Published in Proc Natl Acad Sci U S A on May 02, 2016
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Developmental alterations in Huntington's disease neural cells and pharmacological rescue in cells and mice. Nat Neurosci (2017) 0.75
Embryonic Mutant Huntingtin Aggregate Formation in Mouse Models of Huntington's Disease. J Huntingtons Dis (2016) 0.75
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Shining a light on early stress responses and late-onset disease vulnerability. Proc Natl Acad Sci U S A (2017) 0.75
Oxidative Stress and Huntington's Disease: The Good, The Bad, and The Ugly. J Huntingtons Dis (2016) 0.75
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Loss of bidirectional striatal synaptic plasticity in L-DOPA-induced dyskinesia. Nat Neurosci (2003) 3.25
Increased sensitivity to N-methyl-D-aspartate receptor-mediated excitotoxicity in a mouse model of Huntington's disease. Neuron (2002) 3.15
Oscillatory entrainment of striatal neurons in freely moving rats. Neuron (2004) 3.11
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Transient and progressive electrophysiological alterations in the corticostriatal pathway in a mouse model of Huntington's disease. J Neurosci (2003) 1.88
Impaired TrkB receptor signaling underlies corticostriatal dysfunction in Huntington's disease. Neuron (2014) 1.72
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Age-dependent alterations of corticostriatal activity in the YAC128 mouse model of Huntington disease. J Neurosci (2009) 1.43
Differential susceptibility to excitotoxic stress in YAC128 mouse models of Huntington disease between initiation and progression of disease. J Neurosci (2009) 1.40
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The mouse beam walking assay offers improved sensitivity over the mouse rotarod in determining motor coordination deficits induced by benzodiazepines. J Psychopharmacol (2005) 1.32
Differential electrophysiological changes in striatal output neurons in Huntington's disease. J Neurosci (2011) 1.27
Decreased neuronal and increased oligodendroglial densities in Huntington's disease caudate nucleus. J Neuropathol Exp Neurol (1991) 1.27
Group I metabotropic glutamate receptor signalling and its implication in neurological disease. CNS Neurol Disord Drug Targets (2010) 1.22
Impairment of developmental stem cell-mediated striatal neurogenesis and pluripotency genes in a knock-in model of Huntington's disease. Proc Natl Acad Sci U S A (2009) 1.17
Marked differences in neurochemistry and aggregates despite similar behavioural and neuropathological features of Huntington disease in the full-length BACHD and YAC128 mice. Hum Mol Genet (2012) 1.15
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Metabotropic glutamate receptor-mediated cell signaling pathways are altered in a mouse model of Huntington's disease. J Neurosci (2010) 1.11
Short latency cerebellar modulation of the basal ganglia. Nat Neurosci (2014) 1.10
Acquired infection with Toxoplasma gondii in adult mice results in sensorimotor deficits but normal cognitive behavior despite widespread brain pathology. Microbes Infect (2010) 1.09
GABAergic circuits control spike-timing-dependent plasticity. J Neurosci (2013) 1.05
Aberrant cortical synaptic plasticity and dopaminergic dysfunction in a mouse model of Huntington's disease. Hum Mol Genet (2006) 1.05
Multiple sources of striatal inhibition are differentially affected in Huntington's disease mouse models. J Neurosci (2013) 1.04
Accurate spike sorting for multi-unit recordings. Eur J Neurosci (2010) 1.01
Loss of corticostriatal and thalamostriatal synaptic terminals precedes striatal projection neuron pathology in heterozygous Q140 Huntington's disease mice. Neurobiol Dis (2013) 0.95
An inexpensive drivable cannulated microelectrode array for simultaneous unit recording and drug infusion in the same brain nucleus of behaving rats. J Neurophysiol (2011) 0.94
Changes in striatal procedural memory coding correlate with learning deficits in a mouse model of Huntington disease. Proc Natl Acad Sci U S A (2011) 0.93
Metabotropic glutamate receptor 5 positive allosteric modulators are neuroprotective in a mouse model of Huntington's disease. Br J Pharmacol (2013) 0.92
Huntington's disease and Group I metabotropic glutamate receptors. Mol Neurobiol (2010) 0.90
Selective loss of bi-directional synaptic plasticity in the direct and indirect striatal output pathways accompanies generation of parkinsonism and l-DOPA induced dyskinesia in mouse models. Neurobiol Dis (2014) 0.88
Unbalance of CB1 receptors expressed in GABAergic and glutamatergic neurons in a transgenic mouse model of Huntington's disease. Neurobiol Dis (2011) 0.88
Loss of mRNA levels, binding and activation of GTP-binding proteins for cannabinoid CB1 receptors in the basal ganglia of a transgenic model of Huntington's disease. Brain Res (2002) 0.87
Huntingtin is required for normal excitatory synapse development in cortical and striatal circuits. J Neurosci (2014) 0.87
Mutant huntingtin affects cortical progenitor cell division and development of the mouse neocortex. J Neurosci (2014) 0.87
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Deficits of glutamate transmission in the striatum of toxic and genetic models of Huntington's disease. Neurosci Lett (2006) 0.86
Increased Body Weight of the BAC HD Transgenic Mouse Model of Huntington's Disease Accounts for Some but Not All of the Observed HD-like Motor Deficits. PLoS Curr (2013) 0.86
Expanded CAG repeats in the murine Huntington's disease gene increases neuronal differentiation of embryonic and neural stem cells. Mol Cell Neurosci (2008) 0.86
Selective roles of normal and mutant huntingtin in neural induction and early neurogenesis. PLoS One (2013) 0.85
Tonic mGluR5/CB1-dependent suppression of inhibition as a pathophysiological hallmark in the striatum of mice carrying a mutant form of huntingtin. J Physiol (2012) 0.84
Cortical interneuron loss and symptom heterogeneity in Huntington disease. Ann Neurol (2014) 0.81