Published in Biochem Biophys Res Commun on March 15, 1993
Cholesterol depletion and modification of COOH-terminal targeting sequence of the prion protein inhibit formation of the scrapie isoform. J Cell Biol (1995) 3.66
Fatal familial insomnia and familial Creutzfeldt-Jakob disease: different prion proteins determined by a DNA polymorphism. Proc Natl Acad Sci U S A (1994) 1.85
Etiology and pathogenesis of prion diseases. Am J Pathol (1995) 1.35
Humanized knock-in mice expressing chimeric prion protein showed varied susceptibility to different human prions. Am J Pathol (2003) 1.16
SUT-2 potentiates tau-induced neurotoxicity in Caenorhabditis elegans. Hum Mol Genet (2009) 1.16
Pathogenic mutations in the hydrophobic core of the human prion protein can promote structural instability and misfolding. J Mol Biol (2010) 1.08
Prion fibrillization is mediated by a native structural element that comprises helices H2 and H3. J Biol Chem (2010) 1.00
Experimental verification of a traceback phenomenon in prion infection. J Virol (2010) 0.96
Relationships between clinicopathological features and cerebrospinal fluid biomarkers in Japanese patients with genetic prion diseases. PLoS One (2013) 0.90
Genetic studies in human prion diseases. J Korean Med Sci (2014) 0.90
Evidence that the 127-164 region of prion proteins has two equi-energetic conformations with beta or alpha features. Biophys J (2001) 0.90
The prion protein gene in humans revisited: lessons from a worldwide resequencing study. Genome Res (2005) 0.89
Inherited Creutzfeldt-Jakob disease in a British family associated with a novel 144 base pair insertion of the prion protein gene. J Neurol Neurosurg Psychiatry (1995) 0.88
Ovine reference materials and assays for prion genetic testing. BMC Vet Res (2010) 0.88
Two different clinical phenotypes of Creutzfeldt-Jakob disease with a M232R substitution. J Neurol (2007) 0.86
Clinical features of genetic Creutzfeldt-Jakob disease with V180I mutation in the prion protein gene. BMJ Open (2014) 0.85
Deciphering the pathogenesis of sporadic Creutzfeldt-Jakob disease with codon 129 M/V and type 2 abnormal prion protein. Acta Neuropathol Commun (2013) 0.85
Multicentre multiobserver study of diffusion-weighted and fluid-attenuated inversion recovery MRI for the diagnosis of sporadic Creutzfeldt-Jakob disease: a reliability and agreement study. BMJ Open (2012) 0.83
Pathogenic mutations in the glycosylphosphatidylinositol signal peptide of PrP modulate its topology in neuroblastoma cells. Mol Cell Neurosci (2008) 0.83
Transmission properties of atypical Creutzfeldt-Jakob disease: a clue to disease etiology? J Virol (2015) 0.81
Co-occurrence of types 1 and 2 PrP(res) in sporadic Creutzfeldt-Jakob disease MM1. Am J Pathol (2011) 0.81
Probing the role of structural features of mouse PrP in yeast by expression as Sup35-PrP fusions. Prion (2012) 0.79
The structure of human prions: from biology to structural models-considerations and pitfalls. Viruses (2014) 0.78
Neurodegeneration in humans caused by prions. West J Med (1994) 0.77
Characterization of variant Creutzfeldt-Jakob disease prions in prion protein-humanized mice carrying distinct codon 129 genotypes. J Biol Chem (2013) 0.77
Species barrier prevents an abnormal isoform of prion protein from accumulating in follicular dendritic cells of mice with Creutzfeldt-Jakob disease. J Virol (1993) 0.76
A Japanese family with a variant of Gerstmann-Sträussler-Scheinker disease. J Neurol Neurosurg Psychiatry (1997) 0.76
Increased interleukin-17 in the cerebrospinal fluid in sporadic Creutzfeldt-Jakob disease: a case-control study of rapidly progressive dementia. J Neuroinflammation (2013) 0.76
Hereditary Human Prion Diseases: an Update. Mol Neurobiol (2016) 0.76
Distinctive properties of plaque-type dura mater graft-associated Creutzfeldt-Jakob disease in cell-protein misfolding cyclic amplification. Lab Invest (2016) 0.76
Systematic investigation of predicted effect of nonsynonymous SNPs in human prion protein gene: a molecular modeling and molecular dynamics study. J Biomol Struct Dyn (2013) 0.75
Genomic Characteristics of Genetic Creutzfeldt-Jakob Disease Patients with V180I Mutation and Associations with Other Neurodegenerative Disorders. PLoS One (2016) 0.75
Molecular characterization of an enterobacterial metallo beta-lactamase found in a clinical isolate of Serratia marcescens that shows imipenem resistance. Antimicrob Agents Chemother (1994) 8.64
PCR detection of metallo-beta-lactamase gene (blaIMP) in gram-negative rods resistant to broad-spectrum beta-lactams. J Clin Microbiol (1996) 6.68
A novel integron-like element carrying the metallo-beta-lactamase gene blaIMP. Antimicrob Agents Chemother (1995) 6.00
Chromosomal beta-lactamase of Klebsiella oxytoca, a new class A enzyme that hydrolyzes broad-spectrum beta-lactam antibiotics. Antimicrob Agents Chemother (1989) 5.98
Multifocal outbreaks of metallo-beta-lactamase-producing Pseudomonas aeruginosa resistant to broad-spectrum beta-lactams, including carbapenems. Antimicrob Agents Chemother (1996) 5.36
Close evolutionary relationship between the chromosomally encoded beta-lactamase gene of Klebsiella pneumoniae and the TEM beta-lactamase gene mediated by R plasmids. FEBS Lett (1986) 5.13
Formic acid pretreatment enhances immunostaining of cerebral and systemic amyloids. Lab Invest (1987) 4.98
Arabidopsis ethylene-responsive element binding factors act as transcriptional activators or repressors of GCC box-mediated gene expression. Plant Cell (2000) 4.78
Plasmid-mediated dissemination of the metallo-beta-lactamase gene blaIMP among clinically isolated strains of Serratia marcescens. Antimicrob Agents Chemother (1995) 4.71
Metastasis suppressor gene KiSS-1 encodes peptide ligand of a G-protein-coupled receptor. Nature (2001) 4.55
Genomic DNA fingerprinting by pulsed-field gel electrophoresis as an epidemiological marker for study of nosocomial infections caused by methicillin-resistant Staphylococcus aureus. J Clin Microbiol (1991) 4.33
Direct neural fate specification from embryonic stem cells: a primitive mammalian neural stem cell stage acquired through a default mechanism. Neuron (2001) 3.42
Plasmid-mediated AmpC-type beta-lactamase isolated from Klebsiella pneumoniae confers resistance to broad-spectrum beta-lactams, including moxalactam. Antimicrob Agents Chemother (1993) 3.19
Characterization of a plasmid-borne and constitutively expressed blaMOX-1 gene encoding AmpC-type beta-lactamase. Gene (1994) 3.08
Chronic inflammatory polyradiculoneuropathy. Mayo Clin Proc (1975) 3.01
Virulence for mice of Klebsiella strains belonging to the O1 group: relationship to their capsular (K) types. Infect Immun (1983) 2.93
Diffusion-weighted MRI abnormalities as an early diagnostic marker for Creutzfeldt-Jakob disease. Neurology (2004) 2.76
Beta-protein amyloid is widely distributed in the central nervous system of patients with Alzheimer's disease. Am J Pathol (1989) 2.61
Genomic organization of the Klebsiella pneumoniae cps region responsible for serotype K2 capsular polysaccharide synthesis in the virulent strain Chedid. J Bacteriol (1995) 2.47
Fhit, a putative tumor suppressor in humans, is a dinucleoside 5',5"'-P1,P3-triphosphate hydrolase. Biochemistry (1996) 2.46
Inclusion of the transcervical approach in video-assisted thoracoscopic extended thymectomy (VATET) for myasthenia gravis: a prospective trial. Surg Endosc (2006) 2.39
The FHIT gene 3p14.2 is abnormal in lung cancer. Cell (1996) 2.36
Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome. Biochem Biophys Res Commun (1989) 2.35
New neuropeptides containing carboxy-terminal RFamide and their receptor in mammals. Nat Cell Biol (2000) 2.05
Preferential activation of different I waves by transcranial magnetic stimulation with a figure-of-eight-shaped coil. Exp Brain Res (1997) 2.03
Transmission of chronic spongiform encephalopathy with kuru plaques from humans to small rodents. Ann Neurol (1979) 2.01
Campylobacter fetus subspecies fetus cellulitis associated with bacteremia in debilitated hosts. Clin Infect Dis (1998) 2.01
Trehalose sensitivity in Drosophila correlates with mutations in and expression of the gustatory receptor gene Gr5a. Curr Biol (2001) 1.99
Paired-pulse magnetic stimulation of the human motor cortex: differences among I waves. J Physiol (1998) 1.96
A novel dodecadepsipeptide, cereulide, is an emetic toxin of Bacillus cereus. FEMS Microbiol Lett (1995) 1.95
Vascular variant of prion protein cerebral amyloidosis with tau-positive neurofibrillary tangles: the phenotype of the stop codon 145 mutation in PRNP. Proc Natl Acad Sci U S A (1996) 1.94
Abnormal isoform of prion protein accumulates in follicular dendritic cells in mice with Creutzfeldt-Jakob disease. J Virol (1991) 1.90
Abnormal isoform of prion proteins accumulates in the synaptic structures of the central nervous system in patients with Creutzfeldt-Jakob disease. Am J Pathol (1992) 1.86
Amyloid plaques in Creutzfeldt-Jakob disease stain with prion protein antibodies. Ann Neurol (1986) 1.85
Nosocomial spread of cephem-resistant Escherichia coli strains carrying multiple Toho-1-like beta-lactamase genes. Antimicrob Agents Chemother (1997) 1.84
Typing prion isoforms. Nature (1997) 1.82
FHIT gene alterations in head and neck squamous cell carcinomas. Proc Natl Acad Sci U S A (1996) 1.80
Hydrated autoclave pretreatment enhances tau immunoreactivity in formalin-fixed normal and Alzheimer's disease brain tissues. Lab Invest (1991) 1.78
Structure and expression of the human FHIT gene in normal and tumor cells. Cancer Res (1997) 1.76
The FHIT gene at 3p14.2 is abnormal in breast carcinomas. Cancer Res (1996) 1.75
Effect of fluoride concentration and pH on corrosion behavior of titanium for dental use. J Dent Res (1999) 1.75
Fine-needle aspiration cytologic technique for lung cancer has a high potential of malignant cell spread through the tract. Chest (2000) 1.69
Defenestration of the sinusoidal endothelial cell in a rat model of cirrhosis. Hepatology (1993) 1.67
The sequential development of abnormal prion protein accumulation in mice with Creutzfeldt-Jakob disease. Am J Pathol (1992) 1.66
Diagnostic criteria for sporadic Creutzfeldt-Jakob disease. Arch Neurol (1996) 1.66
Aging reactions in a low gold, white dental alloy. J Dent Res (1982) 1.64
An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques. Biochem Biophys Res Commun (1993) 1.63
Magnetic stimulation over the cerebellum in humans. Ann Neurol (1995) 1.61
Identification of species and capsular types of Klebsiella clinical isolates, with special reference to Klebsiella planticola. Microbiol Immunol (1989) 1.60
Creutzfeldt-Jakob disease with florid plaques after cadaveric dural graft in a Japanese woman. Lancet (1997) 1.60
Morphometric comparison of the vulnerability of peripheral motor and sensory neurons in amyotrophic lateral sclerosis. J Neuropathol Exp Neurol (1981) 1.59
Linkage and association of febrile seizures to the IMPA2 gene on human chromosome 18. Neurology (2004) 1.57
Role of multiple efflux pumps in Escherichia coli in indole expulsion. FEMS Microbiol Lett (1999) 1.54
Immunohistochemical confirmation of Creutzfeldt-Jakob disease with a long clinical course with amyloid plaque core antibodies. Am J Pathol (1988) 1.52
Foveal translocation with scleral imbrication in patients with myopic neovascular maculopathy. Am J Ophthalmol (2001) 1.52
Laparoscopic splenectomy. Am J Surg (1994) 1.52
Recurrent brief episodes with psychotic features in adolescence: periodic psychosis of puberty revisited. Br J Psychiatry (1995) 1.50
Strongyloidiasis associated with nephrotic syndrome. Intern Med (1998) 1.49
Ca(2+)-desensitizing effect of a deletion mutation Delta K210 in cardiac troponin T that causes familial dilated cardiomyopathy. Proc Natl Acad Sci U S A (2002) 1.49
Effects of endoscopic injection sclerotherapy on portal hypertensive gastropathy: a prospective study. Gastrointest Endosc (1992) 1.49
Metabolism of trichothecene mycotoxins. I. Microsomal deacetylation of T-2 toxin in animal tissues. J Biochem (1977) 1.49
The nucleotide sequence of cDNA for a Drosophila ribosomal protein with homology to rat ribosomal protein S26. Nucleic Acids Res (1989) 1.48
The bceT gene of Bacillus cereus encodes an enterotoxic protein. Microbiology (1995) 1.47
Dietary patterns and depressive symptoms among Japanese men and women. Eur J Clin Nutr (2010) 1.46
Accumulation of alpha B-crystallin in central nervous system glia and neurons in pathologic conditions. Am J Pathol (1992) 1.46
Transmission of Creutzfeldt-Jakob disease from human blood and urine into mice. Lancet (1985) 1.46
Effect of pH on activities of novel beta-lactamases and beta-lactamase inhibitors against these beta-lactamases. Antimicrob Agents Chemother (1995) 1.46
Antineuronal antibody in Sjögren's syndrome masquerading as paraneoplastic cerebellar degeneration. Lancet (1994) 1.44
DNA ploidy pattern of each carcinomatous component in adenosquamous lung carcinoma. Ann Thorac Surg (1993) 1.44
Glial fibrillary acidic protein in medulloblastoma. Acta Neuropathol (1981) 1.44
Rosenthal fibers share epitopes with alpha B-crystallin, glial fibrillary acidic protein, and ubiquitin, but not with vimentin. Immunoelectron microscopy with colloidal gold. Am J Pathol (1991) 1.42
Intracortical inhibition of the motor cortex is normal in chorea. J Neurol Neurosurg Psychiatry (1999) 1.41
MuSK antibodies in AChR Ab-seropositive MG vs AChR Ab-seronegative MG. Neurology (2004) 1.40
Sequence heterogeneity of HTLV-I proviral DNA in the central nervous system of patients with HTLV-I-associated myelopathy. Ann Neurol (1994) 1.38
Cerebroventricular infusion of pentosan polysulphate in human variant Creutzfeldt-Jakob disease. J Infect (2005) 1.38
SPECT in focal enterovirus encephalitis: evidence for local cerebral vasculitis. Pediatr Neurol (2000) 1.38
False lumens in type III aortic dissections: progress CT study. Radiology (1985) 1.38
Codon 219 Lys allele of PRNP is not found in sporadic Creutzfeldt-Jakob disease. Ann Neurol (1998) 1.37
Vascular anatomy of duodenal varices: angiographic and histopathological assessments. Am J Gastroenterol (1993) 1.36
Positions of chromosome 3p14.2 fragile sites (FRA3B) within the FHIT gene. Cancer Res (1997) 1.35
Purification and partial characterization of a type-specific antigen of Rickettsia tsutsugamushi. Infect Immun (1989) 1.34
Partial deletion of the cloned rfb gene of Escherichia coli O9 results in synthesis of a new O-antigenic lipopolysaccharide. J Bacteriol (1989) 1.34
Polyneuritic amyloidosis in a Japanese family. Arch Neurol (1968) 1.34
Intraperitoneal hyperthermic perfusion combined with surgery effective for gastric cancer patients with peritoneal seeding. Ann Surg (1988) 1.33
A novel dodecadepsipeptide, cereulide, isolated from Bacillus cereus causes vacuole formation in HEp-2 cells. FEMS Microbiol Lett (1994) 1.33
Molecular characterization of type-specific capsular polysaccharide biosynthesis genes of Streptococcus agalactiae type Ia. J Bacteriol (1999) 1.32
Experimental transmission of human subacute spongiform encephalopathy to small rodents. I. Clinical and histological observations. Acta Neuropathol (1980) 1.31
Reproducibility of haemodynamical simulations in a subject-specific stented aneurysm model--a report on the Virtual Intracranial Stenting Challenge 2007. J Biomech (2008) 1.30
Formalin fixed brains are useful for magnetic resonance imaging (MRI) study. J Neurol Sci (1987) 1.29
Metabolism of trichothecene mycotoxins. II. Substrate specificity of microsomal deacetylation of trichothecenes. J Biochem (1978) 1.29
Interleukin-8 activity correlates with histological severity in Helicobacter pylori-associated antral gastritis. Am J Gastroenterol (1996) 1.28
IR and NMR analyses of hardening and maturation of glass-ionomer cement. J Dent Res (1996) 1.28
Genomic organization of the human amyloid beta-protein precursor gene. Gene (1990) 1.28
Laparoscopic hepatic resection for hepatocellular carcinoma. Surg Endosc (1995) 1.27
Interhemispheric facilitation of the hand motor area in humans. J Physiol (2001) 1.26
A novel gene required for rhamnose-glucose polysaccharide synthesis in Streptococcus mutans. J Bacteriol (1999) 1.26