Published in Muscle Nerve on August 01, 1988
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Sustained dystrophin expression induced by peptide-conjugated morpholino oligomers in the muscles of mdx mice. Mol Ther (2008) 2.69
The lipid phosphatase myotubularin is essential for skeletal muscle maintenance but not for myogenesis in mice. Proc Natl Acad Sci U S A (2002) 1.91
Increased calcium entry into dystrophin-deficient muscle fibres of MDX and ADR-MDX mice is reduced by ion channel blockers. J Physiol (1999) 1.47
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Therapeutic potential of proteasome inhibition in Duchenne and Becker muscular dystrophies. Am J Pathol (2010) 1.14
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Contractile properties of skinned muscle fibres from young and adult normal and dystrophic (mdx) mice. J Physiol (1993) 0.97
Peroxisome proliferator-activated receptor γ coactivator1- gene α transfer restores mitochondrial biomass and improves mitochondrial calcium handling in post-necrotic mdx mouse skeletal muscle. J Physiol (2012) 0.92
Temporal changes in magnetic resonance imaging in the mdx mouse. BMC Res Notes (2013) 0.91
Protein turnover is elevated in muscle of mdx mice in vivo. Biochem J (1990) 0.90
Increased sphingosine-1-phosphate improves muscle regeneration in acutely injured mdx mice. Skelet Muscle (2013) 0.88
Exercise training improves plantar flexor muscle function in mdx mice. Med Sci Sports Exerc (2012) 0.87
New method for determining total calcium content in tissue applied to skeletal muscle with and without calsequestrin. J Gen Physiol (2015) 0.87
Myogenin regulates exercise capacity but is dispensable for skeletal muscle regeneration in adult mdx mice. PLoS One (2011) 0.85
Transgenic expression of Laminin α1 chain does not prevent muscle disease in the mdx mouse model for Duchenne muscular dystrophy. Am J Pathol (2011) 0.84
Serum cholinesterases are differentially regulated in normal and dystrophin-deficient mutant mice. Front Mol Neurosci (2012) 0.83
Intracellular energetic units in healthy and diseased hearts. Exp Clin Cardiol (2005) 0.80
Expression of the glucose transporter GLUT4 in the muscular dystrophic mdx mouse. Biochem J (1993) 0.79
Metabogenic and Nutriceutical Approaches to Address Energy Dysregulation and Skeletal Muscle Wasting in Duchenne Muscular Dystrophy. Nutrients (2015) 0.77
Pre- and postsynaptic changes in the neuromuscular junction in dystrophic mice. Front Physiol (2015) 0.77
Suite of Clinically Relevant Functional Assays to Address Therapeutic Efficacy and Disease Mechanism in the Dystrophic mdx Mouse. J Appl Physiol (1985) (2016) 0.75
Abnormalities in brain structure and biochemistry associated with mdx mice measured by in vivo MRI and high resolution localized (1)H MRS. Neuromuscul Disord (2015) 0.75
The molecular basis for Duchenne versus Becker muscular dystrophy: correlation of severity with type of deletion. Am J Hum Genet (1989) 5.09
Analysis of deletions in DNA from patients with Becker and Duchenne muscular dystrophy. Nature (1986) 4.13
Prenatal diagnosis and carrier detection of Duchenne muscular dystrophy with closely linked RFLPs. Lancet (1985) 3.08
Mitochondrial calcium overload: A general mechanism for cell-necrosis in muscle diseases. Lancet (1976) 2.22
Anti-DNA antibodies bind directly to renal antigens and induce kidney dysfunction in the isolated perfused rat kidney. J Immunol (1989) 1.86
Mesenteric panniculitis: review of the leterature and presentation of cases. Surgery (1977) 1.83
Prostaglandin and thromboxane synthesis in a pure macrophage population and the inhibition, by E-type prostaglandins, of chemiluminescence. FEBS Lett (1978) 1.55
Low serum C3, leukopenia, and thrombocytopenia: unusual features of henoch-schonlein purpura. Eur J Pediatr (1999) 1.50
Comparison of the segregation of the RYR1 C1840T mutation with segregation of the caffeine/halothane contracture test results for malignant hyperthermia susceptibility in a large Manitoba Mennonite family. Anesthesiology (1996) 1.48
Regional localization of 18 human X-linked DNA sequences. Cytogenet Cell Genet (1986) 1.48
Lupus anti-DNA autoantibodies cross-react with a glomerular structural protein: a case for tissue injury by molecular mimicry. Eur J Immunol (2001) 1.46
Bilateral pulmonary artery aneurysms in Behçet's disease. Eur Respir J (1993) 1.45
Endobronchial actinomycosis simulating bronchogenic carcinoma. Diagnosis by bronchial biopsy. Chest (1991) 1.44
Postpartum renal failure in systemic lupus erythematosus. Clin Nephrol (1990) 1.39
Dual challenge for glomerular damage in mice: uninephrectomy and repetitive pregnancies. Isr J Med Sci (1990) 1.37
Nephrotic syndrome associated with amyloid-like glomerular deposits. Nephron (1977) 1.33
Idiopathic infantile arterial calcification: a case report and review of the literature. Eur J Pediatr (1984) 1.32
Identical mutation in patients with limb girdle muscular dystrophy type 2B or Miyoshi myopathy suggests a role for modifier gene(s). Hum Mol Genet (1999) 1.31
Identical dysferlin mutation in limb-girdle muscular dystrophy type 2B and distal myopathy. Neurology (2000) 1.25
Secondary reduction in calpain 3 expression in patients with limb girdle muscular dystrophy type 2B and Miyoshi myopathy (primary dysferlinopathies). Neuromuscul Disord (2000) 1.22
Limb-girdle muscular dystrophy and Miyoshi myopathy in an aboriginal Canadian kindred map to LGMD2B and segregate with the same haplotype. Am J Hum Genet (1996) 1.20
Renal pathologic findings associated with monoclonal gammopathies. Arch Intern Med (1975) 1.19
Chromatin-positive Klinefelter's syndrome with undetectable peripheral FSH levels. Am J Med (1975) 1.16
Recombinations in individuals homozygous by descent localize the Friedreich ataxia locus in a cloned 450-kb interval. Am J Hum Genet (1994) 1.14
Fatal late postpartum intravascular coagulation with acute renal failure. Am J Med Sci (1969) 1.10
Segregation analysis of a marker localised Xp21.2-Xp21.3 in Duchenne and Becker muscular dystrophy families. Hum Genet (1985) 1.09
DNA studies in a family with Duchenne muscular dystrophy and a deletion at Xp21. Am J Hum Genet (1987) 1.08
Three years' experience with neonatal screening for Duchenne/Becker muscular dystrophy: gene analysis, gene expression, and phenotype prediction. Am J Med Genet (1991) 1.03
Chemiluminescence and immune cell activation. I. Early activation of rat thymocytes can be monitored by chemiluminescence measurements. Eur J Immunol (1978) 1.02
Multipoint genetic mapping of the Xq26-q28 region in families with fragile X mental retardation and in normal families reveals tight linkage of markers in q26-q27. Hum Genet (1987) 1.00
Renal manifestations in recurrent polyserositis (familial Mediterranean fever). Isr J Med Sci (1970) 0.98
Gene studies in newborn males with Duchenne muscular dystrophy detected by neonatal screening. Lancet (1988) 0.97
Isolation of atypical mycobacteria from human sources and the effect of cortisone on their pathogenicity in mice. Isr J Med Sci (1967) 0.96
A gene for autosomal recessive limb-girdle muscular dystrophy in Manitoba Hutterites maps to chromosome region 9q31-q33: evidence for another limb-girdle muscular dystrophy locus. Am J Hum Genet (1998) 0.94
Inhibitory effects of alcohol on intestinal amino acid transport in vivo and in vitro. J Nutr (1968) 0.94
Merkel cell tumor masquerading as granulation tissue on a teenager's toe. Am J Dermatopathol (1992) 0.93
Chemiluminescence and immune cell activation. II. Enhancement of concanavalin A-induced chemiluminescence following in vitro preincubation of rat thymocytes; dependency on macrophage-lymphocyte interaction. Eur J Immunol (1980) 0.92
Extramedullary hematopoietic tumors of the cranial dura mater. Acta Haematol (1969) 0.92
Pseudodeficiency of alpha-galactosidase A. Clin Genet (1982) 0.91
Female sex hormone and nephropathy in Cohen diabetic rat (genetically selected sucrose-fed). Horm Metab Res (1984) 0.91
Acquired glomerulocystic kidney disease following haemolytic-uraemic syndrome. Pediatr Nephrol (1995) 0.91
The femur, fibula, ulna (FFU) complex in siblings. Clin Genet (1983) 0.90
Spontaneous and experimental myocarditis: the effect of Freund's adjuvant on the heart and other organs. Br J Exp Pathol (1966) 0.90
Inflammatory fibroid polyp of the small intestine: report of two cases and review of the literature. Isr J Med Sci (1983) 0.90
Kidney involvement in systemic lupus erythematosus and Fabry's disease. Nephron (1983) 0.89
Value of radiography in the management of possible fishbone ingestion. Ann Otol Rhinol Laryngol (1995) 0.89
Renal vein thrombosis in the adult: a clinical and pathologic study based on renal biopsies. Medicine (Baltimore) (1968) 0.89
Rhabdomyolysis and acute renal failure induced by paraphenylenediamine. Hum Toxicol (1989) 0.89
A calcium-associated magnesium-responsive defect of respiration and oxidative phosphorylation by skeletal muscle mitochondria of BIO 14.6 dystrophic hamsters. Life Sci II (1970) 0.89
The 56/58 kDa androgen-binding protein in male genital skin fibroblasts with a deleted androgen receptor gene. Mol Cell Endocrinol (1991) 0.88
Mycobacterium marinum skin infections mimicking cutaneous leishmaniasis. Br J Dermatol (1976) 0.88
The Friedreich ataxia region: characterization of two novel genes and reduction of the critical region to 300 kb. Hum Mol Genet (1994) 0.88
Ectopic functioning adrenocortico-myelolipoma in longstanding Nelson's syndrome. Clin Endocrinol (Oxf) (1979) 0.87
Impact of genetic counselling after neonatal screening for Duchenne muscular dystrophy. J Med Genet (1993) 0.87
p53 expression in patients with cirrhosis with and without hepatocellular carcinoma. Cancer (1995) 0.87
Rectal mucosal biopsy in aganglionosis and allied conditions. Hum Pathol (1983) 0.87
Mitochondrial calcium overloading in cardiomyopathic hamsters. J Mol Cell Cardiol (1978) 0.86
Experimental allergic sialoadenitis. VI. Prevention by antihistamine and induction by intraductal instillation of performed immune complexes. Virchows Arch A Pathol Pathol Anat (1973) 0.85
The iron-loaded gerbil model revisited: effects of deferoxamine and deferiprone treatment. J Lab Clin Med (2002) 0.85
Familial renal tubular dysgenesis: a disorder not isolated to proximal convoluted tubules. Pediatr Pathol Lab Med (1996) 0.85
Concanavalin A-induced chemiluminescence in rat thymus lymphocytes. Its origin and role in mitogenesis. Biochem J (1981) 0.85
Amber mutation creates a diagnostic MaeI site in the androgen receptor gene of a family with complete androgen insensitivity. Am J Med Genet (1991) 0.85
Excretion of alpha-foetoprotein in the urine of pregnant rats and hepatoma-bearing animals. Br J Cancer (1973) 0.84
Dysferlin expression after normal myoblast transplantation in SCID and in SJL mice. Neuromuscul Disord (2002) 0.84
Limb girdle muscular dystrophy in Manitoba Hutterites does not map to any of the known LGMD loci. Am J Med Genet (1997) 0.84
Successful treatment of autoimmune manifestations in MRL/l and MRL/n mice using total lymphoid irradiation (TLI). Exp Mol Pathol (1983) 0.84
Alpha-fetoprotein and liver cell proliferation in rats fed choline-deficient diet. Z Ernahrungswiss (1976) 0.83
Proteinuria in the rat: a comparison of tissue components in the voided and renal pelvic urine. Experientia (1969) 0.83
Proliferative glomerulopathy in rheumatic heart disease and chronic lung disease. Am J Med Sci (1972) 0.83
Leiomyomatous hamartosis with congenital jejunoileal atresia. Isr J Med Sci (1980) 0.83
Rectal biopsy as a diagnostic aid in periarteritis nodosa. Isr J Med Sci (1971) 0.83
The role of hypovolemic stress in the production of fat embolism in rabbits. 1. Morphologic alterations of the lungs. Chest (1976) 0.82
Oxidative phosphorylation by muscle mitochondria of dysstrophic mice. Can J Biochem (1967) 0.82
Experimental allergic sialoadenitis. 3. Acute parotitis induced by instillation of antiserum to rat plasma into the glandular duct of rats. Experientia (1972) 0.82
Male sex hormone and nephropathy in Cohen diabetic rat. (Genetically selected sucrose fed). Diabete Metab (1984) 0.82
On the mechanism of a calcium-associated defect of oxidative phosphorylation in progessive muscular dystrophy. Arch Biochem Biophys (1973) 0.82
Oxidative phosphorylation in smooth muscle. Am J Physiol (1970) 0.82
The 56 kDa androgen binding protein is an aldehyde dehydrogenase. Biochem Biophys Res Commun (1991) 0.82
Primary lymphoma of the ovary. A case report and critical review of the literature. Eur J Gynaecol Oncol (1995) 0.82
Urinary excretion of liver antigens in experimental hepatic diseases of the rat. Lab Invest (1971) 0.82
Correlation of selective angiography and pathology in cavernous hemangioma of the kidney. J Urol (1976) 0.82
Effect of the estrogen antagonist, tamoxifen, on development of glomerulosclerosis in the Cohen diabetic rat. Diabetes (1985) 0.82
Effects of enalapril, losartan, and verapamil on blood pressure and glucose metabolism in the Cohen-Rosenthal diabetic hypertensive rat. Hypertension (1997) 0.81
Biochemical investigations in cultured skin fibroblasts from patients with Duchenne muscular dystrophy. Clin Genet (1978) 0.81
Auto-delayed-type hypersensitivity induced in immunodeficient mice with syngeneic modified self-antigens. II. Suppressor T cells control the autoimmune response. Scand J Immunol (1984) 0.81
Isoproterenol induced myocardial lesions in the immunized and non-immunized rat. II. Histopathological lesions after specific immunization. Immunology (1966) 0.81
Crohn's disease isolated to the appendix: truths and fallacies. Hum Pathol (1986) 0.81
Nephropathy in sucrose-fed rats. Electron and light microscopic studies. Diabetes (1971) 0.81
Osteoclast-like giant cell tumour of the urinary bladder. Histopathology (1990) 0.81
Glomerular involvement in storage diseases. J Pathol (1973) 0.81
Oxidative phosphorylation in cardiomyopathic hamsters. Am J Physiol (1972) 0.81
Diffuse intercapillary glomerulosclerosis in sucrose-fed rats. Diabetologia (1971) 0.81
Leu-676-Pro mutation of the androgen receptor causes complete androgen insensitivity syndrome in a large Hutterite kindred. Hum Mutat (1995) 0.81
Liver dysfunction in measles, liver biopsy findings. Dig Dis Sci (1986) 0.81
Osteoid osteoma presenting as an osteocartilaginous exostosis. Isr J Med Sci (1981) 0.80
Changes from high potassium (hk) to low potassium (lk) in bovine red cells. J Gen Physiol (1972) 0.80
Experimental allergic sialoadenitis. I. Acute sialoadenitis induced by a local immune reaction. Virchows Arch A Pathol Pathol Anat (1972) 0.80