Published in Ann Neurol on March 01, 1978
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The mutation at nt 8993 of mitochondrial DNA is a common cause of Leigh's syndrome. Ann Neurol (1993) 1.53
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A microfluorometric enzymatic assay for the determination of alanine and pyruvate in plasma and tissues. J Lab Clin Med (1972) 1.32
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Control of blood sugar in insulin-dependent diabetes: comparison of an artificial endocrine pancreas, continuous subcutaneous insulin infusion, and intensified conventional insulin therapy. N Engl J Med (1980) 1.28
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Differential effects of insulin deficiency on albumin and fibrinogen synthesis in humans. J Clin Invest (1991) 1.26
An animal model for the ketogenic diet. Epilepsia (1974) 1.24
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Insulin resistance of puberty: a defect restricted to peripheral glucose metabolism. J Clin Endocrinol Metab (1991) 1.21
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Alanine and glutamine synthesis and release from skeletal muscle. III. Dietary and hormonal regulation. J Biol Chem (1976) 1.19
Human growth hormone prevents the protein catabolic side effects of prednisone in humans. J Clin Invest (1990) 1.17
Protein metabolism in obesity: effects of body fat distribution and hyperinsulinemia on leucine turnover. Am J Clin Nutr (1991) 1.14
Low dose recombinant human insulin-like growth factor-I fails to affect protein anabolism but inhibits islet cell secretion in humans. J Clin Endocrinol Metab (1992) 1.14
Glucose counterregulation and waning of insulin in the Somogyi phenomenon (posthypoglycemic hyperglycemia). N Engl J Med (1984) 1.14
Increased gluconeogenic substrates in the small-for-gestational-age infant. N Engl J Med (1974) 1.14
Pseudomembranous colitis associated with ampicillin therapy. Am J Dis Child (1974) 1.13
Perforated stress ulcers in infants. J Pediatr Surg (1981) 1.12
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Proceedings: Parenchymatous degeneration of the central nervous system in childhood leukemia. Cancer (1974) 1.11
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Meal stimulation of albumin synthesis: a significant contributor to whole body protein synthesis in humans. Am J Physiol (1992) 1.08
Infantile methemoglobinemia caused by carrot juice. N Engl J Med (1973) 1.08
Ketotic hypoglycemia: an amino acid substrate limited disorder. J Clin Endocrinol Metab (1974) 1.08
Daily periodicity of susceptibility of mice to pneumococcal infection. Nature (1969) 1.06
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Measurement of branched chain amino acids and branched chain alpha-ketoacids in plasma by high-performance liquid chromatography. J Chromatogr (1982) 1.05
Sex steroids, growth hormone, insulin-like growth factor-1: neuroendocrine and metabolic regulation in puberty. Horm Res (1996) 1.05
Effect of alpha-adrenergic stimulation and its blockade on glucose turnover in man. Am J Physiol (1980) 1.04
Inducible nitric oxide synthase (iNOS) gene deficiency increases the mortality of sepsis in mice. Surgery (1999) 1.04
Increased intracellular Ca2+: a critical link in the pathophysiology of sepsis? Proc Natl Acad Sci U S A (1993) 1.04
Effects of free fatty acid availability, glucagon excess, and insulin deficiency on ketone body production in postabsorptive man. J Clin Invest (1983) 1.04
Glucocorticosteroids increase leucine oxidation and impair leucine balance in humans. Am J Physiol (1989) 1.04
Abnormal calcium homeostasis and mitochondrial polarization in a human encephalomyopathy. Proc Natl Acad Sci U S A (1995) 1.04
Origin of chi46,XX/46,XY chimerism in a human true hermaphrodite. Science (1980) 1.03
The alpha-keto acids of branched-chain amino acids: simplified derivatization for physiological samples and complete separation as quinoxalinols by packed column gas chromatography. Anal Biochem (1980) 1.03
Abnormal glucose counterregulation after subcutaneous insulin in insulin-dependent diabetes mellitus. N Engl J Med (1984) 1.02
Inverse relationship of leucine flux and oxidation to free fatty acid availability in vivo. J Clin Invest (1986) 1.02
Long-acting somatostatin analogue therapy and protein metabolism in patients with jejunostomies. Gastroenterology (1994) 1.02
Beta-ketothiolase deficiency as a cause of the "ketotic hyperglycinemia syndrome". Pediatrics (1974) 1.02
Quantitative analysis of regenerating and degenerating areas within the lobule of the carbon tetrachloride-injured liver. Arch Biochem Biophys (1965) 1.02
Association of Crohn disease and Turner syndrome. J Pediatr (1978) 1.00
Insulin and glucose as modulators of the amino acid-induced glucagon release in the isolated pancreas of alloxan and streptozotocin diabetic rats. J Clin Invest (1975) 1.00
Prepyloric gastric antral web: a puzzling epidemic. J Pediatr Surg (1978) 1.00
Antral diaphragm--a cause of gastric outlet obstruction in infants and children. J Pediatr (1977) 1.00
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Middle cerebral artery blood velocity and cerebral blood flow in sickle cell disease. Stroke (1991) 0.99
Gluconeogenesis in very low birth weight infants receiving total parenteral nutrition. Diabetes (1999) 0.99
Adrenergic mechanisms in recovery from hypoglycemia in man: adrenergic blockade. Am J Physiol (1979) 0.99
Dantrolene ameliorates the metabolic hallmarks of sepsis in rats and improves survival in a mouse model of endotoxemia. Proc Natl Acad Sci U S A (1994) 0.98