Published in Lipids on June 01, 1987
Angiotensin mediates renal fibrosis in the nephropathy of glycogen storage disease type Ia. Kidney Int (2007) 0.94
Vascular dysfunction in glycogen storage disease type I. J Pediatr (2008) 0.79
Direct transesterification of all classes of lipids in a one-step reaction. J Lipid Res (1986) 6.42
Efficacy of intravenous continuous infusion of fluorouracil compared with bolus administration in advanced colorectal cancer. J Clin Oncol (1998) 3.79
Biomechanics and neuropathology of adult and paediatric head injury. Br J Neurosurg (2002) 2.87
Defective gamma interferon production in leprosy. Reversal with antigen and interleukin 2. J Exp Med (1983) 2.61
The phosphotyrosine interaction domains of X11 and FE65 bind to distinct sites on the YENPTY motif of amyloid precursor protein. Mol Cell Biol (1996) 2.57
Localization of the X inactivation centre on the human X chromosome in Xq13. Nature (1991) 2.48
Insulin resistance syndrome in a representative sample of children and adolescents from Quebec, Canada. Int J Obes Relat Metab Disord (2004) 2.26
Preliminary report on a mass screening program for neonatal hypothyroidism. J Pediatr (1975) 2.25
The rediscovery of breast feeding. Can Med Assoc J (1978) 2.24
Improved recovery of fatty acid through direct transesterification without prior extraction or purification. J Lipid Res (1984) 1.97
Reappraisal of hepatic arterial infusion in the treatment of nonresectable liver metastases from colorectal cancer. J Natl Cancer Inst (1996) 1.93
Porcine versus pericardial bioprostheses: a comparison of late results in 1,593 patients. Ann Thorac Surg (1989) 1.76
Continuous elemental enteral alimentation in children with Crohn's disease and growth failure. Gastroenterology (1980) 1.68
Chromosome 14-encoded Alzheimer's disease: genetic and clinicopathological description. Ann Neurol (1994) 1.64
Malabsorption of bile acids in children with cystic fibrosis. N Engl J Med (1973) 1.63
Increased levels of plasma malondialdehyde in Friedreich ataxia. Neurology (2000) 1.51
Malignant peripheral nerve sheath tumors associated with neurofibromatosis type 1: a clinicopathologic and molecular study of 17 patients. Arch Dermatol (2001) 1.50
The potential of the hydrocarbon breath test as a measure of lipid peroxidation. Free Radic Biol Med (1994) 1.48
Amyloidosis due to a mutation of the gelsolin gene in an American family with lattice corneal dystrophy type II. N Engl J Med (1991) 1.48
Quantifying physical decline in juvenile neuronal ceroid lipofuscinosis (Batten disease). Neurology (2011) 1.48
Preliminary results on the mental development of hypothyroid infants detected by the Quebec Screening Program. J Pediatr (1983) 1.46
Follow-up at ages 5 and 7 years on mental development in children with hypothyroidism detected by Quebec Screening Program. J Pediatr (1985) 1.46
A clinical rating scale for Batten disease: reliable and relevant for clinical trials. Neurology (2005) 1.45
The adipose tissue phenotype of hormone-sensitive lipase deficiency in mice. Obes Res (2001) 1.45
Factors influencing hemolysis in valve prosthesis. Am Heart J (1972) 1.45
Modification of a screening program for neonatal hypothyroidism. J Pediatr (1978) 1.44
Iatrogenic pneumocephalus secondary to intravenous catheterization. Case report. J Neurosurg (1999) 1.44
Supplementation with carotenoids corrects increased lipid peroxidation in children with cystic fibrosis. Am J Clin Nutr (1996) 1.43
Chronic intermittent elemental diet improves growth failure in children with Crohn's disease. Gastroenterology (1988) 1.41
Assessing the value of employee training. Health Care Manage Rev (1988) 1.39
Infant passenger safety education in perinatal services in California. West J Med (1982) 1.32
Successful treatment of autoimmune enteropathy with cyclosporine. J Pediatr (1990) 1.31
Ca2+ homeostasis and apoptotic resistance of neuroendocrine-differentiated prostate cancer cells. Cell Death Differ (2004) 1.30
Relationship between bile acid malabsorption and pancreatic insufficiency in cystic fibrosis. Gut (1976) 1.30
Beta-1,2-linked oligomannosides from Candida albicans act as signals for tumor necrosis factor alpha production. Infect Immun (1995) 1.30
Orai1 contributes to the establishment of an apoptosis-resistant phenotype in prostate cancer cells. Cell Death Dis (2010) 1.29
Hepatobiliary disease in cystic fibrosis: a survey of current issues and concepts. J Pediatr Gastroenterol Nutr (1982) 1.27
Hepatic changes produced by a single dose of endotoxin in the mouse. Electron microscopy. Am J Pathol (1968) 1.26
Functional complementation of a genetic deficiency with human artificial chromosomes. Am J Hum Genet (2001) 1.26
Thyroid function in neonatal hypothyroidism. J Pediatr (1976) 1.24
Structure and evolutionary origin of the gene encoding mouse NF-M, the middle-molecular-mass neurofilament protein. Eur J Biochem (1987) 1.24
Abnormal biliary lipid composition in cystic fibrosis. Effect of pancreatic enzymes. N Engl J Med (1977) 1.23
Butyrate induced Caco-2 cell apoptosis is mediated via the mitochondrial pathway. Gut (2003) 1.23
Effect of growth conditions on levels of components of the phosphoenolpyruvate:sugar phosphotransferase system in Streptococcus mutans and Streptococcus sobrinus grown in continuous culture. J Bacteriol (1987) 1.22
X11 interaction with beta-amyloid precursor protein modulates its cellular stabilization and reduces amyloid beta-protein secretion. J Biol Chem (1998) 1.21
Small bowel mucosal dysfunction in patients with cystic fibrosis. J Pediatr (1976) 1.20
Progressive and late obstruction of an aorto-coronary venous bypass graft. Circulation (1971) 1.19
Aortocoronary bypass grafts. Early postoperative angiographic evaluation and reexploration for stenosis or thrombosis of the vein graft. Arch Surg (1971) 1.18
Meconium ileus and its equivalent as a risk factor for the development of cirrhosis: an autopsy study in cystic fibrosis. J Pediatr Gastroenterol Nutr (1989) 1.18
A randomized trial of two levels of iron supplementation and developmental outcome in low birth weight infants. J Pediatr (2001) 1.15
Differential structural requirements of heparin and heparan sulfate proteoglycans that promote binding of basic fibroblast growth factor to its receptor. J Biol Chem (1994) 1.15
TSH measurements from blood spots on filter paper: a confirmatory screening test for neonatal hypothyroidism. J Pediatr (1976) 1.14
Expression of a normal and variant Alzheimer's beta-protein gene in amyloid of hereditary cerebral hemorrhage, Dutch type: DNA and protein diagnostic assays. Biochem Biophys Res Commun (1990) 1.13
Aortocoronary bypass graft. Initial blood flow through the graft, and early postoperative patency. Circulation (1971) 1.13
Hepatic changes produced by a single dose of endotoxin in the mouse. Light microscopy and histochemistry. Am J Pathol (1967) 1.13
Interleukin 10 (IL-10) gene variants and susceptibility for paediatric onset Crohn's disease. Aliment Pharmacol Ther (2009) 1.13
Intraduodenal events in cystic fibrosis. J Pediatr Gastroenterol Nutr (1984) 1.13
The sequence and gene characterization of a 400-kb candidate region for IDDM4 on chromosome 11q13. Genomics (2001) 1.11
Specific methylation of plasma nonesterified fatty acids in a one-step reaction. J Lipid Res (1988) 1.10
Comparative bronchial responses to hyperosmolar saline and methacholine in asthma. Thorax (1987) 1.10
Isolation and preliminary characterization of the 14- to 18-kilodalton Candida albicans antigen as a phospholipomannan containing beta-1,2-linked oligomannosides. Infect Immun (1993) 1.09
Pneumatosis and pneumoperitoneum in chronic idiopathic intestinal pseudoobstruction. J Pediatr Surg (1991) 1.08
Cell-lysate conversion of prion protein into its protease-resistant isoform suggests the participation of a cellular chaperone. Biochem Biophys Res Commun (1999) 1.08
Butyrate mediates Caco-2 cell apoptosis via up-regulation of pro-apoptotic BAK and inducing caspase-3 mediated cleavage of poly-(ADP-ribose) polymerase (PARP). Cell Death Differ (1999) 1.08
Atypical MR appearance of Lhermitte-Duclos disease with contrast enhancement. AJNR Am J Neuroradiol (1995) 1.07
One-hour blood xylose test: a reliable index of small bowel function. J Pediatr (1978) 1.07
Apoprotein B structure and receptor recognition of triglyceride-rich low density lipoprotein (LDL) is modified in small LDL but not in triglyceride-rich LDL of normal size. J Biol Chem (1994) 1.07
Paediatric Castleman disease: report of seven cases and review of the literature. Eur J Pediatr (1999) 1.06
High incidence of upper gastrointestinal tract involvement in children with Crohn disease. Pediatrics (1989) 1.06
Detection of beta-1,3-glucanase activity after native polyacrylamide gel electrophoresis: application to tobacco pathogenesis-related proteins. Electrophoresis (1989) 1.05
The Candida albicans phospholipomannan induces in vitro production of tumour necrosis factor-alpha from human and murine macrophages. Immunology (1994) 1.05
Peptic ulcer disease: a clinical study in 73 children. Can Med Assoc J (1974) 1.05
1H-NMR spectroscopy of manno-oligosaccharides of the beta-1,2-linked series released from the phosphopeptidomannan of Candida albicans VW-32 (serotype A). Biochem Biophys Res Commun (1991) 1.04
Anorectal myomectomy in the treatment of short segment Hirschsprung's disease. Ann Surg (1969) 1.03
Detection of virus-specific IgA antibodies in serum of kidney transplant patients with recurrent cytomegalovirus infection by enzymeimmuno and radioimmunoassay techniques. Clin Exp Immunol (1982) 1.02
Malabsorption, hypocholesterolemia, and fat-filled enterocytes with increased intestinal apoprotein B. Chylomicron retention disease. Gastroenterology (1987) 1.02
Reduced brain choline in homocystinuria due to remethylation defects. Neurology (2008) 1.02
Risk of another basal cell carcinoma developing after treatment of a basal cell carcinoma. J Am Acad Dermatol (1993) 1.02
Phosphoenolpyruvate-sugar phosphotransferase transport system of Streptococcus mutans: purification of HPr and enzyme I and determination of their intracellular concentrations by rocket immunoelectrophoresis. Infect Immun (1985) 1.01
Metabolic syndrome X: a review. Can J Cardiol (2000) 1.01
Detection of specific IgA antibodies in serum of kidney transplant patients with recurrent cytomegalovirus infection. Intervirology (1981) 1.00
Substrate-adhering lymphoid cells show impaired tumorigenicity and increased immunogenicity. Nature (1981) 1.00
The cost-effectiveness of fondaparinux compared with enoxaparin as prophylaxis against thromboembolism following major orthopedic surgery. J Thromb Haemost (2003) 0.99
Altered lipid profile, lipoprotein composition, and oxidant and antioxidant status in pediatric Crohn disease. Am J Clin Nutr (2000) 0.99
Elemental diet improves steroid-dependent eosinophilic gastroenteritis and reverses growth failure. J Pediatr Gastroenterol Nutr (1996) 0.98
Hirschsprung's disease in a family with multiple endocrine neoplasia type 2. J Pediatr Gastroenterol Nutr (1982) 0.98
(+)-(S)-dihydroaeruginoic acid, an inhibitor of Septoria tritici and other phytopathogenic fungi and bacteria, produced by Pseudomonas fluorescens. J Nat Prod (1994) 0.98
Liver transplantation for hereditary tyrosinemia: the Quebec experience. Am J Hum Genet (1990) 0.97
Disaccharidase deficiency in children with immunologic deficits. J Pediatr (1970) 0.97
Autoimmune enteropathy. Pediatr Dev Pathol (1999) 0.97
The quantitative determination of fecal bile acids in children by the enzymatic method. Clin Chim Acta (1972) 0.97