PubRank

R A Williamson

Author PubWeight™ 94.78‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 The mammalian sodium channel BNC1 is required for normal touch sensation. Nature 2000 3.30
2 Requirement for the leukocyte-specific adapter protein SLP-76 for normal T cell development. Science 1998 3.18
3 A conformational transition at the N terminus of the prion protein features in formation of the scrapie isoform. J Mol Biol 1997 2.95
4 Antibodies inhibit prion propagation and clear cell cultures of prion infectivity. Nature 2001 2.78
5 Strain-specified relative conformational stability of the scrapie prion protein. Protein Sci 2001 2.60
6 Molecular profile of an antibody response to HIV-1 as probed by combinatorial libraries. J Mol Biol 1993 2.42
7 Familial insertional translocation of a portion of 3q into 11q resulting in duplication and deletion of region 3q22.1 leads to q24 in different offspring. Am J Med Genet 1981 2.23
8 Disruption of the beta-sarcoglycan gene reveals pathogenetic complexity of limb-girdle muscular dystrophy type 2E. Mol Cell 2000 1.66
9 Disruption of the beta subunit of the epithelial Na+ channel in mice: hyperkalemia and neonatal death associated with a pseudohypoaldosteronism phenotype. Proc Natl Acad Sci U S A 1999 1.53
10 Syntaxin 4 heterozygous knockout mice develop muscle insulin resistance. J Clin Invest 2001 1.45
11 Management of fetal hemolytic disease by cordocentesis. I. Prediction of fetal anemia. Am J Obstet Gynecol 1991 1.43
12 The N-terminal domain of tissue inhibitor of metalloproteinases retains metalloproteinase inhibitory activity. Biochemistry 1991 1.41
13 Recombinant human respiratory syncytial virus (RSV) monoclonal antibody Fab is effective therapeutically when introduced directly into the lungs of RSV-infected mice. Proc Natl Acad Sci U S A 1994 1.40
14 Recombinant human Fab to glycoprotein D neutralizes infectivity and prevents cell-to-cell transmission of herpes simplex viruses 1 and 2 in vitro. Proc Natl Acad Sci U S A 1994 1.33
15 Cloning the antibody response in humans with inflammatory CNS disease: isolation of measles virus-specific antibodies from phage display libraries of a subacute sclerosing panencephalitis brain. J Neuroimmunol 1999 1.28
16 Purification of human dihydro-orotate dehydrogenase and its inhibition by A77 1726, the active metabolite of leflunomide. Biochem J 1998 1.13
17 High resolution structure of the N-terminal domain of tissue inhibitor of metalloproteinases-2 and characterization of its interaction site with matrix metalloproteinase-3. J Biol Chem 1998 1.11
18 Genetic susceptibility to preeclampsia: roles of cytosineto-thymine substitution at nucleotide 677 of the gene for methylenetetrahydrofolate reductase, 68-base pair insertion at nucleotide 844 of the gene for cystathionine beta-synthase, and factor V Leiden mutation. Am J Obstet Gynecol 2001 1.10
19 Telling about the analyst's pregnancy. J Am Psychoanal Assoc 1995 1.09
20 Protection of nude mice by passive immunization with a type-common human recombinant monoclonal antibody against HSV. Virology 1996 1.09
21 Appropriate tissue- and cell-specific expression of a single copy human angiotensinogen transgene specifically targeted upstream of the HPRT locus by homologous recombination. J Biol Chem 2000 1.05
22 Gastroschisis and omphalocele: does either antenatal diagnosis or route of delivery make a difference in perinatal outcome? Obstet Gynecol 1990 1.03
23 Human antibody responses to mature and immature forms of viral envelope in respiratory syncytial virus infection: significance for subunit vaccines. J Virol 1999 1.03
24 Antibody binding defines a structure for an epitope that participates in the PrPC-->PrPSc conformational change. J Mol Biol 1999 1.00
25 The relationship of pyospermia and seminal fluid bacteriology to sperm function as reflected in the sperm penetration assay. Fertil Steril 1982 1.00
26 Antibody and virus: binding and neutralization. Virology 2000 1.00
27 Relationship between second trimester maternal serum alpha-fetoprotein and umbilical artery Doppler velocimetry and their association with preterm delivery. Am J Perinatol 1991 0.99
28 Rh isoimmunization related to amniocentesis. Am J Med Genet 1983 0.99
29 The specificity of TIMP-2 for matrix metalloproteinases can be modified by single amino acid mutations. J Biol Chem 1999 0.99
30 Diffuse pulmonary hemangiomatosis. Radiology 1978 0.98
31 Characterization of a type-common human recombinant monoclonal antibody to herpes simplex virus with high therapeutic potential. J Clin Microbiol 1998 0.98
32 Sarcospan-deficient mice maintain normal muscle function. Mol Cell Biol 2000 0.98
33 Surveillance for anencephaly and spina bifida and the impact of prenatal diagnosis--United States, 1985-1994. MMWR CDC Surveill Summ 1995 0.97
34 Management of fetal hemolytic disease by cordocentesis. II. Outcome of treatment. Am J Obstet Gynecol 1991 0.97
35 Topically applied human recombinant monoclonal IgG1 antibody and its Fab and F(ab')2 fragments protect mice from vaginal transmission of HSV-2. Virology 1996 0.97
36 Synthesis, structure-activity relationships, and pharmacokinetic properties of dihydroorotate dehydrogenase inhibitors: 2-cyano-3-cyclopropyl-3-hydroxy-N-[3'-methyl-4'-(trifluoromethyl)phenyl ] propenamide and related compounds. J Med Chem 1996 0.94
37 Risk of preeclampsia in second-trimester triploid pregnancies. Obstet Gynecol 1997 0.93
38 Directed selection of recombinant human monoclonal antibodies to herpes simplex virus glycoproteins from phage display libraries. Proc Natl Acad Sci U S A 1995 0.93
39 Immobilized prion protein undergoes spontaneous rearrangement to a conformation having features in common with the infectious form. EMBO J 2001 0.90
40 Antibodies in human infectious disease. Immunol Res 2000 0.88
41 Copper refolding of prion protein. Biochem Biophys Res Commun 2000 0.87
42 Normal values for human umbilical venous and amniotic fluid pressures and their alteration by fetal disease. Am J Obstet Gynecol 1989 0.87
43 Subchorionic hemorrhage: sonographic diagnosis and clinical significance. AJR Am J Roentgenol 1987 0.86
44 pFab-CMV, a single vector system for the rapid conversion of recombinant Fabs into whole IgG1 antibodies. Immunotechnology 1999 0.86
45 Emphysematous gastritis in a leukemic child. Med Pediatr Oncol 1976 0.86
46 Site-directed mutations that alter the inhibitory activity of the tissue inhibitor of metalloproteinases-1: importance of the N-terminal region between cysteine 3 and cysteine 13. Biochemistry 1992 0.86
47 Factors influencing maternal estimates of genetic risk. Am J Med Genet 1985 0.85
48 Culture of cytomegalovirus from frozen-thawed semen. Fertil Steril 1988 0.85
49 Molecular immunologic strategies to identify antigens and b-cell responses unique to multiple sclerosis. Arch Neurol 2001 0.84
50 Characteristics of immunity induced by viral antigen or conferred by antibody via different administration routes. Clin Exp Immunol 2002 0.83
51 Sperm penetration assay: useful test in evaluation of male fertility. Obstet Gynecol 1981 0.83
52 The glycosylation properties of D2 dopamine receptors from striatal and limbic areas of bovine brain. Biochem J 1988 0.83
53 Analysis of the role of dystroglycan in early postimplantation mouse development. Ann N Y Acad Sci 1998 0.82
54 Mesenchymal hamartoma of the liver identified by fetal sonography. AJR Am J Roentgenol 1983 0.82
55 Fetal gastroschisis complicated by bowel dilation: an indication for imminent delivery? Fetal Diagn Ther 1990 0.82
56 Evaluation of severe growth retardation using cordocentesis--hematologic and metabolic alterations by etiology. Obstet Gynecol 1989 0.82
57 Reduction in amniocentesis risks using a real-time needle guide procedure. Obstet Gynecol 1985 0.82
58 Detection and typing of herpes simplex viruses by using recombinant immunoglobulin fragments produced in bacteria. J Clin Microbiol 1997 0.81
59 Synthesis and characterization of 111In-DTPA-N-TIMP-2: a radiopharmaceutical for imaging matrix metalloproteinase expression. Bioconjug Chem 2001 0.81
60 Hereditary coagulopathies in pregnancy. Clin Obstet Gynecol 1985 0.81
61 The association between fetal karyotype and mean corpuscular volume. Am J Obstet Gynecol 1991 0.80
62 Inhibition of stimulated Jurkat cell adenosine 3',5'-cyclic monophosphate synthesis by the immunomodulatory compound HR325. Biochem Pharmacol 2001 0.80
63 Copper induces conformational changes in the N-terminal part of cell-surface PrPC. Arch Virol 2006 0.80
64 In vivo evaluation of 111In-DTPA-N-TIMP-2 in Kaposi sarcoma associated with HIV infection. Eur J Nucl Med 2001 0.80
65 Potencies of leflunomide and HR325 as inhibitors of prostaglandin endoperoxide H synthase-1 and -2: comparison with nonsteroidal anti-inflammatory drugs. J Pharmacol Exp Ther 1997 0.80
66 Effect of increased circulating corticosterone in the immature fowl on the blastogenic responses of peripheral blood lymphocytes. Dev Comp Immunol 1988 0.80
67 Responsiveness to insulin is a dominant characteristic in somatic cell hybrids. J Cell Physiol 1978 0.79
68 Possible relationship between in utero diethylstilbestrol exposure and male fertility. Am J Obstet Gynecol 1981 0.79
69 Cloning the antibody response in humans with chronic inflammatory disease: immunopanning of subacute sclerosing panencephalitis (SSPE) brain sections with antibody phage libraries prepared from SSPE brain enriches for antibody recognizing measles virus antigens in situ. J Virol 2000 0.79
70 Partial complementation of pyruvate dehydrogenase deficiency by independently expressed lipoyl and catalytic domains of the dihydrolipoamide acetyltransferase component. FEMS Microbiol Lett 1989 0.79
71 Heterogeneity of prenatal onset hydrocephalus: management and counseling implications. Am J Med Genet 1984 0.79
72 Antibody binding to greater than 50% of sperm at the tail tip does not impair male fertility. Fertil Steril 1988 0.78
73 Lipoprotein lipase gene mutations and the genetic susceptibility of preeclampsia. Hypertension 2001 0.78
74 Biochemistry and hematology at decompression sickness: a case report. Aviat Space Environ Med 1976 0.78
75 Ultrastructural sperm tail defects associated with sperm immotility. Fertil Steril 1984 0.78
76 Intrauterine transfusion treatment of nonimmune hydrops fetalis secondary to human parvovirus B19 infection. Am J Obstet Gynecol 1991 0.78
77 Evaluation of multiple-marker screening for Down syndrome in a statewide population. Am J Obstet Gynecol 1993 0.78
78 Copper has differential effect on prion protein with polymorphism of position 129. Biochem Biophys Res Commun 2000 0.78
79 Fetal echogenic bowel on ultrasound: is there clinical significance? Fetal Diagn Ther 1994 0.78
80 Prenatal diagnosis of fetal hyperthyroidism using funipuncture. Obstet Gynecol 1990 0.77
81 Molecular profile of a human monoclonal antibody Fab fragment specific for Epstein-Barr virus gp350/220 antigen. Hum Immunol 2001 0.77
82 Concentration of glycerol required for optimal survival and in vitro fertilizing capacity of frozen sperm is dependent on cryopreservation medium. Fertil Steril 1988 0.77
83 Abnormal pregnancy sonogram: selective indication for fetal karyotype. Obstet Gynecol 1987 0.76
84 Comparison of motility stimulants for cryopreserved human semen. Fertil Steril 1989 0.76
85 Azathioprine teratogenicity: review of the literature and case report. Obstet Gynecol 1981 0.76
86 Expression of endothelial nitric oxide synthase protein is not necessary for mechanical strain-induced nitric oxide production by cultured osteoblasts. Osteoporos Int 2012 0.75
87 Screening for cytomegalovirus antibody. Fertil Steril 1990 0.75
88 Use of oocytes from anonymous, matched, fertile donors for prevention of heritable genetic diseases. J Med Genet 1992 0.75
89 Prediction of pregnancy outcome with single versus serial maternal serum alpha-fetoprotein tests. Am J Obstet Gynecol 1992 0.75
90 Antenatal treatment of fetal alloimmune thrombocytopenia. Obstet Gynecol 1992 0.75
91 Survival and in vitro fertilization potential of sperm following washing and incubation with different protein supplements. Int J Fertil 1990 0.75
92 Antenatal sonographic diagnosis of club foot with particular attention to the implications and outcomes of isolated club foot. Ultrasound Obstet Gynecol 1998 0.75
93 Risk factors for cordocentesis and fetal intravascular transfusion. Am J Obstet Gynecol 1991 0.75
94 The effect of exposure to 40 degrees on the heat production and the serum concentrations of triiodothyronine, thyroxine, and corticosterone in immature domestic fowl. Gen Comp Endocrinol 1985 0.75
95 Use of needle guide to improve sonographically directed amniocentesis. Am J Obstet Gynecol 1984 0.75
96 Diverse maternal and fetal pathology associated with absent diastolic flow in the umbilical artery of high-risk fetuses. Obstet Gynecol 1991 0.75
97 Analysis of the interaction of TIMP-2 and MMPs: engineering the changes. Ann N Y Acad Sci 1999 0.75
98 Maternal serum alpha-fetoprotein screening: report of a pilot project in Iowa. Iowa Med 1986 0.75
99 Association of neural tube defects with omphalocele in chromosomally normal fetuses. Am J Med Genet 1987 0.75
100 Rapid assay of phage-derived recombinant human fabs as bispecific antibodies. Biotechnology (N Y) 1995 0.75
101 Magnetic resonance imaging of fetuses with intracranial defects. Obstet Gynecol 1991 0.75
102 The effect of diazepam on rates of fertilization in the CF-1 mouse. Am J Obstet Gynecol 1981 0.75
103 Moral and religious influences on the amniocentesis decision. Soc Biol 1986 0.75
104 Survival of human sperm following controlled- and noncontrolled-rate cryopreservation. Andrologia 1989 0.75
105 Prospects for fetal treatment. Iowa Med 1987 0.75
106 Case study: conjoined twins and anencephaly. J Clin Ethics 1990 0.75
107 Lethal bone dysplasia in a fetus with manifestations of atelosteogenesis I and Boomerang dysplasia. Am J Med Genet 1993 0.75
108 The effect of a single injection of thyrotrophin on serum concentrations of thyroxine, triiodothyronine, and reverse triiodothyronine in the immature chicken (Gallus domesticus). Gen Comp Endocrinol 1985 0.75
109 Sonographic diagnosis of cloverleaf skull and thanatophoric dysplasia in the second trimester. J Clin Ultrasound 1986 0.75
110 Archeoastronomy at pueblo bonito. Science 1977 0.75
111 Effect of increased circulating corticosterone on serum and thyroidal concentrations of iodothyronines and the responses to thyrotrophin in the immature fowl (Gallus domesticus). Gen Comp Endocrinol 1987 0.75
112 Antenatal ultrasound diagnosis of variant of pentalogy of Cantrell. J Ultrasound Med 1987 0.75
113 Antenatal ultrasound diagnosis of iniencephaly. J Clin Ultrasound 1987 0.75
114 Sequence-specific assignment and determination of the secondary structure of the 163-residue M. tuberculosis and M. bovis antigenic protein mpb70. J Biomol NMR 2001 0.75
115 Achondrogenesis type II (Langer-Saldino) in association with jugular lymphatic obstruction sequence. Prenat Diagn 1989 0.75
116 Expanded Möbius syndrome. Pediatr Neurol 2001 0.75
117 Pregnancy outcome following ultrasound diagnosis of fetal urinary tract anomalies and/or oligohydramnios. Fetal Ther 1986 0.75
118 Prolonged elevation of alphafetoprotein and detectable acetylcholinesterase after death of an anomalous twin fetus. Prenat Diagn 1989 0.75
119 The effect of intravascular transfusion on umbilical venous pressure in anemic fetuses with and without hydrops. Am J Obstet Gynecol 1989 0.75
120 Maternal serum alpha-fetoprotein in presence of both neural tube defects and chromosome anomalies. Lancet 1986 0.75
121 Genital tract examinations and zona-free hamster egg penetration tests from men exposed in utero to diethylstilbestrol. Fertil Steril 1984 0.75
122 Detection of fetal Turner syndrome with multiple-marker screening. Am J Obstet Gynecol 1994 0.75