Published in Thorax on July 01, 1987
Effects of social class, sex, and region of residence on age at death from cystic fibrosis. BMJ (1989) 3.50
Association between socioeconomic status, sex, and age at death from cystic fibrosis in England and Wales (1959 to 2008): cross sectional study. BMJ (2011) 2.10
Partial splenectomy in cystic fibrosis patients with hypersplenism. Arch Dis Child (2003) 2.02
Managing adults with cystic fibrosis. BMJ (1989) 1.83
Medium term treatment of stable stage cystic fibrosis with recombinant human DNase I. Thorax (1995) 1.72
The chest radiograph in cystic fibrosis: a new scoring system compared with the Chrispin-Norman and Brasfield scores. Thorax (1994) 1.58
Exercise testing and prognosis in adult cystic fibrosis. Thorax (1997) 1.12
In vivo effects of recombinant human DNase I on sputum in patients with cystic fibrosis. Thorax (1996) 1.09
Psychosocial functioning of young adults with cystic fibrosis and their families. Thorax (1994) 1.09
Life threatening haemoptysis in cystic fibrosis: an alternative therapeutic approach. Thorax (1990) 1.07
Individualised unsupervised exercise training in adults with cystic fibrosis: a 1 year randomised controlled trial. Thorax (2004) 1.06
Decreased polymorphonuclear leucocyte chemotactic response to leukotriene B4 in cystic fibrosis. Clin Exp Immunol (1992) 0.99
Glucose tolerance in cystic fibrosis. Arch Dis Child (1991) 0.98
Cough in adult cystic fibrosis: diagnosis and response to fundoplication. Cough (2009) 0.96
Cystic fibrosis: channel, catalytic, and folding properties of the CFTR protein. J Bioenerg Biomembr (1997) 0.94
Management of severe haemoptysis by bronchial artery embolisation in a patient with cystic fibrosis. Thorax (1989) 0.88
Rheumatoid factors in cystic fibrosis: associations with disease manifestations and recurrent bacterial infections. Clin Exp Immunol (1989) 0.84
Role of heat shock proteins in the pathogenesis of cystic fibrosis arthritis. Thorax (1997) 0.83
A novel Pseudomonas aeruginosa bacteriophage, Ab31, a chimera formed from temperate phage PAJU2 and P. putida lytic phage AF: characteristics and mechanism of bacterial resistance. PLoS One (2014) 0.82
Genetic and clinical features of patients with cystic fibrosis diagnosed after the age of 16 years. Thorax (1995) 0.82
Cystic fibrosis in a 70 year old woman. Thorax (1992) 0.80
INO-4995 therapeutic efficacy is enhanced with repeat dosing in cystic fibrosis knockout mice and human epithelia. Am J Respir Cell Mol Biol (2009) 0.79
Heart-lung transplantation for end-stage respiratory disease in cystic fibrosis patients. J R Soc Med (1993) 0.75
Heart-lung transplantation for cystic fibrosis. BMJ (1992) 0.75
Survival of patients with cystic fibrosis. BMJ (1989) 0.75
Microparticles for inhalational delivery of antipseudomonal antibiotics. AAPS J (2008) 0.75
A test for concentration of electrolytes in sweat in cystic fibrosis of the pancreas utilizing pilocarpine by iontophoresis. Pediatrics (1959) 12.04
Cystic fibrosis. Am Rev Respir Dis (1976) 6.62
Cystic fibrosis in adults. 75 cases and a review of 232 cases in the literature. Am J Med (1979) 3.54
Partial preservation of pancreatic beta-cell function in children with diabetes. Lancet (1981) 3.07
Cystic fibrosis: a new outlook. 70 patients above 25 years of age. Medicine (Baltimore) (1977) 2.01
Management of pneumothorax in adults with cystic fibrosis. Thorax (1982) 1.99
Cystic fibrosis of the pancreas in adolescence and adulthood. Australas Ann Med (1969) 1.89
Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption. J Pediatr (1982) 1.64
Cystic fibrosis in adolescents and adults. Q J Med (1976) 1.52
Newly diagnosed cystic fibrosis in middle and later life. Thorax (1985) 1.30
Lingual lipase: an important lipase in the digestion of dietary lipids in cystic fibrosis? Pediatr Res (1980) 1.27
Obstructive azoospermia as a diagnostic criterion for the cystic fibrosis syndrome. Lancet (1982) 1.02
Adult cystic fibrosis: postprandial response of gut regulatory peptides. Gastroenterology (1983) 1.01
RAMPs regulate the transport and ligand specificity of the calcitonin-receptor-like receptor. Nature (1998) 5.98
Heterodimerization is required for the formation of a functional GABA(B) receptor. Nature (1998) 5.59
Effect of aerosol propellants and surfactants on airway resistance. Thorax (1969) 3.66
Liposome-mediated CFTR gene transfer to the nasal epithelium of patients with cystic fibrosis. Nat Med (1995) 3.61
Identification of the cystic fibrosis gene. BMJ (1990) 3.28
Independent genetic determinants of pancreatic and pulmonary status in cystic fibrosis. Lancet (1990) 3.27
Antibiotic therapy against Pseudomonas aeruginosa in cystic fibrosis: a European consensus. Eur Respir J (2000) 3.14
Q fever endocarditis treated with trimethoprim and sulphamethoxazole. Br Med J (1972) 3.06
Aerosol carbenicillin and gentamicin treatment of Pseudomonas aeruginosa infection in patients with cystic fibrosis. Lancet (1981) 2.87
Liver disease and bile duct abnormalities in adults with cystic fibrosis. Lancet (1989) 2.76
The relationship of phenotype changes in Pseudomonas aeruginosa to the clinical condition of patients with cystic fibrosis. Am Rev Respir Dis (1983) 2.68
High-dose beclomethasone inhaler in the treatment of asthma. Lancet (1983) 2.58
Wasting as an independent predictor of mortality in patients with cystic fibrosis. Thorax (2001) 2.50
Effects of long term inhaled high dose beclomethasone dipropionate on adrenal function. Thorax (1983) 2.35
Primary Pneumocystis carinii and cytomegalovirus infections. Lancet (1981) 2.23
Evaluation of the forced expiration technique as an adjunct to postural drainage in treatment of cystic fibrosis. Br Med J (1979) 2.15
Systematic review of randomized controlled trials of low-carbohydrate vs. low-fat/low-calorie diets in the management of obesity and its comorbidities. Obes Rev (2008) 2.11
A prognostic model for the prediction of survival in cystic fibrosis. Thorax (1997) 2.10
Comparison of the effect of alprenolol and propranolol on specific airway conductance in asthmatic subjects. Br Med J (1970) 2.02
Meconium ileus equivalent in adults with cystic fibrosis of pancreas: a report of six cases. Br Med J (1976) 2.02
Treatment and prevention of pulmonary complications of cystic fibrosis in infancy and early childhood. Arch Dis Child (1972) 1.99
Management of pneumothorax in adults with cystic fibrosis. Thorax (1982) 1.99
Bacterial flora of respiratory tract in patients with cystic fibrosis, 1950-71. Arch Dis Child (1972) 1.89
Bronchial lability in cystic fibrosis. Arch Dis Child (1973) 1.82
Autoantibodies against bactericidal/permeability-increasing protein in patients with cystic fibrosis. QJM (1996) 1.78
Malignant mesothelioma of the pleura: relation between histological type and clinical behaviour. Thorax (1982) 1.76
Long term venous access using a totally implantable drug delivery system in patients with cystic fibrosis and bronchiectasis. Respir Med (1989) 1.75
Improved survival at low lung function in cystic fibrosis: cohort study from 1990 to 2007. BMJ (2011) 1.74
Medium term treatment of stable stage cystic fibrosis with recombinant human DNase I. Thorax (1995) 1.72
Cationic lipid-mediated CFTR gene transfer to the lungs and nose of patients with cystic fibrosis: a double-blind placebo-controlled trial. Lancet (1999) 1.69
Serum immunoreactive trypsin in cystic fibrosis. Thorax (1981) 1.68
Oral ciprofloxacin compared with conventional intravenous treatment for Pseudomonas aeruginosa infection in adults with cystic fibrosis. Lancet (1987) 1.66
Demographic and social characteristics of adults with cystic fibrosis in the United Kingdom. BMJ (1993) 1.65
Quality of life in adults with cystic fibrosis. Thorax (1996) 1.64
Mycobacterial isolations in young adults with cystic fibrosis. Thorax (1984) 1.60
Meta-analyses of studies of ventricular enlargement and cortical sulcal prominence in mood disorders. Comparisons with controls or patients with schizophrenia. Arch Gen Psychiatry (1995) 1.55
Methicillin-resistant Staphylococcus aureus: impact at a national cystic fibrosis centre. J Hosp Infect (1998) 1.55
Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study. Epidemiologic Registry of Cystic Fibrosis. Eur Respir J (2000) 1.54
Hospital care for adults with cystic fibrosis: an overview and comparison between special cystic fibrosis clinics and general clinics using a patient questionnaire. Thorax (1994) 1.52
Interaction of corticosteroids and catecholamines in the treatment of asthma. Thorax (1975) 1.52
Cystic fibrosis in adolescents and adults. Q J Med (1976) 1.52
Presence of cystic fibrosis-related diabetes mellitus is tightly linked to poor lung function in patients with cystic fibrosis: data from the European Epidemiologic Registry of Cystic Fibrosis. Pediatr Pulmonol (2001) 1.49
Characterisation of the normal right ventricular pressure-volume relation by biplane angiography and simultaneous micromanometer pressure measurements. Br Heart J (1988) 1.48
Cystic fibrosis--immunological reactions to A. fumigatus and common allergens. Clin Allergy (1975) 1.48
Infection control revisited: dilemma facing today's bronchoscopists. BMJ (1988) 1.46
Meta-analysis of brain and cranial size in schizophrenia. Schizophr Res (1996) 1.45
Circulating immune complexes in patients with cryptogenic fibrosing alveolitis. Clin Exp Immunol (1979) 1.44
Sweat tests to diagnose cystic fibrosis in adults. Br Med J (Clin Res Ed) (1983) 1.41
Twice vs three-times daily antibiotics in the treatment of pulmonary exacerbations of cystic fibrosis. J Cyst Fibros (2011) 1.40
Intermediate-term results of heart-lung transplantation for cystic fibrosis. Lancet (1992) 1.40
Information technology in nutrition and dietetic education. Br J Nutr (1998) 1.39
Inhalation of antibiotics in cystic fibrosis. Eur Respir J (1995) 1.39
Adult cystic fibrosis: association of acute pulmonary exacerbations and increasing severity of lung disease with auxotrophic mutants of Pseudomonas aeruginosa. Thorax (1993) 1.37
Increased sputum amino acid concentrations and auxotrophy of Pseudomonas aeruginosa in severe cystic fibrosis lung disease. Thorax (2000) 1.37
The GABAB receptor interacts directly with the related transcription factors CREB2 and ATFx. Proc Natl Acad Sci U S A (2000) 1.36
Importance of viruses and Legionella pneumophila in respiratory exacerbations of young adults with cystic fibrosis. Thorax (1984) 1.36
Linked marker haplotypes and the delta F508 mutation in adults with mild pulmonary disease and cystic fibrosis. Lancet (1990) 1.35
Lack of inducible nitric oxide synthase in bronchial epithelium: a possible mechanism of susceptibility to infection in cystic fibrosis. J Pathol (1998) 1.34
Radiology of uncomplicated asthma. Thorax (1974) 1.33
Cystic fibrosis. Postgrad Med J (1984) 1.32
Nasal potential difference: a clinical diagnostic test for cystic fibrosis. Eur Respir J (1990) 1.32
A cohort study of cystic fibrosis and malignancy. Br J Cancer (1993) 1.31
Simple tests of ventilatory capacity in children with cystic fibrosis. I. Clinical and radiological findings in 85 patients. II. Three-year follow-up on 50 patients. Arch Dis Child (1968) 1.30
Prevalence of atopy and exercise-induced bronchial lability in relatives of patients with cystic fibrosis. Arch Dis Child (1975) 1.29
Vertebral deformities and low bone mineral density in adults with cystic fibrosis: a cross-sectional study. Osteoporos Int (2001) 1.27
Two different Escherichia coli proP promoters respond to osmotic and growth phase signals. J Bacteriol (1995) 1.24
Home-use nebulizers: a potential primary source of Burkholderia cepacia and other colistin-resistant, gram-negative bacteria in patients with cystic fibrosis. J Clin Microbiol (1996) 1.22
Auxotrophy of Pseudomonas aeruginosa in cystic fibrosis. FEMS Microbiol Lett (1992) 1.21
Dietary fibre, bacterial metabolism and toxicity of nitrate in the rat. Xenobiotica (1982) 1.20
Fatal pulmonary infection with Mycobacterium fortuitum in cystic fibrosis. Br J Dis Chest (1984) 1.18
No added benefit from nebulized amiloride in patients with cystic fibrosis. Eur Respir J (1993) 1.18
Beclomethasone dipropionate aerosol in asthma. Transfer of steroid-dependent asthmatic patients from oral prednisone to beclomethasone dipropionate aerosol. Am Rev Respir Dis (1974) 1.17
Enteric coated microspheres of pancreatin in the treatment of cystic fibrosis: comparison with a standard enteric coated preparation. Thorax (1987) 1.15
Vasculitis complicating cystic fibrosis. Q J Med (1989) 1.14
Nasal epithelial ion transport and genetic analysis of infertile men with congenital bilateral absence of the vas deferens. Hum Mol Genet (1993) 1.14
Two years experience with recombinant human DNase I in the treatment of pulmonary disease in cystic fibrosis. Respir Med (1995) 1.13
Do sympathomimetic amines prevent exercise-induced asthma by bronchodilatation alone? Br J Dis Chest (1977) 1.13
The amino terminus of receptor activity modifying proteins is a critical determinant of glycosylation state and ligand binding of calcitonin receptor-like receptor. Mol Pharmacol (1999) 1.12
Factors associated with poor pulmonary function: cross-sectional analysis of data from the ERCF. European Epidemiologic Registry of Cystic Fibrosis. Eur Respir J (2001) 1.11
The arthropathy of cystic fibrosis. Ann Rheum Dis (1988) 1.10
In vivo effects of recombinant human DNase I on sputum in patients with cystic fibrosis. Thorax (1996) 1.09