Published in Autophagy on December 01, 2013
Mevalonate Pathway Regulates Cell Size Homeostasis and Proteostasis through Autophagy. Cell Rep (2015) 0.89
Neuroprotective Effect of Simvastatin via Inducing the Autophagy on Spinal Cord Injury in the Rat Model. Biomed Res Int (2015) 0.81
Simvastatin inhibits neural cell apoptosis and promotes locomotor recovery via activation of Wnt/β-catenin signaling pathway after spinal cord injury. J Neurochem (2016) 0.81
Proteomics of rimmed vacuoles define new risk allele in inclusion body myositis. Ann Neurol (2016) 0.77
Study of Autophagy and Microangiopathy in Sural Nerves of Patients with Chronic Idiopathic Axonal Polyneuropathy. PLoS One (2016) 0.77
"Get the Balance Right": Pathological Significance of Autophagy Perturbation in Neuromuscular Disorders. J Neuromuscul Dis (2016) 0.76
Looking at the metabolic consequences of the colchicine-based in vivo autophagic flux assay. Autophagy (2016) 0.75
Fifteen days of 3,200 m simulated hypoxia marginally regulates markers for protein synthesis and degradation in human skeletal muscle. Hypoxia (Auckl) (2016) 0.75
ENabling Reduction of Low-grade Inflammation in SEniors Pilot Study: Concept, Rationale, and Design. J Am Geriatr Soc (2017) 0.75
Guidelines for the use and interpretation of assays for monitoring autophagy. Autophagy (2012) 20.08
Mutations in prion-like domains in hnRNPA2B1 and hnRNPA1 cause multisystem proteinopathy and ALS. Nature (2013) 4.03
Valosin-containing protein (VCP) is required for autophagy and is disrupted in VCP disease. J Cell Biol (2009) 3.50
Impaired protein aggregate handling and clearance underlie the pathogenesis of p97/VCP-associated disease. J Biol Chem (2008) 1.82
Inclusion body myopathy, Paget's disease of the bone and fronto-temporal dementia: a disorder of autophagy. Hum Mol Genet (2010) 1.75
Endolysosomal sorting of ubiquitylated caveolin-1 is regulated by VCP and UBXD1 and impaired by VCP disease mutations. Nat Cell Biol (2011) 1.69
Quantitation of "autophagic flux" in mature skeletal muscle. Autophagy (2010) 1.53
Interaction with polyglutamine aggregates reveals a Q/N-rich domain in TDP-43. J Biol Chem (2010) 1.47
Novel interstitial 2.6 Mb deletion on 9q21 associated with multiple congenital anomalies. Am J Med Genet A (2014) 1.47
Clinical utility of LC3 and p62 immunohistochemistry in diagnosis of drug-induced autophagic vacuolar myopathies: a case-control study. PLoS One (2012) 1.43
Dermatomyositis with inclusion body myositis pathology. Muscle Nerve (2009) 1.39
Exome sequencing reveals DNAJB6 mutations in dominantly-inherited myopathy. Ann Neurol (2012) 1.35
Myosin binding protein C1: a novel gene for autosomal dominant distal arthrogryposis type 1. Hum Mol Genet (2010) 1.32
Rare somatic cells from human breast tissue exhibit extensive lineage plasticity. Proc Natl Acad Sci U S A (2013) 1.31
Inflammatory myopathies with mitochondrial pathology and protein aggregates. J Neurol Sci (2008) 1.28
Quantitation of selective autophagic protein aggregate degradation in vitro and in vivo using luciferase reporters. Autophagy (2009) 1.25
p97/VCP at the intersection of the autophagy and the ubiquitin proteasome system. Autophagy (2010) 1.16
Neuronal activity regulates astrocytic Nrf2 signaling. Proc Natl Acad Sci U S A (2013) 1.13
Hyperammonemia-mediated autophagy in skeletal muscle contributes to sarcopenia of cirrhosis. Am J Physiol Endocrinol Metab (2012) 1.12
Motor neuron involvement in multisystem proteinopathy: implications for ALS. Neurology (2013) 1.08
Complex formation with the Type B gamma-aminobutyric acid receptor affects the expression and signal transduction of the extracellular calcium-sensing receptor. Studies with HEK-293 cells and neurons. J Biol Chem (2007) 1.04
Infant botulism, type F, presenting at 54 hours of life. Pediatr Neurol (2005) 1.02
Prion-like nuclear aggregation of TDP-43 during heat shock is regulated by HSP40/70 chaperones. Hum Mol Genet (2013) 0.99
Acute and bilateral blindness due to optic neuropathy associated with copper deficiency. Arch Neurol (2009) 0.96
mTOR dysfunction contributes to vacuolar pathology and weakness in valosin-containing protein associated inclusion body myopathy. Hum Mol Genet (2012) 0.96
A knock-in mouse model for the R120G mutation of αB-crystallin recapitulates human hereditary myopathy and cataracts. PLoS One (2011) 0.95
Type B gamma-aminobutyric acid receptors modulate the function of the extracellular Ca2+-sensing receptor and cell differentiation in murine growth plate chondrocytes. Endocrinology (2007) 0.95
Comparative utility of LC3, p62 and TDP-43 immunohistochemistry in differentiation of inclusion body myositis from polymyositis and related inflammatory myopathies. Acta Neuropathol Commun (2013) 0.94
Myopathy-causing mutations in an HSP40 chaperone disrupt processing of specific client conformers. J Biol Chem (2014) 0.90
The AMPK β2 subunit is required for energy homeostasis during metabolic stress. Mol Cell Biol (2012) 0.90
Rapamycin-induced autophagy aggravates pathology and weakness in a mouse model of VCP-associated myopathy. Autophagy (2013) 0.87
Mitochondrial pathology in immune and inflammatory myopathies. Curr Opin Rheumatol (2010) 0.87
p62 expression and autophagy in αB-crystallin R120G mutant knock-in mouse model of hereditary cataract. Exp Eye Res (2013) 0.87
Rapamycin nanoparticles target defective autophagy in muscular dystrophy to enhance both strength and cardiac function. FASEB J (2014) 0.84
An aggregation sensing reporter identifies leflunomide and teriflunomide as polyglutamine aggregate inhibitors. Hum Mol Genet (2011) 0.84
LC3 and p62 as diagnostic markers of drug-induced autophagic vacuolar cardiomyopathy: a study of 3 cases. Am J Surg Pathol (2013) 0.81
In vivo kinetic approach reveals slow SOD1 turnover in the CNS. J Clin Invest (2015) 0.81
Axial mitochondrial myopathy in a patient with rapidly progressive adult-onset scoliosis. Acta Neuropathol Commun (2014) 0.78
ATM and GLUT1-S490 phosphorylation regulate GLUT1 mediated transport in skeletal muscle. PLoS One (2013) 0.78
The CHC22 clathrin-GLUT4 transport pathway contributes to skeletal muscle regeneration. PLoS One (2013) 0.78
Analysis of Mll1 deficiency identifies neurogenic transcriptional modules and Brn4 as a factor for direct astrocyte-to-neuron reprogramming. Neurosurgery (2014) 0.78
Molecular basis for vulnerability to mitochondrial and oxidative stress in a neuroendocrine CRI-G1 cell line. PLoS One (2011) 0.77
Reply to Deighton et al.: Neuronal activity regulates distinct antioxidant pathways in neurons and astrocytes. Proc Natl Acad Sci U S A (2014) 0.77
CNS intravascular large cell lymphoma in a patient with autoimmune hemolytic anemia. Neuropathology (2014) 0.75
Quantitation of selective autophagic protein aggregate degradation in vitro and in vivo using luciferase reporters. Autophagy (2010) 0.75
Keap1/Cullin3 Modulates p62/SQSTM1 Activity via UBA Domain Ubiquitination. Cell Rep (2017) 0.75