PubRank

Stephen J DeArmond

Author PubWeight™ 81.80‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Synthetic mammalian prions. Science 2004 7.35
2 A change in the conformation of prions accompanies the emergence of a new prion strain. Neuron 2002 3.36
3 Challenging the clinical utility of the 14-3-3 protein for the diagnosis of sporadic Creutzfeldt-Jakob disease. Arch Neurol 2003 3.20
4 Continuum of prion protein structures enciphers a multitude of prion isolate-specified phenotypes. Proc Natl Acad Sci U S A 2006 2.69
5 Design and construction of diverse mammalian prion strains. Proc Natl Acad Sci U S A 2009 2.41
6 Purified and synthetic Alzheimer's amyloid beta (Aβ) prions. Proc Natl Acad Sci U S A 2012 2.36
7 Transmission of multiple system atrophy prions to transgenic mice. Proc Natl Acad Sci U S A 2013 2.19
8 Protease-sensitive synthetic prions. PLoS Pathog 2010 2.14
9 Asymptomatic deer excrete infectious prions in faeces. Nature 2009 2.10
10 Mutant PrPSc conformers induced by a synthetic peptide and several prion strains. J Virol 2004 2.07
11 Transmission of elk and deer prions to transgenic mice. J Virol 2006 2.03
12 Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proc Natl Acad Sci U S A 2003 2.01
13 Clinicopathological correlations in corticobasal degeneration. Ann Neurol 2011 1.86
14 Prion clearance in bigenic mice. J Gen Virol 2005 1.79
15 Conformational transformation and selection of synthetic prion strains. J Mol Biol 2011 1.66
16 Dominant-negative inhibition of prion replication in transgenic mice. Proc Natl Acad Sci U S A 2002 1.65
17 Time-controlled transcardiac perfusion cross-linking for the study of protein interactions in complex tissues. Nat Biotechnol 2004 1.63
18 Measuring prions by bioluminescence imaging. Proc Natl Acad Sci U S A 2009 1.59
19 Continuous quinacrine treatment results in the formation of drug-resistant prions. PLoS Pathog 2009 1.58
20 Trafficking of prion proteins through a caveolae-mediated endosomal pathway. J Cell Biol 2003 1.51
21 Prions in skeletal muscle. Proc Natl Acad Sci U S A 2002 1.48
22 Bioluminescence imaging of Abeta deposition in bigenic mouse models of Alzheimer's disease. Proc Natl Acad Sci U S A 2011 1.39
23 Cytosolic prion protein in neurons. J Neurosci 2003 1.34
24 Selective frontoinsular von Economo neuron and fork cell loss in early behavioral variant frontotemporal dementia. Cereb Cortex 2011 1.24
25 Notch-1 activation and dendritic atrophy in prion disease. Proc Natl Acad Sci U S A 2005 1.17
26 Transmission of scrapie and sheep-passaged bovine spongiform encephalopathy prions to transgenic mice expressing elk prion protein. J Gen Virol 2009 1.15
27 The neurodegeneration sequence in prion diseases: evidence from functional, morphological and ultrastructural studies of the GABAergic system. J Neuropathol Exp Neurol 2004 1.14
28 Resistance of bovine spongiform encephalopathy (BSE) prions to inactivation. PLoS Pathog 2008 1.14
29 Correlating DWI MRI with pathologic and other features of Jakob-Creutzfeldt disease. Alzheimer Dis Assoc Disord 2009 1.13
30 Cryo-immunogold electron microscopy for prions: toward identification of a conversion site. J Neurosci 2008 1.12
31 Drug resistance confounding prion therapeutics. Proc Natl Acad Sci U S A 2013 1.10
32 Spontaneous generation of anchorless prions in transgenic mice. Proc Natl Acad Sci U S A 2011 1.08
33 Human prion strain selection in transgenic mice. Ann Neurol 2010 1.06
34 Spontaneous generation of rapidly transmissible prions in transgenic mice expressing wild-type bank vole prion protein. Proc Natl Acad Sci U S A 2012 1.03
35 Salivary prions in sheep and deer. Prion 2012 1.02
36 Prion infection of mouse neurospheres. Proc Natl Acad Sci U S A 2006 1.01
37 Conformation-dependent high-affinity monoclonal antibodies to prion proteins. J Immunol 2010 1.00
38 A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. J Neurosci 2009 1.00
39 Differential diagnosis of Jakob-Creutzfeldt disease. Arch Neurol 2012 0.98
40 Convergent replication of mouse synthetic prion strains. Am J Pathol 2013 0.98
41 Developmental expression of PrP in the post-implantation embryo. Brain Res 2006 0.97
42 Sporadic corticobasal syndrome due to FTLD-TDP. Acta Neuropathol 2009 0.95
43 Prion Disease Induces Alzheimer Disease-Like Neuropathologic Changes. J Neuropathol Exp Neurol 2015 0.91
44 Neurotoxicity of intra-arterial papaverine preserved with chlorobutanol used for the treatment of cerebral vasospasm after aneurysmal subarachnoid hemorrhage. Stroke 2004 0.90
45 A brain aggregate model gives new insights into the pathobiology and treatment of prion diseases. J Neuropathol Exp Neurol 2012 0.86
46 Identification of I137M and other mutations that modulate incubation periods for two human prion strains. J Virol 2012 0.86
47 Chimeric elk/mouse prion proteins in transgenic mice. J Gen Virol 2012 0.85
48 Behavioral variant frontotemporal dementia with corticobasal degeneration pathology: phenotypic comparison to bvFTD with Pick's disease. J Mol Neurosci 2011 0.83
49 Prion and doppel proteins bind to granule cells of the cerebellum. Proc Natl Acad Sci U S A 2002 0.82
50 Pathologic evidence that the T188R mutation in PRNP is associated with prion disease. J Neuropathol Exp Neurol 2010 0.80
51 Sporadic Jakob-Creutzfeldt disease presenting as primary progressive aphasia. JAMA Neurol 2013 0.79
52 Levels of the Mahogunin Ring Finger 1 E3 ubiquitin ligase do not influence prion disease. PLoS One 2013 0.79
53 Human growth hormone-related iatrogenic Creutzfeldt-Jakob disease with abnormal imaging. Arch Neurol 2006 0.78
54 Pharmacokinetics of quinacrine efflux from mouse brain via the P-glycoprotein efflux transporter. PLoS One 2012 0.77
55 Changes in neuropeptide expression in mice infected with prions. Neurobiol Aging 2006 0.76
56 Seizures in corticobasal degeneration: a case report. Neurocase 2009 0.75
57 Autobiography Series: From Sleep-Wake Mechanisms to Prion Diseases. J Neuropathol Exp Neurol 2017 0.75