Published in Annu Rev Biochem on January 01, 1988
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Multiple deletions of the osmolyte transporters BetL, Gbu, and OpuC of Listeria monocytogenes affect virulence and growth at high osmolarity. Appl Environ Microbiol (2002) 1.46
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An ATP-dependent L-carnitine transporter in Listeria monocytogenes Scott A is involved in osmoprotection. J Bacteriol (1995) 1.36
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A postgenomic appraisal of osmotolerance in Listeria monocytogenes. Appl Environ Microbiol (2003) 1.26
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Disease-associated mutation in SRSF2 misregulates splicing by altering RNA-binding affinities. Proc Natl Acad Sci U S A (2015) 0.91
Peroxisomal fatty acid oxidation and inhibitors of the mitochondrial carnitine palmitoyltransferase I in isolated rat hepatocytes. Biochem J (1992) 0.91
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Proteinase treatment of intact hepatic mitochondria has differential effects on inhibition of carnitine palmitoyltransferase by different inhibitors. Biochem J (1992) 0.87
Comparison of the active sites of the purified carnitine acyltransferases from peroxisomes and mitochondria by using a reaction-intermediate analogue. Biochem J (1993) 0.87
Cholate extracts of mitochondrial outer membranes increase inhibition by malonyl-CoA of carnitine palmitoyltransferase-I by a mechanism involving phospholipids. Biochem J (1994) 0.87
Defects in activation and transport of fatty acids. J Inherit Metab Dis (1999) 0.87
The facC gene of Aspergillus nidulans encodes an acetate-inducible carnitine acetyltransferase. J Bacteriol (1998) 0.87
Carnitine and carnitine acetyltransferases in the yeast Saccharomyces cerevisiae: a role for carnitine in stress protection. Curr Genet (2008) 0.86
Cloning and characterization of murine carnitine acetyltransferase: evidence for a requirement during cell cycle progression. Biochem J (1997) 0.86
Serum carnitine as an independent biomarker of malnutrition in patients with impaired oral intake. J Clin Biochem Nutr (2014) 0.85
Crystal structures of murine carnitine acetyltransferase in ternary complexes with its substrates. J Biol Chem (2006) 0.84
Expression of novel isoforms of carnitine palmitoyltransferase I (CPT-1) generated by alternative splicing of the CPT-ibeta gene. Biochem J (1998) 0.84
Molecular analysis of carnitine palmitoyltransferase II deficiency with hepatocardiomuscular expression. Am J Hum Genet (1996) 0.84
Crystal structure of rat carnitine palmitoyltransferase II (CPT-II). Biochem Biophys Res Commun (2006) 0.84
Muscle carnitine acetyltransferase and carnitine deficiency in a case of mitochondrial encephalomyopathy. J Inherit Metab Dis (1999) 0.84
Changes of plasma fasting carnitine ester profile in patients with ulcerative colitis. World J Gastroenterol (2006) 0.83
Inhibition by etomoxir of rat liver carnitine octanoyltransferase is produced through the co-ordinate interaction with two histidine residues. Biochem J (2000) 0.83
Measurement of the rates of acetyl-CoA hydrolysis and synthesis from acetate in rat hepatocytes and the role of these fluxes in substrate cycling. Biochem J (1990) 0.81
Grape seed extract (Vitis vinifera) partially reverses high fat diet-induced obesity in C57BL/6J mice. Nutr Res Pract (2008) 0.81
Plasma carnitine ester profile in adult celiac disease patients maintained on long-term gluten free diet. World J Gastroenterol (2005) 0.81
Abbreviated half-lives and impaired fuel utilization in carnitine palmitoyltransferase II variant fibroblasts. PLoS One (2015) 0.80
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Plasma carnitine ester profile in homozygous and heterozygous OCTN2 deficiency. J Inherit Metab Dis (2009) 0.79
Cloning, sequencing and heterologous expression of a cDNA encoding pigeon liver carnitine acetyltransferase. Biochem J (1995) 0.79
Characterisation of carnitine palmitoyltransferases in patients with a carnitine palmitoyltransferase deficiency: implications for diagnosis and therapy. J Neurol Neurosurg Psychiatry (1997) 0.79
Carnitine in bacterial physiology and metabolism. Microbiology (2015) 0.78
Effect of membrane environment on the activity and inhibitability by malonyl-CoA of the carnitine acyltransferase of hepatic microsomal membranes. Biochem J (1997) 0.77
Mitochondrial ATP synthase subunit c stored in hereditary ceroid-lipofuscinosis contains trimethyl-lysine. Biochem J (1995) 0.77
Pea chloroplast carnitine acetyltransferase. Proc Biol Sci (2000) 0.77
Molecular mechanisms of statin intolerance. Arch Med Sci (2016) 0.77
L-carnitine alleviates sciatic nerve crush injury in rats: functional and electron microscopy assessments. Neural Regen Res (2014) 0.77
Isothermal titration calorimetry with micelles: Thermodynamics of inhibitor binding to carnitine palmitoyltransferase 2 membrane protein. FEBS Open Bio (2013) 0.77
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Metabolic Pathway Signatures Associated with Urinary Metabolite Biomarkers Differentiate Bladder Cancer Patients from Healthy Controls. Yonsei Med J (2016) 0.77
Effect of carboxylic acid xenobiotics and their metabolites on the activity of carnitine acyltransferases. Biochem J (1991) 0.77
Active sites residues of beef liver carnitine octanoyltransferase (COT) and carnitine palmitoyltransferase (CPT-II). Biochem J (1998) 0.77
Ca2+-induced accumulation of pyrophosphate in mitochondria during acetate metabolism. Biochem J (1989) 0.77
Carnitine transport and fatty acid oxidation. Biochim Biophys Acta (2016) 0.76
The effect of L-carnitine on oxidative stress responses of experimental contrast-induced nephropathy in rats. J Vet Med Sci (2013) 0.76
Opposing effects of ketamine and acetyl l-carnitine on the serotonergic system of zebrafish. Neurosci Lett (2015) 0.76
Strategies of bacterial over expression of membrane transporters relevant in human health: the successful case of the three members of OCTN subfamily. Mol Biotechnol (2013) 0.76
Metabolic engineering for high yielding L(-)-carnitine production in Escherichia coli. Microb Cell Fact (2013) 0.76
Distinct effects of ketamine and acetyl l-carnitine on the dopamine system in zebrafish. Neurotoxicol Teratol (2016) 0.76
Systemic regulation of L-carnitine in nutritional metabolism in zebrafish, Danio rerio. Sci Rep (2017) 0.75
Mitigation of statins-induced cytotoxicity and mitochondrial dysfunction by L-carnitine in freshly-isolated rat hepatocytes. Res Pharm Sci (2015) 0.75
l-carnitine as a Potential Additive in Blood Storage Solutions: A Study on Erythrocytes. Indian J Hematol Blood Transfus (2015) 0.75
Carnitine palmitoyltransferase in human erythrocyte membrane. Properties and malonyl-CoA sensitivity. Biochem J (1991) 0.75
Requirements for Carnitine Shuttle-Mediated Translocation of Mitochondrial Acetyl Moieties to the Yeast Cytosol. MBio (2016) 0.75
Compartmentation of Metabolism of the C12-, C9-, and C5-n-dicarboxylates in Rat Liver, Investigated by Mass Isotopomer Analysis: ANAPLEROSIS FROM DODECANEDIOATE. J Biol Chem (2015) 0.75
Serum Levels of Acyl-Carnitines along the Continuum from Normal to Alzheimer's Dementia. PLoS One (2016) 0.75
Alterations in the carnitine cycle in a mouse model of Rett syndrome. Sci Rep (2017) 0.75
Inheritance of the S113L mutation within an inbred family with carnitine palmitoyltransferase enzyme deficiency. Hum Genet (1996) 0.75
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Quantitation of CoASH and acyl-CoA. Anal Biochem (1992) 0.77