Published in Biochemistry on February 04, 2003
Mitochondrial tRNA 3' end metabolism and human disease. Nucleic Acids Res (2004) 1.37
Human mitochondrial leucyl-tRNA synthetase corrects mitochondrial dysfunctions due to the tRNALeu(UUR) A3243G mutation, associated with mitochondrial encephalomyopathy, lactic acidosis, and stroke-like symptoms and diabetes. Mol Cell Biol (2010) 1.09
Overexpressed mitochondrial leucyl-tRNA synthetase suppresses the A3243G mutation in the mitochondrial tRNA(Leu(UUR)) gene. RNA (2008) 1.00
Pathogenic mechanism of a human mitochondrial tRNAPhe mutation associated with myoclonic epilepsy with ragged red fibers syndrome. Proc Natl Acad Sci U S A (2007) 0.89
Correction of the consequences of mitochondrial 3243A>G mutation in the MT-TL1 gene causing the MELAS syndrome by tRNA import into mitochondria. Nucleic Acids Res (2011) 0.89
Metabolically induced heteroplasmy shifting and l-arginine treatment reduce the energetic defect in a neuronal-like model of MELAS. Biochim Biophys Acta (2012) 0.89
Aminoacylation properties of pathology-related human mitochondrial tRNA(Lys) variants. RNA (2004) 0.88
Structural probing of a pathogenic tRNA dimer. RNA (2005) 0.88
Mitochondrial lysyl-tRNA synthetase independent import of tRNA lysine into yeast mitochondria. PLoS One (2012) 0.81
Structural dynamics of a mitochondrial tRNA possessing weak thermodynamic stability. Biochemistry (2014) 0.80
A novel mitochondrial tRNA(Val) T1658C mutation identified in a CPEO family. Mol Vis (2010) 0.75
The phenotypic expression of mitochondrial tRNA-mutations can be modulated by either mitochondrial leucyl-tRNA synthetase or the C-terminal domain thereof. Front Genet (2015) 0.75
Clinical and Molecular Characteristics in 100 Chinese Pediatric Patients with m.3243A>G Mutation in Mitochondrial DNA. Chin Med J (Engl) (2016) 0.75
A green algal apicoplast ancestor. Science (2002) 1.85
The typically mitochondrial DNA-encoded ATP6 subunit of the F1F0-ATPase is encoded by a nuclear gene in Chlamydomonas reinhardtii. J Biol Chem (2001) 1.03
Overexpressed mitochondrial leucyl-tRNA synthetase suppresses the A3243G mutation in the mitochondrial tRNA(Leu(UUR)) gene. RNA (2008) 1.00
Recognition of human mitochondrial tRNALeu(UUR) by its cognate leucyl-tRNA synthetase. J Mol Biol (2004) 0.99
Lysyl-tRNA synthetase is a target for mutant SOD1 toxicity in mitochondria. J Biol Chem (2008) 0.98
Atomic-level functional model of dengue virus Envelope protein infectivity. Proc Natl Acad Sci U S A (2013) 0.97
Mitochondrial genome sequence analysis: a custom bioinformatics pipeline substantially improves Affymetrix MitoChip v2.0 call rate and accuracy. BMC Bioinformatics (2011) 0.95
What limits the allotopic expression of nucleus-encoded mitochondrial genes? The case of the chimeric Cox3 and Atp6 genes. Mitochondrion (2010) 0.88
Mitochondrial lysyl-tRNA synthetase independent import of tRNA lysine into yeast mitochondria. PLoS One (2012) 0.81
Genetic correction of mitochondrial diseases: using the natural migration of mitochondrial genes to the nucleus in chlorophyte algae as a model system. Ann N Y Acad Sci (2004) 0.79
Structure of nuclear-localized cox3 genes in Chlamydomonas reinhardtii and in its colorless close relative Polytomella sp. Curr Genet (2002) 0.79
Expression and distribution of acetylcholinesterase among the cellular components of the neuromuscular junction formed in human myotube in vitro. Chem Biol Interact (2005) 0.77