PubRank

Joseph M Pilewski

Author PubWeight™ 99.07‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 IL-22 mediates mucosal host defense against Gram-negative bacterial pneumonia. Nat Med 2008 9.05
2 Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation. N Engl J Med 2010 6.23
3 Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth-related oncogene-alpha and granulocyte colony-stimulating factor in bronchial epithelium: implications for airway inflammation in cystic fibrosis. J Immunol 2005 3.47
4 Epithelial Na+ channels are fully activated by furin- and prostasin-dependent release of an inhibitory peptide from the gamma-subunit. J Biol Chem 2007 3.09
5 Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation. Thorax 2011 2.84
6 Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis. Nat Chem Biol 2009 2.70
7 Egr-1 regulates autophagy in cigarette smoke-induced chronic obstructive pulmonary disease. PLoS One 2008 2.67
8 Comprehensive gene expression profiles reveal pathways related to the pathogenesis of chronic obstructive pulmonary disease. Proc Natl Acad Sci U S A 2004 2.42
9 Autoantibodies in patients with chronic obstructive pulmonary disease. Am J Respir Crit Care Med 2007 1.94
10 Palliative care and location of death in decedents with idiopathic pulmonary fibrosis. Chest 2015 1.85
11 The epithelial Na+ channel is inhibited by a peptide derived from proteolytic processing of its alpha subunit. J Biol Chem 2006 1.80
12 Airway surface liquid volume regulates ENaC by altering the serine protease-protease inhibitor balance: a mechanism for sodium hyperabsorption in cystic fibrosis. J Biol Chem 2006 1.77
13 Patients with idiopathic pulmonary fibrosis with antibodies to heat shock protein 70 have poor prognoses. Am J Respir Crit Care Med 2013 1.77
14 Activated CD47 promotes pulmonary arterial hypertension through targeting caveolin-1. Cardiovasc Res 2012 1.69
15 SLC26A9 is a constitutively active, CFTR-regulated anion conductance in human bronchial epithelia. J Gen Physiol 2009 1.44
16 Cellular and humoral autoreactivity in idiopathic pulmonary fibrosis. J Immunol 2007 1.39
17 High mortality rates among solid organ transplant recipients infected with extensively drug-resistant Acinetobacter baumannii: using in vitro antibiotic combination testing to identify the combination of a carbapenem and colistin as an effective treatment regimen. Diagn Microbiol Infect Dis 2011 1.38
18 Lung tissues in patients with systemic sclerosis have gene expression patterns unique to pulmonary fibrosis and pulmonary hypertension. Arthritis Rheum 2011 1.33
19 AMPK agonists ameliorate sodium and fluid transport and inflammation in cystic fibrosis airway epithelial cells. Am J Respir Cell Mol Biol 2009 1.27
20 Secreted and transmembrane mucins inhibit gene transfer with AAV4 more efficiently than AAV5. J Biol Chem 2002 1.27
21 Vitamin D3 attenuates Th2 responses to Aspergillus fumigatus mounted by CD4+ T cells from cystic fibrosis patients with allergic bronchopulmonary aspergillosis. J Clin Invest 2010 1.27
22 Prostasin expression is regulated by airway surface liquid volume and is increased in cystic fibrosis. Am J Physiol Lung Cell Mol Physiol 2008 1.21
23 Acute regulation of the epithelial sodium channel in airway epithelia by proteases and trafficking. Am J Respir Cell Mol Biol 2010 1.18
24 Chaperone displacement from mutant cystic fibrosis transmembrane conductance regulator restores its function in human airway epithelia. FASEB J 2008 1.17
25 Insulin-like growth factor-binding protein-5 induces pulmonary fibrosis and triggers mononuclear cellular infiltration. Am J Pathol 2006 1.17
26 c-Cbl facilitates endocytosis and lysosomal degradation of cystic fibrosis transmembrane conductance regulator in human airway epithelial cells. J Biol Chem 2010 1.15
27 Defining an inhibitory domain in the alpha-subunit of the epithelial sodium channel. Am J Physiol Renal Physiol 2007 1.15
28 Posaconazole serum concentrations among cardiothoracic transplant recipients: factors impacting trough levels and correlation with clinical response to therapy. Antimicrob Agents Chemother 2010 1.15
29 Molecular and functional properties of lung SP cells. Am J Physiol Lung Cell Mol Physiol 2006 1.12
30 Prospective, observational study of voriconazole therapeutic drug monitoring among lung transplant recipients receiving prophylaxis: factors impacting levels of and associations between serum troughs, efficacy, and toxicity. Antimicrob Agents Chemother 2012 1.11
31 CX3CL1 up-regulation is associated with recruitment of CX3CR1+ mononuclear phagocytes and T lymphocytes in the lungs during cigarette smoke-induced emphysema. Am J Pathol 2008 1.06
32 Plasma B lymphocyte stimulator and B cell differentiation in idiopathic pulmonary fibrosis patients. J Immunol 2013 1.05
33 Up-regulation of AMP-activated kinase by dysfunctional cystic fibrosis transmembrane conductance regulator in cystic fibrosis airway epithelial cells mitigates excessive inflammation. J Biol Chem 2005 1.04
34 Hepatocyte growth factor and other fibroblast secretions modulate the phenotype of human bronchial epithelial cells. Am J Physiol Lung Cell Mol Physiol 2007 1.02
35 The HLA class II Allele DRB1*1501 is over-represented in patients with idiopathic pulmonary fibrosis. PLoS One 2011 1.02
36 Experience with immune monitoring in lung transplant recipients: correlation of low immune function with infection. Transplantation 2009 1.01
37 Interleukin-17A induces bicarbonate secretion in normal human bronchial epithelial cells. Am J Physiol Lung Cell Mol Physiol 2008 1.01
38 Selective toxicity of engineered lentivirus lytic peptides in a CF airway cell model. Peptides 2003 1.01
39 Patients with cystic fibrosis have inducible IL-17+IL-22+ memory cells in lung draining lymph nodes. J Allergy Clin Immunol 2012 1.00
40 Postdeposition dispersion of aerosol medications using surfactant carriers. J Aerosol Med Pulm Drug Deliv 2008 0.99
41 Extracorporeal membrane oxygenation for primary graft dysfunction after lung transplantation: long-term survival. Ann Thorac Surg 2009 0.98
42 Successful outcome of human metapneumovirus (hMPV) pneumonia in a lung transplant recipient treated with intravenous ribavirin. J Heart Lung Transplant 2007 0.98
43 Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis. J Cyst Fibros 2012 0.98
44 Localized expression of tenascin in systemic sclerosis-associated pulmonary fibrosis and its regulation by insulin-like growth factor binding protein 3. Arthritis Rheum 2012 0.96
45 Extracorporeal membrane oxygenation as a bridge to lung transplant: midterm outcomes. Ann Thorac Surg 2011 0.95
46 Finally, mice with CF lung disease. Nat Med 2004 0.95
47 Plasma inflammatory mediators associated with bone metabolism in COPD. COPD 2010 0.89
48 Donor smoking history and age in lung transplantation: a revisit. Transplantation 2013 0.88
49 Liquid hyper-absorption as a cause of increased DTPA clearance in the cystic fibrosis airway. EJNMMI Res 2013 0.85
50 Ganciclovir-resistant cytomegalovirus infections among lung transplant recipients are associated with poor outcomes despite treatment with foscarnet-containing regimens. Antimicrob Agents Chemother 2013 0.85
51 Role of insulin-like growth factor binding protein-3 in allergic airway remodeling. Am J Respir Crit Care Med 2009 0.84
52 Staphylococcus aureus infections in the early period after lung transplantation: epidemiology, risk factors, and outcomes. J Heart Lung Transplant 2012 0.84
53 Lobar lung transplantation: a relevant surgical option in the current era of lung allocation score. Ann Thorac Surg 2013 0.83
54 The status of gene therapy for cystic fibrosis. Semin Respir Crit Care Med 2003 0.83
55 Clinical trials of health information technology interventions intended for patient use: unique issues and considerations. Clin Trials 2013 0.83
56 Five-year outcomes with alemtuzumab induction after lung transplantation. J Heart Lung Transplant 2011 0.82
57 Imaging the postdeposition dispersion of an inhaled surfactant aerosol. J Aerosol Med Pulm Drug Deliv 2012 0.82
58 Highly effective cystic fibrosis clinical research teams: critical success factors. J Gen Intern Med 2014 0.80
59 Exploring the meaning of chronic rejection after lung transplantation and its impact on clinical management and caregiving. J Pain Symptom Manage 2010 0.80
60 Syndecan-2 is a novel target of insulin-like growth factor binding protein-3 and is over-expressed in fibrosis. PLoS One 2012 0.80
61 Comprehensive analysis of gene expression on GOLD-2 Versus GOLD-0 smokers reveals novel genes important in the pathogenesis of COPD. Proc Am Thorac Soc 2006 0.80
62 Effect of apical hyperosmotic sodium challenge and amiloride on sodium transport in human bronchial epithelial cells from cystic fibrosis donors. Am J Physiol Cell Physiol 2013 0.79
63 Early major neurologic complications after lung transplantation: incidence, risk factors, and outcome. Transplantation 2013 0.79
64 Nature and correlates of post-traumatic stress symptomatology in lung transplant recipients. J Heart Lung Transplant 2013 0.78
65 Intrapulmonary disposition of amphotericin B after aerosolized delivery of amphotericin B lipid complex (Abelcet; ABLC) in lung transplant recipients. Transplantation 2010 0.78
66 Elevated CXCL10 (IP-10) in bronchoalveolar lavage fluid is associated with acute cellular rejection after human lung transplantation. Transplantation 2014 0.77
67 Lung transplantation with lungs from older donors: recipient and surgical factors affect outcomes. Transplantation 2014 0.77
68 Lung transplantation for pulmonary hypertension. Pulm Circ 2011 0.77
69 Psychiatric Predictors of Long-term Transplant-Related Outcomes in Lung Transplant Recipients. Transplantation 2016 0.77
70 A polymorphism linked to elevated levels of interferon-γ is associated with an increased risk of cytomegalovirus disease among Caucasian lung transplant recipients at a single center. J Heart Lung Transplant 2011 0.77
71 Post-transplant colonization with non-Aspergillus molds and risk of development of invasive fungal disease in lung transplant recipients. J Heart Lung Transplant 2008 0.76
72 Lung transplantation after lung volume reduction surgery. Transplantation 2013 0.76
73 Cystic fibrosis: recent successes present new challenges. Ann Intern Med 2014 0.75
74 Gastrin-releasing peptide receptor expression in non-cancerous bronchial epithelia is associated with lung cancer: a case-control study. Respir Res 2012 0.75
75 Does simultaneous lung-liver transplantation provide an immunologic advantage compared with isolated lung transplantation? J Thorac Cardiovasc Surg 2011 0.75
76 Surgical Strategy for Lung Transplantation in Adults With Small Chests: Lobar Transplant Versus a Pediatric Donor. Transplantation 2016 0.75