Published in J Inherit Metab Dis on January 16, 2008
Oxidative damage to nucleic acids in severe emphysema. Chest (2008) 1.10
Selenoprotein S/SEPS1 modifies endoplasmic reticulum stress in Z variant alpha1-antitrypsin deficiency. J Biol Chem (2009) 1.01
Antisense oligonucleotide treatment ameliorates alpha-1 antitrypsin-related liver disease in mice. J Clin Invest (2013) 0.94
The prevalence of alpha-1 antitrypsin deficiency in Ireland. Respir Res (2011) 0.93
Rapamycin reduces intrahepatic alpha-1-antitrypsin mutant Z protein polymers and liver injury in a mouse model. Exp Biol Med (Maywood) (2010) 0.93
The impact of surfactant protein-A on ozone-induced changes in the mouse bronchoalveolar lavage proteome. Proteome Sci (2009) 0.85
Z α-1 antitrypsin deficiency and the endoplasmic reticulum stress response. World J Gastrointest Pharmacol Ther (2010) 0.83
Gene targeted therapeutics for liver disease in alpha-1 antitrypsin deficiency. Biologics (2009) 0.82
How Can We Improve the Detection of Alpha1-Antitrypsin Deficiency? PLoS One (2015) 0.80
α1-antitrypsin modulates microglial-mediated neuroinflammation and protects microglial cells from amyloid-β-induced toxicity. J Neuroinflammation (2014) 0.78
Proteomic changes of alveolar lining fluid in illnesses associated with exposure to inhaled non-infectious microbial particles. PLoS One (2014) 0.77
Effect of hypoxia on lung gene expression and proteomic profile: insights into the pulmonary surfactant response. J Proteomics (2014) 0.77
Novel class of potential therapeutics that target ricin retrograde translocation. Toxins (Basel) (2013) 0.76
Gene Therapy for Alpha-1 Antitrypsin Deficiency Lung Disease. Ann Am Thorac Soc (2016) 0.75
Global strategy for the diagnosis, management, and prevention of chronic obstructive pulmonary disease. NHLBI/WHO Global Initiative for Chronic Obstructive Lung Disease (GOLD) Workshop summary. Am J Respir Crit Care Med (2001) 27.83
XBP1 mRNA is induced by ATF6 and spliced by IRE1 in response to ER stress to produce a highly active transcription factor. Cell (2001) 18.68
Functional and genomic analyses reveal an essential coordination between the unfolded protein response and ER-associated degradation. Cell (2000) 13.44
Perk is essential for translational regulation and cell survival during the unfolded protein response. Mol Cell (2000) 11.09
Transcriptional and translational control in the Mammalian unfolded protein response. Annu Rev Cell Dev Biol (2002) 6.48
ER stress and the unfolded protein response. Mutat Res (2005) 6.43
The mechanism of Z alpha 1-antitrypsin accumulation in the liver. Nature (1992) 5.71
Tripartite management of unfolded proteins in the endoplasmic reticulum. Cell (2000) 5.56
Cirrhosis associated with alpha-1-antitrypsin deficiency: a previously unrecognized inherited disorder. J Lab Clin Med (1969) 5.40
A time-dependent phase shift in the mammalian unfolded protein response. Dev Cell (2003) 4.99
Translational control in the endoplasmic reticulum stress response. J Clin Invest (2002) 4.56
Liver disease in alpha1-antitrypsin deficiency detected by screening of 200,000 infants. N Engl J Med (1976) 4.39
ER quality control: the cytoplasmic connection. Cell (1997) 4.01
PULMONARY EMPHYSEMA AND ALPHA1-ANTITRYPSIN DEFICIENCY. Acta Med Scand (1964) 3.93
Two distinct stress signaling pathways converge upon the CHOP promoter during the mammalian unfolded protein response. J Mol Biol (2002) 3.87
Activating transcription factor 3 is integral to the eukaryotic initiation factor 2 kinase stress response. Mol Cell Biol (2004) 3.57
EDEM as an acceptor of terminally misfolded glycoproteins released from calnexin. Science (2003) 3.28
Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency. Proc Natl Acad Sci U S A (2000) 3.17
Replacement therapy for alpha 1-antitrypsin deficiency associated with emphysema. N Engl J Med (1987) 2.81
Sustained secretion of human alpha-1-antitrypsin from murine muscle transduced with adeno-associated virus vectors. Proc Natl Acad Sci U S A (1998) 2.80
Mutation of antitrypsin to antithrombin. alpha 1-antitrypsin Pittsburgh (358 Met leads to Arg), a fatal bleeding disorder. N Engl J Med (1983) 2.36
Alpha 1-antitrypsin deficiency, emphysema, and liver disease. Genetic basis and strategies for therapy. J Clin Invest (1990) 2.35
Alpha1-antitrypsin deficiency--a model for conformational diseases. N Engl J Med (2002) 2.11
Worldwide racial and ethnic distribution of alpha1-antitrypsin deficiency: summary of an analysis of published genetic epidemiologic surveys. Chest (2002) 2.10
The electrophoretic α1-globulin pattern of serum in α1-antitrypsin deficiency. 1963. COPD (2013) 2.06
Alpha-1-antitrypsin deficiency: a new paradigm for hepatocellular carcinoma in genetic liver disease. Hepatology (2005) 2.05
The liver in adolescents with alpha 1-antitrypsin deficiency. Hepatology (1995) 1.95
Accumulation of mutant alpha1-antitrypsin Z in the endoplasmic reticulum activates caspases-4 and -12, NFkappaB, and BAP31 but not the unfolded protein response. J Biol Chem (2005) 1.93
Alpha 1 antitrypsin deficiency: the clinical and physiological features of pulmonary emphysema in subjects homozygous for Pi type Z. A survey by the British Thoracic Association. Br J Dis Chest (1983) 1.91
Z alpha1-antitrypsin polymerizes in the lung and acts as a neutrophil chemoattractant. Chest (2004) 1.88
Enhancement of endoplasmic reticulum (ER) degradation of misfolded Null Hong Kong alpha1-antitrypsin by human ER mannosidase I. J Biol Chem (2003) 1.86
ONO-5046, a novel inhibitor of human neutrophil elastase. Biochem Biophys Res Commun (1991) 1.85
Liver injury in alpha1-antitrypsin deficiency: an aggregated protein induces mitochondrial injury. J Clin Invest (2002) 1.84
Retention of mutant alpha(1)-antitrypsin Z in endoplasmic reticulum is associated with an autophagic response. Am J Physiol Gastrointest Liver Physiol (2000) 1.83
Alpha 1-antitrypsin deficiency in Europe: geographical distribution of Pi types S and Z. Respir Med (1998) 1.73
The isolation of a clone for human alpha 1-antitrypsin and the detection of alpha 1-antitrypsin in mRNA from liver and leukocytes. Biochem Biophys Res Commun (1983) 1.62
alpha 1-Antitrypsin: molecular pathology, leukocytes, and tissue damage. J Clin Invest (1986) 1.61
Clinical features and history of the destructive lung disease associated with alpha-1-antitrypsin deficiency of adults with pulmonary symptoms. Am Rev Respir Dis (1988) 1.58
Antineutrophil cytoplasmic antibodies induce monocyte IL-8 release. Role of surface proteinase-3, alpha1-antitrypsin, and Fcgamma receptors. J Clin Invest (1997) 1.55
Activation of endoplasmic reticulum-specific stress responses associated with the conformational disease Z alpha 1-antitrypsin deficiency. J Immunol (2004) 1.53
The proteasome participates in degradation of mutant alpha 1-antitrypsin Z in the endoplasmic reticulum of hepatoma-derived hepatocytes. J Biol Chem (2001) 1.49
Lung polymers in Z alpha1-antitrypsin deficiency-related emphysema. Am J Respir Cell Mol Biol (1998) 1.47
Variability of pulmonary function in alpha-1-antitrypsin deficiency: clinical correlates. Ann Intern Med (1989) 1.41
Multiple tissues express alpha 1-antitrypsin in transgenic mice and man. J Clin Invest (1988) 1.34
Mutants of neuroserpin that cause dementia accumulate as polymers within the endoplasmic reticulum. J Biol Chem (2004) 1.33
High level expression of active human alpha-1-antitrypsin in the milk of transgenic sheep. Biotechnology (N Y) (1991) 1.32
Mitochondrial autophagy and injury in the liver in alpha 1-antitrypsin deficiency. Am J Physiol Gastrointest Liver Physiol (2003) 1.31
6-mer peptide selectively anneals to a pathogenic serpin conformation and blocks polymerization. Implications for the prevention of Z alpha(1)-antitrypsin-related cirrhosis. J Biol Chem (2001) 1.31
A pilot study of all-trans-retinoic acid for the treatment of human emphysema. Am J Respir Crit Care Med (2002) 1.28
Chromosomal localization of the human alpha 1-antitrypsin gene (PI) to 14q31-32. Am J Hum Genet (1985) 1.26
Alpha1-antitrypsin deficiency in 26-year-old subjects: lung, liver, and protease/protease inhibitor studies. Chest (2005) 1.24
Cell-specific expression of alpha 1-antitrypsin in human intestinal epithelium. J Clin Invest (1993) 1.23
Prevention of polymerization of M and Z alpha1-Antitrypsin (alpha1-AT) with trimethylamine N-oxide. Implications for the treatment of alpha1-at deficiency. Am J Respir Cell Mol Biol (2001) 1.17
Outcome of liver disease associated with alpha 1 antitrypsin deficiency (PiZ). Implications for genetic counselling and antenatal diagnosis. Arch Dis Child (1983) 1.17
Grp78, Grp94, and Grp170 interact with alpha1-antitrypsin mutants that are retained in the endoplasmic reticulum. Am J Physiol Gastrointest Liver Physiol (2005) 1.14
Synthetic inhibitors of elastase. Med Res Rev (1994) 1.14
Anti-neutrophil-elastase defenses of the lower respiratory tract in alpha 1-antitrypsin deficiency directly augmented with an aerosol of alpha 1-antitrypsin. Ann Intern Med (1989) 1.12
Prenatal diagnosis of alpha 1 antitrypsin deficiency and estimates of fetal risk for disease. J Med Genet (1987) 1.07
Fasting in alpha1-antitrypsin deficient liver: constitutive [correction of consultative] activation of autophagy. Am J Physiol Gastrointest Liver Physiol (2002) 1.06
Serum alpha 1-antitrypsin deficiency associated with the common S-type (Glu264----Val) mutation results from intracellular degradation of alpha 1-antitrypsin prior to secretion. J Biol Chem (1989) 1.06
Role of ubiquitin in proteasomal degradation of mutant alpha(1)-antitrypsin Z in the endoplasmic reticulum. Am J Physiol Gastrointest Liver Physiol (2000) 1.06
DeltaF508-CFTR causes constitutive NF-kappaB activation through an ER-overload response in cystic fibrosis lungs. Biol Chem (2002) 1.05
Inhibition of lipopolysaccharide-mediated human monocyte activation, in vitro, by alpha1-antitrypsin. Biochem Biophys Res Commun (2004) 1.04
The unfolded protein response is involved in the pathology of Alzheimer's disease. Ann N Y Acad Sci (2002) 1.04
Factors associated with advanced liver disease in adults with alpha1-antitrypsin deficiency. Clin Gastroenterol Hepatol (2005) 1.04
In vivo post-transcriptional gene silencing of alpha-1 antitrypsin by adeno-associated virus vectors expressing siRNA. Lab Invest (2007) 1.03
Targeting a surface cavity of alpha 1-antitrypsin to prevent conformational disease. J Biol Chem (2003) 1.02
Assignment of human alpha 1-antitrypsin to chromosome 14 by somatic cell hybrid analysis. Proc Natl Acad Sci U S A (1982) 1.01
Augmentation of lung antineutrophil elastase capacity with recombinant human alpha-1-antitrypsin. J Appl Physiol (1985) (1987) 0.99
Heterozygous alpha-I antitrypsin deficiency as a co-factor in the development of chronic liver disease: a review. Neth J Med (2007) 0.98
Inhibition of intracellular degradation increases secretion of a mutant form of alpha1-antitrypsin associated with profound deficiency. J Clin Invest (1998) 0.98
Tauroursodeoxycholic acid inhibits apoptosis induced by Z alpha-1 antitrypsin via inhibition of Bad. Hepatology (2007) 0.95
A review of alpha-1 antitrypsin deficiency. Semin Respir Crit Care Med (2005) 0.94
Late manifestation of chronic liver disease in adults with alpha-1-antitrypsin deficiency. Dig Dis Sci (1987) 0.93
Alpha 1-antitrypsin deficiency: the radiological features of pulmonary emphysema in subjects of Pi type Z and Pi type SZ: a survey by the British Thoracic Association. Clin Radiol (1982) 0.93
Detection of circulating and endothelial cell polymers of Z and wild type alpha 1-antitrypsin by a monoclonal antibody. J Biol Chem (2002) 0.93
Respiratory symptoms and lung function in young adults with severe alpha(1)-antitrypsin deficiency (PiZZ). Thorax (2002) 0.93
Heterozygous alpha 1-antitrypsin phenotypes in patients with end stage liver disease. Am J Gastroenterol (1997) 0.92
Glucosidase and mannosidase inhibitors mediate increased secretion of mutant alpha1 antitrypsin Z. J Biol Chem (2000) 0.92
Serine protease inhibitors in patients with chronic viral hepatitis. J Hepatol (1997) 0.92
Aerosolized hyaluronic acid decreases alveolar injury induced by human neutrophil elastase. Proc Soc Exp Biol Med (1998) 0.92
Long-term follow-up of a cohort of children with alpha-1-antitrypsin deficiency. J Pediatr (1990) 0.92
High prevalence of viral infection in adults with homozygous and heterozygous alpha 1-antitrypsin deficiency and chronic liver disease. Ann Intern Med (1992) 0.91
Strategies for aerosol therapy of alpha 1-antitrypsin deficiency by the aerosol route. Lung (1990) 0.90
High resolution computed tomography (HRCT) in emphysema associated with alpha-1-antitrypsin deficiency. Clin Radiol (1992) 0.89
MR889, a neutrophil elastase inhibitor, in patients with chronic obstructive pulmonary disease: a double-blind, randomized, placebo-controlled clinical trial. Eur Respir J (1996) 0.89
In-frame single codon deletion in the Mmalton deficiency allele of alpha 1-antitrypsin. Am J Hum Genet (1989) 0.89
The relationship of chronic sputum expectoration to physiologic, radiologic, and health status characteristics in alpha(1)-antitrypsin deficiency (PiZ). Chest (2002) 0.87
Lung neutrophil burden correlates with increased pro-inflammatory cytokines and decreased lung function in individuals with alpha(1)-antitrypsin deficiency Chest (2000) 0.86
Expression of hereditary hemochromatosis C282Y HFE protein in HEK293 cells activates specific endoplasmic reticulum stress responses. BMC Cell Biol (2007) 0.86
Modulation of airspace enlargement in elastase-induced emphysema by intratracheal instillment of hyaluronidase and hyaluronic acid. Exp Lung Res (1995) 0.85
Ribozyme-mediated specific gene replacement of the alpha1-antitrypsin gene in human hepatoma cells. J Hepatol (1999) 0.85
Frequency and significance of phenotypes for alpha1-antitrypsin deficiency in type 1 autoimmune hepatitis. Dig Dis Sci (1998) 0.85
Variable degree of liver involvement in siblings with PiZZ alpha-1-antitrypsin deficiency-related liver disease. J Pediatr Gastroenterol Nutr (2006) 0.84
Inhibition of neutrophil serine proteinases by suramin. J Biol Chem (1997) 0.83
Vitamin E deficiency in adults with chronic liver disease. Am J Clin Nutr (1985) 0.83
Recombinant adeno-associated virus gene therapy for cystic fibrosis and alpha(1)-antitrypsin deficiency. Chest (2002) 0.82
Heterozygous MZ alpha-1-antitrypsin deficiency in adults with chronic liver disease. Scand J Gastroenterol (1990) 0.81
Does alpha1-antitrypsin phenotype PiMZ increase the risk of fibrosis in liver disease due to hepatitis C virus infection? Eur J Gastroenterol Hepatol (2006) 0.81
Iodination of proteins, glycoproteins, and peptides using a solid-phase oxidizing agent, 1,3,4,6-tetrachloro-3 alpha,6 alpha-diphenyl glycoluril (Iodogen). Anal Biochem (1981) 5.49
On the structure of rhinovirus 1A. Virology (1971) 4.57
Administration of an adenovirus containing the human CFTR cDNA to the respiratory tract of individuals with cystic fibrosis. Nat Genet (1994) 4.40
Case-control study of infections with Salmonella enteritidis phage type 4 in England. BMJ (1989) 3.79
An extremely luminous panchromatic outburst from the nucleus of a distant galaxy. Science (2011) 3.09
Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line. J Clin Invest (1992) 2.62
A preliminary study of aerosolized recombinant human deoxyribonuclease I in the treatment of cystic fibrosis. N Engl J Med (1992) 2.57
Protease-antiprotease imbalance in the lungs of children with cystic fibrosis. Am J Respir Crit Care Med (1994) 2.26
Alternative lengthening of telomeres and survival in patients with glioblastoma multiforme. Lancet (2003) 2.26
Monoclonal antibodies to three non-glycosylated antigens of herpes simplex virus type 2. J Gen Virol (1982) 2.23
Physical and genetic analysis of cosmids from the vicinity of the cystic fibrosis locus. Nucleic Acids Res (1987) 2.16
Specific interaction between HPV-16 E1-E4 and cytokeratins results in collapse of the epithelial cell intermediate filament network. Nature (1991) 2.09
Isolation of a new DNA marker in linkage disequilibrium with cystic fibrosis, situated between J3.11 (D7S8) and IRP. Am J Hum Genet (1989) 1.97
Systemic deficiency of glutathione in cystic fibrosis. J Appl Physiol (1985) (1993) 1.88
Oxidation of either methionine 351 or methionine 358 in alpha 1-antitrypsin causes loss of anti-neutrophil elastase activity. J Biol Chem (2000) 1.82
Prepared for internship? Ir Med J (2009) 1.74
Quantitative determination of reducing sugars, oligosaccharides, and glycoproteins with (3H)borohydride. Anal Biochem (1973) 1.72
Subarachnoid hemorrhage due to late recurrence of a previously unruptured aneurysm after complete endovascular occlusion. AJNR Am J Neuroradiol (1999) 1.63
A case of Lassa fever: experience at St Thomas's Hospital. Br Med J (Clin Res Ed) (1982) 1.59
Frontotemporal dementia presenting as schizophrenia-like psychosis in young people: clinicopathological series and review of cases. Br J Psychiatry (2009) 1.55
Second to fourth digit ratio (2D:4D), breast cancer risk factors, and breast cancer risk: a prospective cohort study. Br J Cancer (2012) 1.55
Expression of HCLCA1 in cystic fibrosis lungs is associated with mucus overproduction. Eur Respir J (2004) 1.54
PHLS overview of communicable diseases 1997: results of a priority setting exercise. Commun Dis Rep CDR Suppl (1998) 1.54
Two outbreaks of Salmonella enteritidis phage type 4 infection associated with the consumption of fresh shell-egg products. Epidemiol Infect (1989) 1.52
Renal functional reserve in patients with severe chronic obstructive pulmonary disease. Thorax (1997) 1.51
PHLS overview of communicable diseases 1999. Commun Dis Public Health (2001) 1.47
Intracranial 4D flow MRI: toward individualized assessment of arteriovenous malformation hemodynamics and treatment-induced changes. AJNR Am J Neuroradiol (2013) 1.46
Evidence of ambiguous processing and selective degradation in the noncapsid proteins of rhinovirus 1A. J Virol (1976) 1.43
A national outbreak of Salmonella typhimurium DT 124 caused by contaminated salami sticks. Epidemiol Infect (1989) 1.43
A large outbreak of food poisoning of unknown aetiology associated with Stilton cheese. Epidemiol Infect (1991) 1.41
Interleukin-8 up-regulation by neutrophil elastase is mediated by MyD88/IRAK/TRAF-6 in human bronchial epithelium. J Biol Chem (2001) 1.41
Large outbreak of food poisoning caused by Salmonella typhimurium definitive type 49 in mayonnaise. BMJ (1989) 1.34
Modification of nasal epithelial potential differences of individuals with cystic fibrosis consequent to local administration of a normal CFTR cDNA adenovirus gene transfer vector. Hum Gene Ther (1995) 1.34
Cathepsin B, L, and S cleave and inactivate secretory leucoprotease inhibitor. J Biol Chem (2001) 1.30
Association of IL-10 polymorphism with severity of illness in community acquired pneumonia. Thorax (2003) 1.28
Picornaviral gene order: comparison of a rhinovirus with a cardiovirus. J Virol (1973) 1.24
Montelukast versus salmeterol in patients with asthma and exercise-induced bronchoconstriction. Montelukast/Salmeterol Exercise Study Group. J Allergy Clin Immunol (1999) 1.18
Role of IL-18 in CD4+ T lymphocyte activation in sarcoidosis. J Immunol (2000) 1.17
Oral irritant properties of menthol: sensitizing and desensitizing effects of repeated application and cross-desensitization to nicotine. Physiol Behav (2001) 1.16
PHLS overview of communicable diseases 1997: results of a priority setting exercise. Commun Dis Rep CDR Wkly (1998) 1.14
Australia's National Tobacco Campaign. Tob Control (2003) 1.14
Consensus neuropathological diagnosis of common dementia syndromes: testing and standardising the use of multiple diagnostic criteria. Acta Neuropathol (2002) 1.12
The interaction of growth hormone releasing hormone with other hypothalamic hormones on the release of anterior pituitary hormones. Clin Endocrinol (Oxf) (1986) 1.12
Ambient pCO2 modulates intracellular pH, intracellular oxidant generation, and interleukin-8 secretion in human neutrophils. J Leukoc Biol (2002) 1.11
Bronchoscopically administered recombinant human DNase for lobar atelectasis in cystic fibrosis. Pediatr Pulmonol (2001) 1.09
Hereditary diffuse leucoencephalopathy with spheroids. J Neurol Neurosurg Psychiatry (2003) 1.08
Quantitative assessment of the epithelial and inflammatory cell populations in large airways of normals and individuals with cystic fibrosis. Am J Respir Crit Care Med (1996) 1.07
Two outbreaks of Legionnaires' disease in Bolton Health District. Epidemiol Infect (1990) 1.05
Caffeine, performance, and metabolism during repeated Wingate exercise tests. J Appl Physiol (1985) (1998) 1.04
Increased elastase release by CF neutrophils is mediated by tumor necrosis factor-alpha and interleukin-8. Am J Physiol Lung Cell Mol Physiol (2000) 1.03
Alpha-synuclein accumulates in Lewy bodies in Parkinson's disease and dementia with Lewy bodies but not in Alzheimer's disease beta-amyloid plaque cores. Neurosci Lett (1999) 1.03
Comparison of disc diffusion and epsilometer (E-test) testing techniques to determine antimicrobial susceptibility of Campylobacter isolates of food and human clinical origin. J Microbiol Methods (2009) 1.03
Recombinant secretory leukoprotease inhibitor augments glutathione levels in lung epithelial lining fluid. J Appl Physiol (1985) (1993) 1.02
Prediction of heart rate and oxygen uptake during incremental and maximal exercise in healthy adults. Chest (1994) 1.02
Two case reports of pneumomediastinum. Ir J Med Sci (2007) 1.02
Decreased growth of human prostate LNCaP tumors in SCID mice fed a low-fat, soy protein diet with isoflavones. Nutr Cancer (1999) 1.02
Idiopathic hypothalamic dysfunction: a paraneoplastic syndrome? Lancet (1995) 1.01
Stimulation of adrenal mitogenesis by N-terminal proopiocortin peptides. Nature (1982) 1.01
TDP-43 neuropathology is similar in sporadic amyotrophic lateral sclerosis with or without TDP-43 mutations. Neuropathol Appl Neurobiol (2009) 0.99
Campylobacter spp. in Irish feedlot cattle: a longitudinal study involving pre-harvest and harvest phases of the food chain. J Vet Med B Infect Dis Vet Public Health (2004) 0.99
Perivascular T cells express the pro-inflammatory chemokine RANTES mRNA in multiple sclerosis lesions. Scand J Immunol (1997) 0.98
Control of expression of the I factor, a LINE-like transposable element in Drosophila melanogaster. EMBO J (1996) 0.98
IL-6 release and airway administration of human CFR cDNA adenovirus vector. Nat Med (1995) 0.98
Neurobiological and psychophysical mechanisms underlying the oral sensation produced by carbonated water. J Neurosci (1999) 0.97
Alpha1-antitrypsin deficiency: biological answers to clinical questions. Am J Med Sci (2001) 0.97
Angioplasty guidewire velocity: a new simple method to calculate absolute coronary blood velocity and flow. Am J Cardiol (1997) 0.97
Vitamin D receptor agonists inhibit pro-inflammatory cytokine production from the respiratory epithelium in cystic fibrosis. J Cyst Fibros (2011) 0.96
The role of secretory leucoprotease inhibitor in the resolution of inflammatory responses. Biochem Soc Trans (2007) 0.95
Purification and characterization of a gamma-melanotropin precursor from frozen human pituitary glands. Biochem J (1980) 0.95
Reconstructing embedding spaces of coupled dynamical systems from multivariate data. Phys Rev E Stat Nonlin Soft Matter Phys (2002) 0.94
The hydrophobic core sequence modulates the neurotoxic and secondary structure properties of the prion peptide 106-126. J Neurochem (1999) 0.93
The tangible cost implications of a hospital outbreak of multiply-resistant Salmonella. Epidemiol Infect (1989) 0.93
A large outbreak of Salmonella enteritidis phage type 4 associated with eggs from overseas. Epidemiol Infect (1989) 0.93
Glutathione aerosol suppresses lung epithelial surface inflammatory cell-derived oxidants in cystic fibrosis. J Appl Physiol (1985) (1999) 0.93
Organic acids in urine from human newborns. Clin Chem (1976) 0.93
Size at birth and adult fat mass in twin sheep are determined in early gestation. J Physiol (2011) 0.92
5-fluorouracil steady state pharmacokinetics and outcome in patients receiving protracted venous infusion for advanced colorectal cancer. Br J Cancer (2001) 0.92
Amyloidogenicity and neurotoxicity of peptides corresponding to the helical regions of PrP(C). J Neurosci Res (2000) 0.92
Pharmacokinetics of EMLA cream 5% application to oral mucosa. Anesth Prog (1997) 0.92
Recombinant DNA-produced alpha 1-antitrypsin administered by aerosol augments lower respiratory tract antineutrophil elastase defenses in individuals with alpha 1-antitrypsin deficiency. J Clin Invest (1989) 0.91
The effect of capsular polysaccharide and lipopolysaccharide of Bacteroides fragilis on polymorph function and serum killing. J Med Microbiol (1984) 0.91
Plasma leptin in female athletes: relationship with body fat, reproductive, nutritional, and endocrine factors. J Appl Physiol (1985) (2000) 0.91
Pro-gamma-melanocyte-stimulating hormone cleavage in adrenal gland undergoing compensatory growth. Nature (1983) 0.90
Prevalence and risk of Down syndrome in monozygotic and dizygotic multiple pregnancies in Europe: implications for prenatal screening. BJOG (2014) 0.90
Local resection of ampullary adenocarcinomas of the duodenum. ANZ J Surg (2001) 0.90
Contrasting natural histories of thoracic spine pneumatocysts: resolution versus rapid enlargement. Br J Radiol (2011) 0.89
Direct measurement of human plasma corticotropin-releasing hormone by "two-site" immunoradiometric assay. J Clin Endocrinol Metab (1987) 0.89
The development of a radioimmunoassay for Tamm--Horsfall glycoprotein in serum. Biochem J (1980) 0.89
Intravenous recombinant secretory leukoprotease inhibitor augments antineutrophil elastase defense. J Appl Physiol (1985) (1992) 0.89