Published in Annu Rev Genet on January 01, 1997
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Changes in the middle region of Sup35 profoundly alter the nature of epigenetic inheritance for the yeast prion [PSI+]. Proc Natl Acad Sci U S A (2002) 2.15
Oligopeptide repeats in the yeast protein Sup35p stabilize intermolecular prion interactions. EMBO J (2001) 1.69
Discovery of 2-aminothiazoles as potent antiprion compounds. J Virol (2009) 1.51
Changing a single amino acid in the N-terminus of murine PrP alters TSE incubation time across three species barriers. EMBO J (2001) 1.30
A new mechanism for transmissible prion diseases. J Neurosci (2012) 1.25
Cell division modulates prion accumulation in cultured cells. Proc Natl Acad Sci U S A (2007) 1.25
Detection of new quantitative trait Loci for susceptibility to transmissible spongiform encephalopathies in mice. Genetics (2003) 1.22
Prion gene haplotypes of U.S. cattle. BMC Genet (2006) 1.10
The intriguing prion disorders. Cell Mol Life Sci (2006) 1.09
Neuronal aggregates: formation, clearance, and spreading. Dev Cell (2015) 1.09
Pregnancy status and fetal prion genetics determine PrPSc accumulation in placentomes of scrapie-infected sheep. Proc Natl Acad Sci U S A (2002) 1.07
Thinking laterally about neurodegenerative proteinopathies. J Clin Invest (2013) 0.99
Proteasomal dysfunction and endoplasmic reticulum stress enhance trafficking of prion protein aggregates through the secretory pathway and increase accumulation of pathologic prion protein. J Biol Chem (2011) 0.94
Preclinical deposition of pathological prion protein in muscle of experimentally infected primates. PLoS One (2010) 0.91
Molecular modelling indicates that the pathological conformations of prion proteins might be beta-helical. Biochem J (1999) 0.90
Novel mutation of the PRNP gene of a clinical CJD case. BMC Infect Dis (2006) 0.86
Absolute quantification of prion protein (90-231) using stable isotope-labeled chymotryptic peptide standards in a LC-MRM AQUA workflow. J Am Soc Mass Spectrom (2012) 0.83
Green fluorescent protein as a reporter of prion protein folding. Virol J (2006) 0.82
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Disease-associated mutations in the prion protein impair laminin-induced process outgrowth and survival. J Biol Chem (2012) 0.76
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Prion protein biology. Cell (1998) 4.20
Activation of mouse genes in transformed cells. Cell (1983) 3.85
A transmembrane form of the prion protein in neurodegenerative disease. Science (1998) 3.76
Scrapie-infected murine neuroblastoma cells produce protease-resistant prion proteins. J Virol (1988) 3.37
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Strain-specified relative conformational stability of the scrapie prion protein. Protein Sci (2001) 2.60
Selective neuronal targeting in prion disease. Neuron (1997) 1.82
Elimination of prions by branched polyamines and implications for therapeutics. Proc Natl Acad Sci U S A (1999) 1.73
Identification of two prion protein regions that modify scrapie incubation time. J Virol (2001) 1.63
The construction of cosmid libraries of eukaryotic DNA using the Homer series of vectors. Nucleic Acids Res (1982) 1.47
Branched polyamines cure prion-infected neuroblastoma cells. J Virol (2001) 1.32
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Human prion diseases and neurodegeneration. Curr Top Microbiol Immunol (1996) 0.97
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Ipsilateral synchronous ductal and colloid breast carcinomas with mammographic correlation. Australas Radiol (1992) 0.75
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The use of cDNA cloning techniques to isolate genes activated in tumour cells. Haematol Blood Transfus (1983) 0.75
Electronic data processing (EDP) and multiphasic health screening. J Occup Med (1972) 0.75
Medical statistics, system monitoring and provisional normals. J Occup Med (1972) 0.75