Published in Mitochondrion on September 18, 2010
Mitochondrial optic neuropathies - disease mechanisms and therapeutic strategies. Prog Retin Eye Res (2010) 3.58
Extreme mitochondrial evolution in the ctenophore Mnemiopsis leidyi: Insight from mtDNA and the nuclear genome. Mitochondrial DNA (2011) 1.08
Gene Therapy for Leber Hereditary Optic Neuropathy: Initial Results. Ophthalmology (2015) 0.97
Leber's Hereditary Optic Neuropathy-Gene Therapy: From Benchtop to Bedside. J Ophthalmol (2010) 0.96
Treatment of hereditary optic neuropathies. Nat Rev Neurol (2012) 0.86
Mitochondrial cytochrome c oxidase deficiency. Clin Sci (Lond) (2016) 0.84
Experimental relocation of the mitochondrial ATP9 gene to the nucleus reveals forces underlying mitochondrial genome evolution. PLoS Genet (2012) 0.82
Differential targeting of VDAC3 mRNA isoforms influences mitochondria morphology. Proc Natl Acad Sci U S A (2014) 0.81
Nuclear expression of mitochondrial ND4 leads to the protein assembling in complex I and prevents optic atrophy and visual loss. Mol Ther Methods Clin Dev (2015) 0.80
Emerging therapies for mitochondrial disorders. Brain (2016) 0.80
Unexpectedly Streamlined Mitochondrial Genome of the Euglenozoan Euglena gracilis. Genome Biol Evol (2015) 0.76
The Chlamydomonas genome reveals the evolution of key animal and plant functions. Science (2007) 11.15
A green algal apicoplast ancestor. Science (2002) 1.85
The typically mitochondrial DNA-encoded ATP6 subunit of the F1F0-ATPase is encoded by a nuclear gene in Chlamydomonas reinhardtii. J Biol Chem (2001) 1.03
Identification of novel mitochondrial protein components of Chlamydomonas reinhardtii. A proteomic approach. Plant Physiol (2003) 1.01
Overexpressed mitochondrial leucyl-tRNA synthetase suppresses the A3243G mutation in the mitochondrial tRNA(Leu(UUR)) gene. RNA (2008) 1.00
Recognition of human mitochondrial tRNALeu(UUR) by its cognate leucyl-tRNA synthetase. J Mol Biol (2004) 0.99
Lysyl-tRNA synthetase is a target for mutant SOD1 toxicity in mitochondria. J Biol Chem (2008) 0.98
Atomic-level functional model of dengue virus Envelope protein infectivity. Proc Natl Acad Sci U S A (2013) 0.97
Mitochondrial genome sequence analysis: a custom bioinformatics pipeline substantially improves Affymetrix MitoChip v2.0 call rate and accuracy. BMC Bioinformatics (2011) 0.95
The pathogenic A3243G mutation in human mitochondrial tRNALeu(UUR) decreases the efficiency of aminoacylation. Biochemistry (2003) 0.94
Bifunctional aldehyde/alcohol dehydrogenase (ADHE) in chlorophyte algal mitochondria. Plant Mol Biol (2003) 0.94
The mitochondrial ATP synthase of chlorophycean algae contains eight subunits of unknown origin involved in the formation of an atypical stator-stalk and in the dimerization of the complex. J Bioenerg Biomembr (2006) 0.93
A novel 11-kDa inhibitory subunit in the F1FO ATP synthase of Paracoccus denitrificans and related alpha-proteobacteria. FASEB J (2009) 0.91
Structure of dimeric F1F0-ATP synthase. J Biol Chem (2010) 0.90
Swi/SNF-GCN5-dependent chromatin remodelling determines induced expression of GDH3, one of the paralogous genes responsible for ammonium assimilation and glutamate biosynthesis in Saccharomyces cerevisiae. Mol Microbiol (2005) 0.89
Atypical cristae morphology of human syncytiotrophoblast mitochondria: role for complex V. J Biol Chem (2011) 0.87
The ζ subunit of the F1FO-ATP synthase of α-proteobacteria controls rotation of the nanomotor with a different structure. FASEB J (2014) 0.86
The mitochondrial oxidative phosphorylation proteome of Chlamydomonas reinhardtii deduced from the Genome Sequencing Project. Plant Physiol (2005) 0.86
Lineage-specific fragmentation and nuclear relocation of the mitochondrial cox2 gene in chlorophycean green algae (Chlorophyta). Mol Phylogenet Evol (2012) 0.83
Cytochrome f and subunit IV, two essential components of the photosynthetic bf complex typically encoded in the chloroplast genome, are nucleus-encoded in Euglena gracilis. Biochim Biophys Acta (2003) 0.83
Subunit-subunit interactions and overall topology of the dimeric mitochondrial ATP synthase of Polytomella sp. Biochim Biophys Acta (2010) 0.82
In Yarrowia lipolytica mitochondria, the alternative NADH dehydrogenase interacts specifically with the cytochrome complexes of the classic respiratory pathway. Biochim Biophys Acta (2008) 0.82
Mitochondrial lysyl-tRNA synthetase independent import of tRNA lysine into yeast mitochondria. PLoS One (2012) 0.81
Divergence of the mitochondrial electron transport chains from the green alga Chlamydomonas reinhardtii and its colorless close relative Polytomella sp. Biochim Biophys Acta (2005) 0.81
Loss of mitochondrial ATP synthase subunit beta (Atp2) alters mitochondrial and chloroplastic function and morphology in Chlamydomonas. Biochim Biophys Acta (2010) 0.80
Chlamydomonas reinhardtii: the model of choice to study mitochondria from unicellular photosynthetic organisms. Methods Mol Biol (2007) 0.80
Genetic correction of mitochondrial diseases: using the natural migration of mitochondrial genes to the nucleus in chlorophyte algae as a model system. Ann N Y Acad Sci (2004) 0.79
Structure of nuclear-localized cox3 genes in Chlamydomonas reinhardtii and in its colorless close relative Polytomella sp. Curr Genet (2002) 0.79
A deletion in the PRKAR1A gene is associated with Carney complex. J Pediatr Endocrinol Metab (2008) 0.79
The fully-active and structurally-stable form of the mitochondrial ATP synthase of Polytomella sp. is dimeric. J Bioenerg Biomembr (2009) 0.78
Expression and distribution of acetylcholinesterase among the cellular components of the neuromuscular junction formed in human myotube in vitro. Chem Biol Interact (2005) 0.77
Interactions of subunits Asa2, Asa4 and Asa7 in the peripheral stalk of the mitochondrial ATP synthase of the chlorophycean alga Polytomella sp. Biochim Biophys Acta (2013) 0.77
During the stationary growth phase, Yarrowia lipolytica prevents the overproduction of reactive oxygen species by activating an uncoupled mitochondrial respiratory pathway. Biochim Biophys Acta (2011) 0.77
Characterization of oxidative phosphorylation in the colorless chlorophyte Polytomella sp. Its mitochondrial respiratory chain lacks a plant-like alternative oxidase. Biochim Biophys Acta (2002) 0.77
The polypeptides COX2A and COX2B are essential components of the mitochondrial cytochrome c oxidase of Toxoplasma gondii. Biochim Biophys Acta (2007) 0.77
Reconstructing the mitochondrial protein import machinery of Chlamydomonas reinhardtii. Genetics (2008) 0.76
On the evolutionary origins of apicoplasts: revisiting the rhodophyte vs. chlorophyte controversy. Microbes Infect (2004) 0.76
In Polytomella sp. mitochondria, biogenesis of the heterodimeric COX2 subunit of cytochrome c oxidase requires two different import pathways. Biochim Biophys Acta (2012) 0.76
Correction: New Insights on the Mechanism of the K+-Independent Activity of Crenarchaeota Pyruvate Kinases. PLoS One (2015) 0.75
The Mexican Society of Biochemistry: Keeping young at 54. IUBMB Life (2011) 0.75
The cytosol-synthesized subunit II (Cox2) precursor with the point mutation W56R is correctly processed in yeast mitochondria to rescue cytochrome oxidase. Biochim Biophys Acta (2012) 0.75