Published in J Pediatr Gastroenterol Nutr on April 01, 1989
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Recommendations for management of liver and biliary tract disease in cystic fibrosis. Cystic Fibrosis Foundation Hepatobiliary Disease Consensus Group. J Pediatr Gastroenterol Nutr (1999) 1.28
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Evidence for a primary defect of pancreatic HCO3-secretion in cystic fibrosis. Pediatr Res (1982) 1.26
Uncertainty in the diagnosis of cystic fibrosis: possible role of in vivo nasal potential difference measurements. J Pediatr (1998) 1.26
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Use of pancreatic enzyme supplements for patients with cystic fibrosis in the context of fibrosing colonopathy. Consensus Committee. J Pediatr (1995) 1.16
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Late gastrointestinal bleeding and protein loss after distal small-bowel resection in infancy. J Pediatr Gastroenterol Nutr (1989) 1.11
Malnutrition: a cause of elevated sweat chloride concentration. Acta Paediatr Scand (1986) 1.03
Meconium ileus in the absence of cystic fibrosis. Arch Dis Child (1992) 1.03
Lavage treatment of distal intestinal obstruction syndrome in children with cystic fibrosis. Pediatrics (1989) 1.02
The association of cystic fibrosis, gastroesophageal reflux, and reduced pulmonary function. Can Assoc Radiol J (1988) 1.00
Pathogenesis of malnutrition in cystic fibrosis, and its treatment. Clin Nutr (2000) 0.98
Peptic ulcer disease in children: etiology, clinical findings, and clinical course. Pediatrics (1988) 0.96
Colipase and maximally activated pancreatic lipase in normal subjects and patients with steatorrhea. J Clin Invest (1982) 0.93
Isolated congenital lipase-colipase deficiency. Gastroenterology (1984) 0.92
Treatment of vitamin K deficiency in cystic fibrosis: Effectiveness of a daily fat-soluble vitamin combination. J Pediatr (2001) 0.92
Malabsorption of medium-chain triglycerides in infants with cystic fibrosis: correction with pancreatic enzyme supplement. J Pediatr (1980) 0.92
Decline of exocrine pancreatic function in cystic fibrosis patients with pancreatic sufficiency. Pediatr Res (1992) 0.91
The cystic fibrosis gene and resting energy expenditure. J Pediatr (1991) 0.90
Nutritional management of cystic fibrosis. Annu Rev Nutr (1993) 0.90
Steatorrhea and pancreatic insufficiency in Shwachman syndrome. Gastroenterology (1982) 0.89
Pancreatic function testing in cystic fibrosis. J Pediatr Gastroenterol Nutr (1984) 0.89
Pathophysiology of the pancreatic defect in Johanson-Blizzard syndrome: a disorder of acinar development. J Pediatr (1994) 0.89
Serum immunoreactive cationic trypsinogen: a useful indicator of severe exocrine dysfunction in the paediatric patient without cystic fibrosis. Gut (1986) 0.87
Bentiromide test for assessing pancreatic dysfunction using analysis of para-aminobenzoic acid in plasma and urine. Studies in cystic fibrosis and Shwachman's syndrome. Gastroenterology (1985) 0.86
Longitudinal evaluation of serum trypsinogen measurement in pancreatic-insufficient and pancreatic-sufficient patients with cystic fibrosis. J Pediatr (1995) 0.85
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Immunoreactive forms of cationic trypsin in plasma and ascitic fluid of dogs in experimental pancreatitis. Am J Pathol (1981) 0.84
Exocrine pancreatic alterations in long-lived surviving cystic fibrosis mice. Pediatr Res (1996) 0.84
Cystic fibrosis modifier genes related to Pseudomonas aeruginosa infection. Genes Immun (2011) 0.84
Does the Macroduct collection system reliably define sweat chloride concentration in subjects with intermediate results? Clin Biochem (2009) 0.84
Appendicitis in cystic fibrosis. Arch Dis Child (1991) 0.83
Treatment failure in celiac disease due to coexistent exocrine pancreatic insufficiency. Pediatrics (1987) 0.83
Effects of cisapride in patients with cystic fibrosis and distal intestinal obstruction syndrome. J Pediatr (1990) 0.82
Pancreatitis and mutations of the cystic fibrosis gene. N Engl J Med (1998) 0.81
Elevated serum immunoreactive pancreatic cationic trypsinogen in acute malnutrition: evidence of pancreatic damage. J Pediatr (1985) 0.81
Exclusion of linkage of Shwachman-Diamond syndrome to chromosome regions 6q and 12q implicated by a de novo translocation. Am J Med Genet (1999) 0.81
Behçet's syndrome involving the gastrointestinal tract--a diagnostic dilemma in childhood. Pediatr Radiol (1986) 0.80
Segregation analysis in Shwachman-Diamond syndrome: evidence for recessive inheritance. Am J Hum Genet (2000) 0.80
Pancreatic cysts and calcification in cystic fibrosis. Can Assoc Radiol J (1986) 0.80
Radioimmunoassay of active pancreatic enzymes in sera from patients with acute pancreatitis. I. Active carboxypeptidase B. Clin Chem (1985) 0.80
Plasma immunoreactive anionic pancreatic trypsin in cystic fibrosis. J Pediatr Gastroenterol Nutr (1982) 0.79
Biochemical tests in the diagnosis of chronic pancreatitis and in the evaluation of pancreatic insufficiency. Clin Biochem (1993) 0.78
Plasma immunoreactive pancreatic cationic trypsinogen in cystic fibrosis: a sensitive indicator of exocrine pancreatic dysfunction. Pediatr Res (1981) 0.78
Altered PABA pharmacokinetics in cystic fibrosis. Implications for bentiromide test. Dig Dis Sci (1985) 0.78
Challenges in the dietary treatment of cystic fibrosis related diabetes mellitus. Clin Nutr (2000) 0.77
Correlation of intestinal lactulose permeability with exocrine pancreatic dysfunction. J Pediatr (1992) 0.77
Is chymotrypsin output a better diagnostic index than the measurement of chymotrypsin in random stool? Enzyme (1988) 0.76
Cardiac rhabdomyomata and megacystis-microcolon-intestinal hypoperistalsis syndrome. J Med Genet (1991) 0.76
Radiologic manifestations of malabsorption: a nonspecific finding. Pediatrics (1984) 0.76
Synergistic effects of cAMP- and calcium-mediated amylase secretion in isolated pancreatic acini from cystic fibrosis mice. Pediatr Res (1999) 0.76
Outcomes of patients with cystic fibrosis undergoing lung transplantation with and without cystic fibrosis-associated liver cirrhosis. Clin Transplant (2011) 0.75
Abnormalities of circulating immunoreactive pancreatic anionic trypsinogen in cystic fibrosis: an assay artifact due to cross-reacting serum antibodies. Clin Biochem (1986) 0.75
Pancreatic and intestinal dysfunction in cystic fibrosis. Prog Clin Biol Res (1987) 0.75
Stool chymotrypsin activity measured by a spectrophotometric procedure to identify pancreatic disease in infants. Clin Biochem (1986) 0.75
Glycine conjugation of para-aminobenzoic acid (PABA): a quantitative test of liver function. Clin Biochem (1995) 0.75
Effects of food intake and cholecystokinin on plasma trypsinogen levels in dogs. Am J Physiol (1984) 0.75
Postnatal development of the rat exocrine pancreas. I. Alterations in high- and low-affinity cholecystokinin receptors and enzyme secretion. Pancreas (1997) 0.75
Elevated sweat chloride levels in anorexia nervosa. J Pediatr (1986) 0.75
Serial alterations in the forms of immunoreactive pancreatic cationic trypsin in plasma from patients with acute pancreatitis. J Pediatr Gastroenterol Nutr (1985) 0.75
Chronic intussusception due to antral myoepithelioma. J Pediatr Surg (1986) 0.75
The radiologic and endoscopic investigation and etiologic classification of gastritis in children. Can Assoc Radiol J (1990) 0.75
Liquid-chromatographic measurement of p-aminobenzoic acid and its metabolites in serum. Clin Chem (1988) 0.75
Postnatal development of the rat exocrine pancreas. II. Effects of protein-calorie malnutrition on amylase secretion and CCK receptor binding. Pancreas (1997) 0.75
Impact of protein deprivation on protein and DNA synthesis in the developing rat pancreas. Biol Neonate (1998) 0.75