Published in J Vet Intern Med on April 11, 1989
Bone marrow transplantation corrects the enzyme defect in neurons of the central nervous system in a lysosomal storage disease. Proc Natl Acad Sci U S A (1994) 1.27
Purification of feline lysosomal alpha-mannosidase, determination of its cDNA sequence and identification of a mutation causing alpha-mannosidosis in Persian cats. Biochem J (1997) 1.06
Intracellular transport of human lysosomal alpha-mannosidase and alpha-mannosidosis-related mutants. Biochem J (2004) 0.82
A review of gene therapy in canine and feline models of lysosomal storage disorders. Hum Gene Ther Clin Dev (2015) 0.79
Canine and Feline Models of Human Genetic Diseases and Their Contributions to Advancing Clinical Therapies . Yale J Biol Med (2017) 0.75
Prevalence of psychiatric disorders in youths across five sectors of care. J Am Acad Child Adolesc Psychiatry (2001) 3.59
Prevalence of adolescent substance use disorders across five sectors of care. J Am Acad Child Adolesc Psychiatry (2001) 3.39
Detection of cell-dependent cytotoxic antibody to cells infected with herpes simplex virus. Nature (1974) 2.55
Antibody-dependent cell-mediated cytotoxicity to target cells infected with type 1 and type 2 herpes simplex virus. J Immunol (1976) 2.49
Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation. Proc Natl Acad Sci U S A (1998) 2.22
Critical role for glycosphingolipids in Niemann-Pick disease type C. Curr Biol (2001) 2.22
Neurons in Niemann-Pick disease type C accumulate gangliosides as well as unesterified cholesterol and undergo dendritic and axonal alterations. J Neuropathol Exp Neurol (2001) 2.01
Canine X-linked muscular dystrophy. An animal model of Duchenne muscular dystrophy: clinical studies. J Neurol Sci (1988) 1.98
Circadian expression of clock genes in human oral mucosa and skin: association with specific cell-cycle phases. Am J Pathol (2001) 1.94
Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse. Hum Mol Genet (2001) 1.93
Effect of physician recommendation and patient adherence on rates of colorectal cancer testing. Cancer Detect Prev (2004) 1.90
Transcriptional control of a nuclear gene encoding a mitochondrial fatty acid oxidation enzyme in transgenic mice: role for nuclear receptors in cardiac and brown adipose expression. Mol Cell Biol (1996) 1.73
A mouse model for mucopolysaccharidosis type III A (Sanfilippo syndrome). Glycobiology (1999) 1.67
Abnormal nonshivering thermogenesis in mice with inherited defects of fatty acid oxidation. J Clin Invest (1998) 1.50
Ocular manifestations of equine motor neuron disease. Equine Vet J (1999) 1.47
Cobalamin deficiency associated with methylmalonic acidemia in a cat. J Am Vet Med Assoc (1992) 1.40
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Effects of substance abuse on housing stability of homeless mentally Ill persons in supported housing. Psychiatr Serv (1996) 1.29
Equine motor neuron disease; a preliminary report. Cornell Vet (1990) 1.27
Feline sphingolipidosis resembling Niemann-Pick disease type C. Acta Neuropathol (1990) 1.18
Alterations in neuron morphology in feline mannosidosis. A Golgi study. Acta Neuropathol (1981) 1.17
Clinical and topographic magnetic resonance characteristics of suspected brain infarction in 40 dogs. J Vet Intern Med (2006) 1.16
Acral mutilation and nociceptive loss in English pointer dogs. A canine sensory neuropathy. Acta Neuropathol (1981) 1.16
Housing outcomes for homeless adults with mental illness: results from the second-round McKinney program. Psychiatr Serv (1997) 1.16
Canine X-linked muscular dystrophy as an animal model of Duchenne muscular dystrophy: a review. Am J Med Genet (1992) 1.14
Pathogenetic studies of infection of the bovine fetus with bovine viral diarrhea virus. II. Ocular lesions. Vet Pathol (1975) 1.14
GABAergic neuroaxonal dystrophy and other cytopathological alterations in feline Niemann-Pick disease type C. Acta Neuropathol (1997) 1.13
Evaluation of serum bile acid concentrations for the diagnosis of portosystemic venous anomalies in the dog and cat. J Am Vet Med Assoc (1985) 1.13
Canine X-linked muscular dystrophy: morphologic lesions. J Neurol Sci (1990) 1.12
Hereditary cerebellar cortical abiotrophy in the Gordon Setter. J Am Vet Med Assoc (1980) 1.11
Risk factors associated with equine motor neuron disease: a possible model for human MND. Neurology (1993) 1.11
Immune carrier state of feline panleukopenia virus-infected cats. Am J Vet Res (1971) 1.09
Circadian function in patients with advanced non-small-cell lung cancer. Br J Cancer (2005) 1.09
Sarcocystis neurona n. sp. (Protozoa: Apicomplexa), the etiologic agent of equine protozoal myeloencephalitis. J Parasitol (1991) 1.09
Lysosomal storage diseases of animals: an essay in comparative pathology. Vet Pathol (1997) 1.08
Antibody-dependent cellular cytotoxicity to target cells infected with herpes simplex viruses: functional adequacy in the neonate. Pediatrics (1977) 1.07
Purification of feline lysosomal alpha-mannosidase, determination of its cDNA sequence and identification of a mutation causing alpha-mannosidosis in Persian cats. Biochem J (1997) 1.06
Human neonatal and maternal monocyte-macrophage and lymphocyte-mediated antibody-dependent cytotoxicity to cells infected with herpes simplex. J Pediatr (1978) 1.06
The gangliosidoses: comparative features and research applications. Vet Pathol (1979) 1.05
Facial and vestibulocochlear nerve disease in six horses. J Am Vet Med Assoc (1983) 1.04
Feline Niemann-Pick disease type C. Am J Pathol (1994) 1.04
Circadian dynamics of tumor necrosis factor alpha (cachectin) lethality. J Exp Med (1994) 1.00
Motor neuron degeneration in a horse. J Am Vet Med Assoc (1993) 0.99
Metabolic abnormalities in feline Niemann-Pick type C heterozygotes. J Inherit Metab Dis (1996) 0.99
Lysosomal dysfunction causes neurodegeneration in mucolipidosis II 'knock-in' mice. Brain (2012) 0.97
An adult case of canine neuronal ceroid-lipofuscinosis. Acta Neuropathol (1977) 0.97
Myelin deficiency (md): a neurologic mutant in the Wistar rat. Am J Pathol (1979) 0.97
Ferret pyramidal cell dendritogenesis: changes in morphology and ganglioside expression during cortical development. J Comp Neurol (1999) 0.95
Alaskan Husky encephalopathy--a canine neurodegenerative disorder resembling subacute necrotizing encephalomyelopathy (Leigh syndrome). Acta Neuropathol (2000) 0.95
Acquired equine motor neuron disease. Vet Pathol (1994) 0.95
Molecular cloning and characterization of the mouse medium-chain acyl-CoA dehydrogenase cDNA. Genomics (1994) 0.94
Childhood and adolescent onset conduct disorder: a test of the developmental taxonomy. J Abnorm Child Psychol (2001) 0.94
Structure and chromosomal location of the mouse medium-chain acyl-CoA dehydrogenase-encoding gene and its promoter. Gene (1996) 0.93
Reduction of fensulfothion to fensulfothion sulfide by Klebsiella pneumoniae. Appl Environ Microbiol (1977) 0.93
Morphology and embryological interpretation of a congenital occipito-atlanto-axial malformation in a dog. Teratology (1988) 0.93
Fluorescence polarization analysis, lipid composition, and Na+, K+-ATPase kinetics of synaptosomal membranes in feline GM1 and GM2 gangliosidosis. J Neurochem (1985) 0.93
The diagnostic utility of cerebrospinal fluid creatine kinase activity in the horse. J Vet Intern Med (1996) 0.92
A study of cerebellar and cerebral cortical degeneration in miniature poodle pups with emphasis on the ultrastructure of Purkinje cell changes. Acta Neuropathol (1988) 0.92
Clinical and pathologic findings in two draft horses with progressive muscle atrophy, neuromuscular weakness, and abnormal gait characteristic of shivers syndrome. J Am Vet Med Assoc (1999) 0.92
Multisystemic chromatolytic neuronal degeneration in Cairn terriers. A case with generalized cataplectic episodes. J Vet Intern Med (1991) 0.91
GM2 gangliosidosis in a Japanese spaniel. Acta Neuropathol (1985) 0.91
Cloning and characterization of the mouse short-chain acyl-CoA dehydrogenase gene. Mamm Genome (1996) 0.91
Mitochondrial dysfunction in the neuronal ceroid-lipofuscinoses (Batten disease). Neurochem Int (2002) 0.90
Characterization of the rat mutant dystonic (dt): a new animal model of dystonia musculorum deformans. J Neurosci (1984) 0.90
Ossification of the atlas-axis complex in the dog. Anat Histol Embryol (1986) 0.90
Tibetan terrier model of canine ceroid lipofuscinosis. Am J Med Genet (1992) 0.90
Sphingomyelin lipidosis in a cat. Vet Pathol (1987) 0.90
RNA expression and chromosomal location of the mouse long-chain acyl-CoA dehydrogenase gene. Genomics (1995) 0.90
Inherited lysosomal storage disease associated with deficiencies of beta-galactosidase and alpha-neuraminidase in sheep. Am J Med Genet (1988) 0.90
Hereditary cerebellar degeneration in Scottish terriers. J Vet Intern Med (2010) 0.90
Lipoprotein secretion and triglyceride stores in the heart. J Biol Chem (2001) 0.89
Intrinsic, management, and nutritional factors associated with equine motor neuron disease. J Am Vet Med Assoc (1997) 0.89
Evaluation of a colorimetric method for canine glycosylated hemoglobin. Am J Vet Res (1982) 0.89
Subacute necrotising encephalopathy in an Alaskan husky. J Small Anim Pract (1999) 0.89
Null allele at Bcd-1 locus in BALB/cByJ mice is due to a deletion in the short-chain acyl-CoA dehydrogenase gene and results in missplicing of mRNA. Genomics (1993) 0.89
Cerebellar cortical degeneration in a Labrador retriever. Can Vet J (1995) 0.89
Defective Schwann cell function in canine inherited hypertrophic neuropathy. Acta Neuropathol (1984) 0.89
Results of diagnostic investigations and long-term outcome of 33 dogs with brain infarction (2000-2004). J Vet Intern Med (2005) 0.88
Short-chain acyl-coenzyme A dehydrogenase activity, antigen, and biosynthesis are absent in the BALB/cByJ mouse. Pediatr Res (1992) 0.88
Biochemical basis of type AB GM2 gangliosidosis in a Japanese spaniel. J Neurochem (1987) 0.88
Glycosylated hemoglobin and canine diabetes mellitus. J Am Vet Med Assoc (1980) 0.87
Chronic relapsing polyradiculoneuritis in a dog. A clinical, light- and electron-microscopic study. Acta Neuropathol (1974) 0.87
GM1 gangliosidosis in Portuguese water dogs: pathologic and biochemical findings. Vet Pathol (1988) 0.87
Structural characterization of the mouse long-chain acyl-CoA dehydrogenase gene and 5' regulatory region. Mamm Genome (1998) 0.87
Circadian time structure of septic shock: timing is everything. J Infect Dis (1997) 0.87
Intracellular recording and HRP-staining of cortical neurons in feline ganglioside storage disease. Brain Res (1980) 0.87
Hereditary polioencephalomyelopathy of the Australian cattle dog. Acta Neuropathol (1997) 0.86
Porencephaly and hydranencephaly in six dogs. Vet Rec (2011) 0.86
Circadian organization of thymidylate synthase activity in normal tissues: a possible basis for 5-fluorouracil chronotherapeutic advantage. Int J Cancer (2000) 0.86
Expression of human argininosuccinate synthetase after retroviral-mediated gene transfer. Somat Cell Mol Genet (1986) 0.86
Further studies on ectopic dendrite growth and other geometrical distortions of neurons in feline GM1 gangliosidosis. Neuroscience (1987) 0.85
Ectopic dendrites occur only on cortical pyramidal cells containing elevated GM2 ganglioside in alpha-mannosidosis. Proc Natl Acad Sci U S A (1991) 0.85
Animal models of diabetes and obesity, including the PBB/Ld mouse. Fed Proc (1976) 0.85