Mutation of codon 117 of the prion gene in Gerstmann-Sträussler-Scheinker disease]. Rev Neurol (Paris) (1991) 0.85
A variant of Gerstmann-Sträussler-Scheinker disease carrying codon 105 mutation with codon 129 polymorphism of the prion protein gene: a clinicopathological study. J Neurol Sci (1994) 0.85
A missense mutation in the proteolipid protein gene responsible for Pelizaeus-Merzbacher disease in a Japanese family. Hum Mol Genet (1993) 0.85
Advanced glycosylation end-products and heat shock proteins accumulate in the basophilic degeneration of the myocardium and the corpora amylacea of the glia. Pathol Int (1996) 0.84
Immunohistochemical verification of senile and kuru plaques in Creutzfeldt-Jakob disease and the allied disease. Ann Neurol (1988) 0.84
Apolipoprotein E mRNA in the brains of patients with Alzheimer's disease. J Neurol Sci (1995) 0.84
Accumulation of neurofilaments in a sporadic case of amyotrophic lateral sclerosis. Jpn J Psychiatry Neurol (1986) 0.84
Transient expression of glial fibrillary acidic protein in developing oligodendrocytes in vitro. Brain Res (1985) 0.84
Mutation in the prion protein gene at codon 232 in Japanese patients with Creutzfeldt-Jakob disease: a clinicopathological, immunohistochemical and transmission study. Acta Neuropathol (1996) 0.84
The coexistence of Alzheimer's disease and Creutzfeldt-Jakob disease in a patient with dementia of long duration. Acta Neuropathol (1992) 0.83
Immunoreactivity of cerebral amyloidosis is enhanced by protein denaturation treatments. Acta Neuropathol (1991) 0.83
Experimental transmission of human subacute spongiform encephalopathy to small rodents. IV. Positive transmission from a typical case of Gerstmann-Sträussler-Scheinker's disease. Acta Neuropathol (1984) 0.83
Morphometric evaluation of degenerative and regenerative changes in isoniazid-induced neuropathy. Acta Neuropathol (1983) 0.83
Immunohistochemical distribution of amyloid precursor protein during normal rat development. Brain Res Dev Brain Res (1993) 0.83
Atypical multiple sclerosis with concentric or lamellar demyelinated lesions: two Japanese patients studied post mortem. Ann Neurol (1985) 0.83
Marchiafava-Bignami disease, striatal degeneration, and other neurological complications of chronic alcoholism in a Japanese. Acta Neuropathol (1981) 0.83