PubRank

Eleonora Aronica

Author PubWeight™ 148.76‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 The clinicopathologic spectrum of focal cortical dysplasias: a consensus classification proposed by an ad hoc Task Force of the ILAE Diagnostic Methods Commission. Epilepsia 2010 6.23
2 Toll-like receptor 4 and high-mobility group box-1 are involved in ictogenesis and can be targeted to reduce seizures. Nat Med 2010 4.61
3 Detection of human papillomavirus in human focal cortical dysplasia type IIB. Ann Neurol 2012 3.71
4 Innate and adaptive immunity during epileptogenesis and spontaneous seizures: evidence from experimental models and human temporal lobe epilepsy. Neurobiol Dis 2007 2.81
5 tRNA splicing endonuclease mutations cause pontocerebellar hypoplasia. Nat Genet 2008 2.28
6 Intramuscular administration of AAV1-lipoprotein lipase S447X lowers triglycerides in lipoprotein lipase-deficient patients. Arterioscler Thromb Vasc Biol 2008 2.10
7 New autopsy findings in different brain regions of a preterm neonate with kernicterus: neurovascular alterations and up-regulation of efflux transporters. Pediatr Neurol 2013 2.01
8 Potential new antiepileptogenic targets indicated by microarray analysis in a rat model for temporal lobe epilepsy. J Neurosci 2006 1.88
9 mTOR cascade activation distinguishes tubers from focal cortical dysplasia. Ann Neurol 2004 1.85
10 International consensus classification of hippocampal sclerosis in temporal lobe epilepsy: a Task Force report from the ILAE Commission on Diagnostic Methods. Epilepsia 2013 1.82
11 A ketogenic diet suppresses seizures in mice through adenosine A₁ receptors. J Clin Invest 2011 1.79
12 Embryonal tumor with abundant neuropil and true rosettes (ETANTR), ependymoblastoma, and medulloepithelioma share molecular similarity and comprise a single clinicopathological entity. Acta Neuropathol 2013 1.68
13 Epilepsy and brain inflammation. Exp Neurol 2011 1.67
14 Induction of Dickkopf-1, a negative modulator of the Wnt pathway, is associated with neuronal degeneration in Alzheimer's brain. J Neurosci 2004 1.66
15 Neuronal cell death in a rat model for mesial temporal lobe epilepsy is induced by the initial status epilepticus and not by later repeated spontaneous seizures. Epilepsia 2003 1.60
16 MicroRNA-146a: a key regulator of astrocyte-mediated inflammatory response. PLoS One 2012 1.59
17 Fractalkine/CX3CL1 modulates GABAA currents in human temporal lobe epilepsy. Epilepsia 2013 1.50
18 T-cell-mediated inflammatory activity in the stellate ganglia of patients with ion-channel disease and severe ventricular arrhythmias. Circ Arrhythm Electrophysiol 2014 1.45
19 Limbic seizures induce P-glycoprotein in rodent brain: functional implications for pharmacoresistance. J Neurosci 2002 1.44
20 Biallelic TSC gene inactivation in tuberous sclerosis complex. Neurology 2010 1.39
21 Glia as a source of cytokines: implications for neuronal excitability and survival. Epilepsia 2008 1.38
22 Pontocerebellar hypoplasia type 2: a neuropathological update. Acta Neuropathol 2007 1.32
23 Epilepsy in patients with a brain tumour: focal epilepsy requires focused treatment. Brain 2011 1.28
24 Expression and distribution of id helix-loop-helix proteins in human astrocytic tumors. Glia 2002 1.20
25 Malformations of cortical development and epilepsies: neuropathological findings with emphasis on focal cortical dysplasia. Epileptic Disord 2009 1.20
26 Immune responses to intramuscular administration of alipogene tiparvovec (AAV1-LPL(S447X)) in a phase II clinical trial of lipoprotein lipase deficiency gene therapy. Hum Gene Ther 2014 1.19
27 Astrocytes produce interferon-alpha and CXCL10, but not IL-6 or CXCL8, in Aicardi-Goutières syndrome. Glia 2008 1.18
28 Evaluation of the innate and adaptive immunity in type I and type II focal cortical dysplasias. Epilepsia 2010 1.17
29 Inhibition of the multidrug transporter P-glycoprotein improves seizure control in phenytoin-treated chronic epileptic rats. Epilepsia 2006 1.17
30 Retinoic acid induces blood-brain barrier development. J Neurosci 2013 1.17
31 Decreased numbers of progenitor cells but no response to antidepressant drugs in the hippocampus of elderly depressed patients. Neuropharmacology 2010 1.16
32 Activation of Toll-like receptor, RAGE and HMGB1 signalling in malformations of cortical development. Brain 2011 1.16
33 Inhibition of mammalian target of rapamycin reduces epileptogenesis and blood-brain barrier leakage but not microglia activation. Epilepsia 2012 1.15
34 Induction of the Wnt inhibitor, Dickkopf-1, is associated with neurodegeneration related to temporal lobe epilepsy. Epilepsia 2007 1.14
35 LIN28A immunoreactivity is a potent diagnostic marker of embryonal tumor with multilayered rosettes (ETMR). Acta Neuropathol 2012 1.12
36 Gene expression analysis of tuberous sclerosis complex cortical tubers reveals increased expression of adhesion and inflammatory factors. Brain Pathol 2009 1.12
37 Neuroinflammation in delirium: a postmortem case-control study. Rejuvenation Res 2011 1.11
38 EZH2-regulated DAB2IP is a medulloblastoma tumor suppressor and a positive marker for survival. Clin Cancer Res 2012 1.10
39 Long-term epilepsy-associated tumors. Brain Pathol 2012 1.10
40 Decreased expression of synaptic vesicle protein 2A, the binding site for levetiracetam, during epileptogenesis and chronic epilepsy. Epilepsia 2008 1.07
41 Developmental lineage of cell types in cortical dysplasia with balloon cells. Brain 2007 1.07
42 Mouse models to study the effect of cardiovascular risk factors on brain structure and cognition. J Cereb Blood Flow Metab 2013 1.06
43 Pharmacological activation of mGlu4 metabotropic glutamate receptors inhibits the growth of medulloblastomas. J Neurosci 2006 1.06
44 Phosphoinositide 3-kinases upregulate system xc(-) via eukaryotic initiation factor 2α and activating transcription factor 4 - A pathway active in glioblastomas and epilepsy. Antioxid Redox Signal 2014 1.05
45 SGCE isoform characterization and expression in human brain: implications for myoclonus-dystonia pathogenesis? Eur J Hum Genet 2010 1.05
46 ALS-associated mutations in FUS disrupt the axonal distribution and function of SMN. Hum Mol Genet 2013 1.04
47 COX-2 inhibition controls P-glycoprotein expression and promotes brain delivery of phenytoin in chronic epileptic rats. Neuropharmacology 2009 1.03
48 Metabotropic glutamate receptors in glial cells. Neurochem Res 2008 1.02
49 Clinicopathological and immunohistochemical findings in an autopsy case of tuberous sclerosis complex. Neuropathology 2008 0.99
50 DNA polymerase-beta is expressed early in neurons of Alzheimer's disease brain and is loaded into DNA replication forks in neurons challenged with beta-amyloid. J Neurosci 2006 0.99
51 Group I metabotropic glutamate receptors: a role in neurodevelopmental disorders? Mol Neurobiol 2007 0.99
52 GFAPdelta in radial glia and subventricular zone progenitors in the developing human cortex. Development 2010 0.98
53 Fetal brain mTOR signaling activation in tuberous sclerosis complex. Cereb Cortex 2012 0.98
54 Cox-2 inhibition can lead to adverse effects in a rat model for temporal lobe epilepsy. Epilepsy Res 2010 0.97
55 Electrocorticography discharge patterns in patients with a cavernous hemangioma and pharmacoresistent epilepsy. J Neurosurg 2007 0.96
56 Progression of temporal lobe epilepsy in the rat is associated with immunocytochemical changes in inhibitory interneurons in specific regions of the hippocampal formation. Exp Neurol 2004 0.95
57 Cytoarchitectural alterations are widespread in cerebral cortex in tuberous sclerosis complex. Acta Neuropathol 2012 0.94
58 Fatal human rabies due to Duvenhage virus from a bat in Kenya: failure of treatment with coma-induction, ketamine, and antiviral drugs. PLoS Negl Trop Dis 2009 0.94
59 The Wnt antagonist, Dickkopf-1, as a target for the treatment of neurodegenerative disorders. Neurochem Res 2008 0.94
60 The application of cortical layer markers in the evaluation of cortical dysplasias in epilepsy. Acta Neuropathol 2010 0.93
61 Early defect of transforming growth factor β1 formation in Huntington's disease. J Cell Mol Med 2011 0.93
62 Blood plasma inflammation markers during epileptogenesis in post-status epilepticus rat model for temporal lobe epilepsy. Epilepsia 2013 0.92
63 Cellular distribution of vascular endothelial growth factor A (VEGFA) and B (VEGFB) and VEGF receptors 1 and 2 in focal cortical dysplasia type IIB. Acta Neuropathol 2008 0.92
64 Early progenitor cell marker expression distinguishes type II from type I focal cortical dysplasias. J Neuropathol Exp Neurol 2010 0.92
65 Cholinergic imbalance in the multiple sclerosis hippocampus. Acta Neuropathol 2011 0.91
66 Fetal brain lesions in tuberous sclerosis complex: TORC1 activation and inflammation. Brain Pathol 2012 0.91
67 A neuropathology-based approach to epilepsy surgery in brain tumors and proposal for a new terminology use for long-term epilepsy-associated brain tumors. Acta Neuropathol 2014 0.91
68 Doublecortin expression in focal cortical dysplasia in epilepsy. Epilepsia 2009 0.91
69 Anomalous levels of Cl- transporters cause a decrease of GABAergic inhibition in human peritumoral epileptic cortex. Epilepsia 2011 0.90
70 Receptor for Advanced Glycation Endproducts is upregulated in temporal lobe epilepsy and contributes to experimental seizures. Neurobiol Dis 2013 0.90
71 Enhanced epidermal growth factor, hepatocyte growth factor, and vascular endothelial growth factor expression in tuberous sclerosis complex. Am J Pathol 2010 0.90
72 Increased expression of ferritin, an iron-storage protein, in specific regions of the parahippocampal cortex of epileptic rats. Epilepsia 2005 0.90
73 Recessive MYL2 mutations cause infantile type I muscle fibre disease and cardiomyopathy. Brain 2013 0.90
74 BRAF V600E mutation is associated with mTOR signaling activation in glioneuronal tumors. Brain Pathol 2013 0.89
75 Spatial and temporal evolution of distal 10q deletion, a prognostically unfavorable event in diffuse low-grade gliomas. Genome Biol 2014 0.89
76 Chronic exposure of astrocytes to interferon-α reveals molecular changes related to Aicardi-Goutieres syndrome. Brain 2013 0.89
77 Pi3K-mTOR signaling and AMOG expression in epilepsy-associated glioneuronal tumors. Brain Pathol 2009 0.89
78 Differential cellular gene expression in ganglioglioma. Epilepsia 2007 0.88
79 Expression of multidrug transporters MRP1, MRP2, and BCRP shortly after status epilepticus, during the latent period, and in chronic epileptic rats. Epilepsia 2005 0.88
80 GABA(A)-current rundown of temporal lobe epilepsy is associated with repetitive activation of GABA(A) "phasic" receptors. Proc Natl Acad Sci U S A 2007 0.88
81 Overexpression of ADK in human astrocytic tumors and peritumoral tissue is related to tumor-associated epilepsy. Epilepsia 2011 0.88
82 Decreased cortical inhibition and yet cerebellar pathology in 'familial cortical myoclonic tremor with epilepsy'. Mov Disord 2007 0.87
83 17beta-estradiol rescues spinal motoneurons from AMPA-induced toxicity: a role for glial cells. Neurobiol Dis 2005 0.87
84 PLEC1 mutations underlie adult-onset dilated cardiomyopathy in epidermolysis bullosa simplex with muscular dystrophy. J Invest Dermatol 2009 0.87
85 Glutamate transporters alterations in the reorganizing dentate gyrus are associated with progressive seizure activity in chronic epileptic rats. J Comp Neurol 2002 0.86
86 Long-lasting increased excitability differs in dentate gyrus vs. CA1 in freely moving chronic epileptic rats after electrically induced status epilepticus. Hippocampus 2002 0.86
87 Glucocorticoid receptor protein expression in human hippocampus; stability with age. Neurobiol Aging 2013 0.85
88 Amyloid beta deregulates astroglial mGluR5-mediated calcium signaling via calcineurin and Nf-kB. Glia 2013 0.85
89 Good interobserver and intraobserver agreement in the evaluation of the new ILAE classification of focal cortical dysplasias. Epilepsia 2012 0.85
90 Expression patterns of synaptic vesicle protein 2A in focal cortical dysplasia and TSC-cortical tubers. Epilepsia 2009 0.85
91 GAP-43 mRNA and protein expression in the hippocampal and parahippocampal region during the course of epileptogenesis in rats. Eur J Neurosci 2003 0.85
92 EXOSC3 mutations in pontocerebellar hypoplasia type 1: novel mutations and genotype-phenotype correlations. Orphanet J Rare Dis 2014 0.84
93 The BH4 domain of Bcl-X(L) rescues astrocyte degeneration in amyotrophic lateral sclerosis by modulating intracellular calcium signals. Hum Mol Genet 2011 0.84
94 Calcium extrusion protein expression in the hippocampal formation of chronic epileptic rats after kainate-induced status epilepticus. Epilepsia 2004 0.84
95 Selective and persistent upregulation of mdr1b mRNA and P-glycoprotein in the parahippocampal cortex of chronic epileptic rats. Epilepsy Res 2004 0.83
96 Differential expression of major histocompatibility complex class I in developmental glioneuronal lesions. J Neuroinflammation 2013 0.83
97 Pre-B-cell leukemia homeobox interacting protein 1 is overexpressed in astrocytoma and promotes tumor cell growth and migration. Neuro Oncol 2014 0.83
98 TPM2 mutation. Neuromuscul Disord 2008 0.83
99 mTOR Hyperactivation in down syndrome hippocampus appears early during development. J Neuropathol Exp Neurol 2014 0.82
100 Prognostic and Therapeutic Markers in Chordomas: A Study of 287 Tumors. J Neuropathol Exp Neurol 2016 0.82
101 Induction of sodium channel Na(x) (SCN7A) expression in rat and human hippocampus in temporal lobe epilepsy. Epilepsia 2010 0.82
102 Isolation of neural progenitor cells from the human adult subventricular zone based on expression of the cell surface marker CD271. Stem Cells Transl Med 2014 0.82
103 Dynamic changes of proteases and protease inhibitors revealed by microarray analysis in CA3 and entorhinal cortex during epileptogenesis in the rat. Epilepsia 2007 0.82
104 Targeted gene expression analysis in hemimegalencephaly: activation of beta-catenin signaling. Brain Pathol 2005 0.82
105 Altered expression of neurotransmitter-receptor subunit and uptake site mRNAs in hemimegalencephaly. Epilepsia 2004 0.82
106 Attenuated AMPA receptor expression allows glioblastoma cell survival in glutamate-rich environment. PLoS One 2009 0.82
107 Atorvastatin treatment during epileptogenesis in a rat model for temporal lobe epilepsy. Epilepsia 2011 0.81
108 GABA-A channel subunit expression in human glioma correlates with tumor histology and clinical outcome. PLoS One 2012 0.81
109 Increased expression of connective tissue growth factor in amyotrophic lateral sclerosis human spinal cord. Acta Neuropathol 2003 0.81
110 The dual role of TNF-α and its receptors in seizures. Exp Neurol 2013 0.81
111 Aberrant expression of miR-218 and miR-204 in human mesial temporal lobe epilepsy and hippocampal sclerosis-convergence on axonal guidance. Epilepsia 2014 0.81
112 Ectopic brain tissue in the orbit: 5-year follow-up. Orbit 2013 0.81
113 Familial cortical tremor with epilepsy and cerebellar pathological findings. Mov Disord 2004 0.80
114 Familial cortical myoclonic tremor with epilepsy and cerebellar changes: description of a new pathology case and review of the literature. Tremor Other Hyperkinet Mov (N Y) 2012 0.80
115 Doublecortin-like (DCL) expression in focal cortical dysplasia and cortical tubers. Epilepsia 2009 0.80
116 Cerebral necrosis after 25Gy radiotherapy in childhood followed 28 years later by 54Gy radiotherapy. Clin Neurol Neurosurg 2007 0.80
117 Expression of synaptic vesicle protein 2A in epilepsy-associated brain tumors and in the peritumoral cortex. Neuro Oncol 2010 0.80
118 Specific human astrocyte subtype revealed by affinity purified GFAP antibody; unpurified serum cross-reacts with neurofilament-L in Alzheimer. PLoS One 2009 0.80
119 Cerebellar axon/myelin loss, angiogenic sprouting, and neuronal increase of vascular endothelial growth factor in a preterm infant with kernicterus. J Child Neurol 2011 0.80
120 Regulation of Kir4.1 expression in astrocytes and astrocytic tumors: a role for interleukin-1 β. J Neuroinflammation 2012 0.79
121 Differential patterns of NOTCH1-4 receptor expression are markers of glioma cell differentiation. Neuro Oncol 2013 0.79
122 Blockage of A2A and A3 adenosine receptors decreases the desensitization of human GABA(A) receptors microtransplanted to Xenopus oocytes. Proc Natl Acad Sci U S A 2009 0.79
123 Basic mechanisms of status epilepticus due to infection and inflammation. Epilepsia 2009 0.79
124 GFAP-Cre-mediated transgenic activation of Bmi1 results in pituitary tumors. PLoS One 2012 0.79
125 Looking ultra deep: short identical sequences and transcriptional slippage. Genomics 2011 0.78
126 Expression and cellular distribution of major vault protein: a putative marker for pharmacoresistance in a rat model for temporal lobe epilepsy. Epilepsia 2004 0.78
127 Correlation between clinical and histologic findings in the human neonatal hippocampus after perinatal asphyxia. J Neuropathol Exp Neurol 2014 0.77
128 Non-neuronal cell responses differ between normal and Down syndrome developing brains. Int J Dev Neurosci 2013 0.77
129 Cell injury and premature neurodegeneration in focal malformations of cortical development. Brain Pathol 2013 0.77
130 DLG3/SAP102 protein expression in malformations of cortical development: a study of human epileptic cortex by tissue microarray. Epilepsy Res 2009 0.77
131 Hippocampal sclerosis. Handb Clin Neurol 2012 0.77
132 Differential distribution of group I metabotropic glutamate receptors in developing human cortex. Brain Res 2010 0.77
133 Rhabdomyolysis in pontocerebellar hypoplasia type 2 (PCH-2). Neuromuscul Disord 2007 0.77
134 Upregulation of neuronal nitric oxide synthase in in vitro stellate astrocytes and in vivo reactive astrocytes after electrically induced status epilepticus. Neurochem Res 2003 0.76
135 Sodium channel beta1-subunit expression is increased in reactive astrocytes in a rat model for mesial temporal lobe epilepsy. Eur J Neurosci 2002 0.76
136 Long intervening non-coding RNA 00320 is human brain-specific and highly expressed in the cortical white matter. Neurogenetics 2015 0.76
137 Deletion of 15q11.2-15q13.1 in isolated human hemimegalencephaly. Acta Neuropathol 2009 0.76
138 Congenital vascular malformations--cerebral lesions differ from extracranial lesions by their immune expression of the glucose transporter protein GLUT1. Clin Neuropathol 2012 0.75