Published in J Neurol Sci on December 01, 1988
Stable fetal cardiomyocyte grafts in the hearts of dystrophic mice and dogs. J Clin Invest (1995) 1.36
Animal models of Duchenne muscular dystrophy: from basic mechanisms to gene therapy. Dis Model Mech (2015) 1.30
Canine models of Duchenne muscular dystrophy and their use in therapeutic strategies. Mamm Genome (2012) 1.28
Transduction efficiency and immune response associated with the administration of AAV8 vector into dog skeletal muscle. Mol Ther (2008) 1.21
Duchenne's muscular dystrophy: animal models used to investigate pathogenesis and develop therapeutic strategies. Int J Exp Pathol (2003) 1.20
An intronic LINE-1 element insertion in the dystrophin gene aborts dystrophin expression and results in Duchenne-like muscular dystrophy in the corgi breed. Lab Invest (2010) 1.20
Abiotrophy in domestic animals: a review. Can J Vet Res (1990) 1.16
Evaluation of vascular delivery methodologies to enhance rAAV6-mediated gene transfer to canine striated musculature. Mol Ther (2009) 1.13
Kinematics of gait in golden retriever muscular dystrophy. Neuromuscul Disord (2009) 1.13
Small and large animal models in cardiac contraction research: advantages and disadvantages. Pharmacol Ther (2013) 1.08
Long-term restoration of cardiac dystrophin expression in golden retriever muscular dystrophy following rAAV6-mediated exon skipping. Mol Ther (2011) 1.05
Gene therapy in large animal models of muscular dystrophy. ILAR J (2009) 1.05
Age-matched comparison reveals early electrocardiography and echocardiography changes in dystrophin-deficient dogs. Neuromuscul Disord (2011) 1.04
Feline muscular dystrophy with dystrophin deficiency. Am J Pathol (1989) 1.03
Mammalian models of Duchenne Muscular Dystrophy: pathological characteristics and therapeutic applications. J Biomed Biotechnol (2011) 1.02
Cardiac involvement in Beagle-based canine X-linked muscular dystrophy in Japan (CXMDJ): electrocardiographic, echocardiographic, and morphologic studies. BMC Cardiovasc Disord (2006) 1.00
Gender influences cardiac function in the mdx model of Duchenne cardiomyopathy. Muscle Nerve (2010) 0.99
Gender dimorphism influences extracellular matrix expression and regeneration of muscular tissue in mdx dystrophic mice. Histochem Cell Biol (2004) 0.99
A possible new inherited myopathy in a young Labrador retriever. Can Vet J (2008) 0.97
Predictive markers of clinical outcome in the GRMD dog model of Duchenne muscular dystrophy. Dis Model Mech (2014) 0.96
Sparing of the dystrophin-deficient cranial sartorius muscle is associated with classical and novel hypertrophy pathways in GRMD dogs. Am J Pathol (2013) 0.95
Development of Duchenne-type cardiomyopathy. Morphologic studies in a canine model. Am J Pathol (1989) 0.95
Systemic delivery of allogenic muscle stem cells induces long-term muscle repair and clinical efficacy in duchenne muscular dystrophy dogs. Am J Pathol (2011) 0.93
Duchenne muscular dystrophy presenting with failure to thrive. Arch Dis Child (1995) 0.93
Longitudinal ambulatory measurements of gait abnormality in dystrophin-deficient dogs. BMC Musculoskelet Disord (2011) 0.91
Effects of an immunosuppressive treatment in the GRMD dog model of Duchenne muscular dystrophy. PLoS One (2012) 0.91
Comparative Genomics of X-linked Muscular Dystrophies: The Golden Retriever Model. Curr Genomics (2013) 0.90
PTEN contributes to profound PI3K/Akt signaling pathway deregulation in dystrophin-deficient dog muscle. Am J Pathol (2009) 0.89
Pharmacologic management of Duchenne muscular dystrophy: target identification and preclinical trials. ILAR J (2014) 0.88
Duchenne muscular dystrophy gene therapy in the canine model. Hum Gene Ther Clin Dev (2015) 0.86
Intra-amniotic rAAV-mediated microdystrophin gene transfer improves canine X-linked muscular dystrophy and may induce immune tolerance. Mol Ther (2015) 0.85
Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy. Physiol Rev (2016) 0.85
Long-term systemic myostatin inhibition via liver-targeted gene transfer in golden retriever muscular dystrophy. Hum Gene Ther (2011) 0.85
Bortezomib (PS-341) treatment decreases inflammation and partially rescues the expression of the dystrophin-glycoprotein complex in GRMD dogs. PLoS One (2013) 0.85
Initial pulmonary respiration causes massive diaphragm damage and hyper-CKemia in Duchenne muscular dystrophy dog. Sci Rep (2013) 0.83
Clinical phenotype of X-linked myotubular myopathy in Labrador Retriever puppies. J Vet Intern Med (2015) 0.83
TNF-α-Induced microRNAs Control Dystrophin Expression in Becker Muscular Dystrophy. Cell Rep (2015) 0.83
Current Challenges and Future Directions in Recombinant AAV-Mediated Gene Therapy of Duchenne Muscular Dystrophy. Pharmaceuticals (Basel) (2013) 0.82
Gene replacement therapies for duchenne muscular dystrophy using adeno-associated viral vectors. Curr Gene Ther (2012) 0.81
Hematopoietic cell transplantation directly into dystrophic muscle fails to reconstitute satellite cells and myofibers. Biol Blood Marrow Transplant (2007) 0.81
Dystrophin-deficient large animal models: translational research and exon skipping. Am J Transl Res (2015) 0.80
Multiscale models of skeletal muscle reveal the complex effects of muscular dystrophy on tissue mechanics and damage susceptibility. Interface Focus (2015) 0.80
Vascular endothelial dysfunction in Duchenne muscular dystrophy is restored by bradykinin through upregulation of eNOS and nNOS. Basic Res Cardiol (2011) 0.79
A Nonsense Variant in COL6A1 in Landseer Dogs with Muscular Dystrophy. G3 (Bethesda) (2015) 0.77
Differential Gene Expression Profiling of Dystrophic Dog Muscle after MuStem Cell Transplantation. PLoS One (2015) 0.77
Mapping contrast agent uptake and retention in MRI studies of myocardial perfusion: case control study of dogs with Duchenne muscular dystrophy. Int J Cardiovasc Imaging (2012) 0.76
Respiratory dysfunction in unsedated dogs with golden retriever muscular dystrophy. Neuromuscul Disord (2013) 0.76
Influence of immune responses in gene/stem cell therapies for muscular dystrophies. Biomed Res Int (2014) 0.75
Whole genome sequencing reveals a 7 base-pair deletion in DMD exon 42 in a dog with muscular dystrophy. Mamm Genome (2016) 0.75
Adaptive Immune Response Impairs the Efficacy of Autologous Transplantation of Engineered Stem Cells in Dystrophic Dogs. Mol Ther (2016) 0.75
Early loss of ambulation is not a representative clinical feature in Duchenne muscular dystrophy dogs: remarks on the article of Barthélémy et al. Dis Model Mech (2015) 0.75
Profiles of Steroid Hormones in Canine X-Linked Muscular Dystrophy via Stable Isotope Dilution LC-MS/MS. PLoS One (2015) 0.75
Becker muscular dystrophy-like myopathy regarded as so-called "fatty muscular dystrophy" in a pig: a case report and its diagnostic method. J Vet Med Sci (2013) 0.75
Genome-wide association study to identify potential genetic modifiers in a canine model for Duchenne muscular dystrophy. BMC Genomics (2016) 0.75
Increased collagen cross-linking is a signature of dystrophin-deficient muscle. Muscle Nerve (2016) 0.75
Osteopontin is Linked with AKT, FoxO1, and Myostatin in Skeletal Muscle Cells. Muscle Nerve (2017) 0.75
Moving towards successful exon-skipping therapy for Duchenne muscular dystrophy. J Hum Genet (2017) 0.75
Non-Targeted Metabolomics Analysis of Golden Retriever Muscular Dystrophy-Affected Muscles Reveals Alterations in Arginine and Proline Metabolism, and Elevations in Glutamic and Oleic Acid In Vivo. Metabolites (2017) 0.75
Canine and Feline Models of Human Genetic Diseases and Their Contributions to Advancing Clinical Therapies . Yale J Biol Med (2017) 0.75
Clinical and immunologic criteria for the diagnosis of allergic bronchopulmonary aspergillosis. Ann Intern Med (1977) 4.14
Serum IgE and IgG antibody activity against Aspergillus fumigatus as a diagnostic aid in allergic bronchopulmonary aspergillosis. Am Rev Respir Dis (1978) 1.62
Ocular manifestations of equine motor neuron disease. Equine Vet J (1999) 1.47
Nomenclature. Vet Pathol (2012) 1.39
Stable fetal cardiomyocyte grafts in the hearts of dystrophic mice and dogs. J Clin Invest (1995) 1.36
Equine motor neuron disease; a preliminary report. Cornell Vet (1990) 1.27
Feline sphingolipidosis resembling Niemann-Pick disease type C. Acta Neuropathol (1990) 1.18
Clinical and topographic magnetic resonance characteristics of suspected brain infarction in 40 dogs. J Vet Intern Med (2006) 1.16
Acral mutilation and nociceptive loss in English pointer dogs. A canine sensory neuropathy. Acta Neuropathol (1981) 1.16
Canine X-linked muscular dystrophy as an animal model of Duchenne muscular dystrophy: a review. Am J Med Genet (1992) 1.14
Pathogenetic studies of infection of the bovine fetus with bovine viral diarrhea virus. II. Ocular lesions. Vet Pathol (1975) 1.14
Evaluation of serum bile acid concentrations for the diagnosis of portosystemic venous anomalies in the dog and cat. J Am Vet Med Assoc (1985) 1.13
Canine X-linked muscular dystrophy: morphologic lesions. J Neurol Sci (1990) 1.12
Hereditary cerebellar cortical abiotrophy in the Gordon Setter. J Am Vet Med Assoc (1980) 1.11
Risk factors associated with equine motor neuron disease: a possible model for human MND. Neurology (1993) 1.11
Immune carrier state of feline panleukopenia virus-infected cats. Am J Vet Res (1971) 1.09
Mutation segregation and rapid carrier detection of X-linked muscular dystrophy in dogs. Am J Vet Res (1996) 1.09
Sarcocystis neurona n. sp. (Protozoa: Apicomplexa), the etiologic agent of equine protozoal myeloencephalitis. J Parasitol (1991) 1.09
Facial and vestibulocochlear nerve disease in six horses. J Am Vet Med Assoc (1983) 1.04
Allergic angiitis and granulomatosis. Prolonged remission induced by combined prednisone--azathioprine therapy. Arch Intern Med (1978) 1.04
Motor neuron degeneration in a horse. J Am Vet Med Assoc (1993) 0.99
Progressive muscular dystrophy in a golden retriever dog: light microscope and ultrastructural features at 4 and 8 months. Acta Neuropathol (1986) 0.99
Canine viral enteritis. II. Morphologic lesions in naturally occurring parvovirus infection. Cornell Vet (1979) 0.99
Deletion of the dystrophin muscle promoter in feline muscular dystrophy. Neuromuscul Disord (1995) 0.99
Canine viral enteritis. I. Status report on corona- and parvo-like viral enteritides. Cornell Vet (1979) 0.97
An adult case of canine neuronal ceroid-lipofuscinosis. Acta Neuropathol (1977) 0.97
Myelin deficiency (md): a neurologic mutant in the Wistar rat. Am J Pathol (1979) 0.97
Development of Duchenne-type cardiomyopathy. Morphologic studies in a canine model. Am J Pathol (1989) 0.95
Alaskan Husky encephalopathy--a canine neurodegenerative disorder resembling subacute necrotizing encephalomyelopathy (Leigh syndrome). Acta Neuropathol (2000) 0.95
Acquired equine motor neuron disease. Vet Pathol (1994) 0.95
Canine laryngeal rhabdomyoma. Vet Pathol (1985) 0.95
Intravascular leukostasis in a horse with myelomonocytic leukemia. Vet Pathol (1984) 0.94
Increased serum alanine aminotransferase activity associated with muscle necrosis in the dog. J Vet Intern Med (1990) 0.94
Hypercalcemia associated with an adenocarcinoma derived from the apocrine glands of the anal sac. Vet Pathol (1981) 0.94
Duchenne's cardiomyopathy in a canine model: electrocardiographic and echocardiographic studies. J Am Coll Cardiol (1991) 0.93
Morphology and embryological interpretation of a congenital occipito-atlanto-axial malformation in a dog. Teratology (1988) 0.93
Clinical and pathologic findings in two draft horses with progressive muscle atrophy, neuromuscular weakness, and abnormal gait characteristic of shivers syndrome. J Am Vet Med Assoc (1999) 0.92
Canine X-linked muscular dystrophy: selective involvement of muscles in neonatal dogs. Neuromuscul Disord (1991) 0.92
The diagnostic utility of cerebrospinal fluid creatine kinase activity in the horse. J Vet Intern Med (1996) 0.92
A study of cerebellar and cerebral cortical degeneration in miniature poodle pups with emphasis on the ultrastructure of Purkinje cell changes. Acta Neuropathol (1988) 0.92
Animal models of Duchenne and Becker muscular dystrophy. Br Med Bull (1989) 0.91
Severe polysaccharide storage myopathy in Belgian and Percheron draught horses. Equine Vet J (1997) 0.91
GM2 gangliosidosis in a Japanese spaniel. Acta Neuropathol (1985) 0.91
Pathogenesis of canine parvovirus enteritis: sequential virus distribution and passive immunization studies. Vet Pathol (1985) 0.91
Multisystemic chromatolytic neuronal degeneration in Cairn terriers. A case with generalized cataplectic episodes. J Vet Intern Med (1991) 0.91
Tibetan terrier model of canine ceroid lipofuscinosis. Am J Med Genet (1992) 0.90
Ossification of the atlas-axis complex in the dog. Anat Histol Embryol (1986) 0.90
Temperature-dependent inhibition of evoked acetylcholine release in tick paralysis. Nature (1976) 0.90
Hereditary cerebellar degeneration in Scottish terriers. J Vet Intern Med (2010) 0.90
Orchidopexy: theory and practice. Br Med J (Clin Res Ed) (1985) 0.89
Defective Schwann cell function in canine inherited hypertrophic neuropathy. Acta Neuropathol (1984) 0.89
Intrinsic, management, and nutritional factors associated with equine motor neuron disease. J Am Vet Med Assoc (1997) 0.89
Prevalence of mycoplasmal and ureaplasmal recovery from tracheobronchial lavages and of mycoplasmal recovery from pharyngeal swab specimens in cats with or without pulmonary disease. Am J Vet Res (1993) 0.89
Subacute necrotising encephalopathy in an Alaskan husky. J Small Anim Pract (1999) 0.89
Cerebellar cortical degeneration in a Labrador retriever. Can Vet J (1995) 0.89
Pathogenesis of canine parvovirus enteritis: the importance of viremia. Vet Pathol (1985) 0.88
Results of diagnostic investigations and long-term outcome of 33 dogs with brain infarction (2000-2004). J Vet Intern Med (2005) 0.88
Myasthenia in Springer Spaniel littermates. J Small Anim Pract (1975) 0.87
Chronic relapsing polyradiculoneuritis in a dog. A clinical, light- and electron-microscopic study. Acta Neuropathol (1974) 0.87
The clinical and pathologic heterogeneity of feline alpha-mannosidosis. J Vet Intern Med (1989) 0.87
Mice heterozygous for the mld mutation have intermediate levels of myelin basic protein mRNA and its translation products. Brain Res (1986) 0.86
Adjustment of total serum calcium concentration for binding to albumin and protein in cats: 291 cases (1986-1987). J Am Vet Med Assoc (1989) 0.86
Effects on pain of experimentally induced and spontaneous distraction. Psychol Rep (1972) 0.86
Porencephaly and hydranencephaly in six dogs. Vet Rec (2011) 0.86
Hereditary polioencephalomyelopathy of the Australian cattle dog. Acta Neuropathol (1997) 0.86
Canine inherited hypertrophic neuropathy: clinical and electrodiagnostic studies. Am J Vet Res (1984) 0.85
Cerebellar degeneration in Old English Sheepdogs. J Am Vet Med Assoc (2000) 0.84
Primary aortic chondrosarcoma in a dog. Vet Pathol (1988) 0.84
Review of idiopathic feline vestibular syndrome in 75 cats. J Am Vet Med Assoc (1985) 0.84
Prevalence of mycoplasmal and ureaplasmal recovery from tracheobronchial lavages and prevalence of mycoplasmal recovery from pharyngeal swab specimens in dogs with or without pulmonary disease. Am J Vet Res (1993) 0.84
A canine encephalomyelopathy with morphological abnormalities in mitochondria. Acta Neuropathol (1997) 0.84
Epithelial odontogenic tumours in domestic animals. J Comp Pathol (1987) 0.83
Expression of utrophin (dystrophin-related protein) during regeneration and maturation of skeletal muscle in canine X-linked muscular dystrophy. Neuropathol Appl Neurobiol (1994) 0.83
Evaluation of decision criteria for detection of spinal cord compression based on cervical myelography in horses: 38 cases (1981-2001). Equine Vet J (2004) 0.83
Expression of only one myelin basic protein allele in mouse is compatible with normal myelination. Brain Res (1987) 0.83
Bovine viral diarrhea-mucosal disease, abortion, and congenital cerebellar hypoplasia in a dairy herd. J Am Vet Med Assoc (1970) 0.83
Canine intestinal carcinoids. Vet Pathol (1982) 0.83
Clinical, radiographic, and bronchial cytologic features of cats with bronchial disease: 65 cases (1980-1986). J Am Vet Med Assoc (1989) 0.83
Canine protozoan polyradiculoneuritis. Acta Neuropathol (1988) 0.82
Myelination in the CNS of mld mutant mice: comparison between composition and structure. Brain Res (1984) 0.82
Intracranial fusariosis: a novel cause of fungal meningoencephalitis in a dog. Vet Pathol (2004) 0.82
Degenerative myelopathy in an adult miniature poodle. J Am Vet Med Assoc (1985) 0.82
Neuritis of the cauda equina, a chronic idiopathic polyradiculoneuritis in the horse. Acta Neuropathol (1979) 0.82
Verminous encephalitis in a horse produced by nematodes in the family protostrongylidae. Vet Pathol (2007) 0.82
Idiopathic pure red cell aplasia and nonregenerative immune-mediated anemia in dogs: 43 cases (1988-1999). J Am Vet Med Assoc (2000) 0.82
Complex polysaccharide inclusions in skeletal muscle adjacent to sarcomas in two dogs. Vet Pathol (2002) 0.81
Clinical electromyographic studies of canine X-linked muscular dystrophy. Am J Vet Res (1989) 0.81
Quantitative assessment of motor neuron loss in equine motor neuron disease (EMND). Equine Vet J (1998) 0.81
Cerebellar infarction caused by arterial thrombosis in a dog. J Am Vet Med Assoc (1988) 0.81