Nevoid basal cell carcinoma syndrome: bilateral ovarian fibromas in a 3 1/2-year-old girl.

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Published in J Am Acad Dermatol on February 01, 1986

Authors

A D Johnson, A A Hebert, N B Esterly

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A repressor (MAT alpha 2 Product) and its operator control expression of a set of cell type specific genes in yeast. Cell (1985) 5.77

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Interactions between DNA-bound repressors govern regulation by the lambda phage repressor. Proc Natl Acad Sci U S A (1979) 5.02

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The yeast cell-type-specific repressor alpha 2 acts cooperatively with a non-cell-type-specific protein. Cell (1988) 4.82

lambda Repressor and cro--components of an efficient molecular switch. Nature (1981) 4.52

Hemangiomas in children. N Engl J Med (1999) 4.40

Identification of a mating type-like locus in the asexual pathogenic yeast Candida albicans. Science (1999) 4.14

Net1, a Sir2-associated nucleolar protein required for rDNA silencing and nucleolar integrity. Cell (1999) 3.98

Bacteriophage lambda repressor and cro protein: interactions with operator DNA. Methods Enzymol (1980) 3.52

TUP1, CPH1 and EFG1 make independent contributions to filamentation in candida albicans. Genetics (2000) 3.04

Identification and characterization of TUP1-regulated genes in Candida albicans. Genetics (2000) 2.97

Turning genes off by Ssn6-Tup1: a conserved system of transcriptional repression in eukaryotes. Trends Biochem Sci (2000) 2.83

The WD repeats of Tup1 interact with the homeo domain protein alpha 2. Genes Dev (1994) 2.80

Revised clinical and laboratory criteria for subtypes of inherited epidermolysis bullosa. A consensus report by the Subcommittee on Diagnosis and Classification of the National Epidermolysis Bullosa Registry. J Am Acad Dermatol (1991) 2.79

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Report from the third international consensus meeting to harmonise core outcome measures for atopic eczema/dermatitis clinical trials (HOME). Br J Dermatol (2014) 2.76

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Crystal structure of the MATa1/MAT alpha 2 homeodomain heterodimer bound to DNA. Science (1995) 2.63

Silent information regulator protein complexes in Saccharomyces cerevisiae: a SIR2/SIR4 complex and evidence for a regulatory domain in SIR4 that inhibits its interaction with SIR3. Proc Natl Acad Sci U S A (1997) 2.52

Flexibility of the yeast alpha 2 repressor enables it to occupy the ends of its operator, leaving the center free. Genes Dev (1988) 2.50

The chromo domain protein chd1p from budding yeast is an ATP-dependent chromatin-modifying factor. EMBO J (2000) 2.44

Insect repellents: an overview. J Am Acad Dermatol (1997) 2.42

A molecular mechanism for combinatorial control in yeast: MCM1 protein sets the spacing and orientation of the homeodomains of an alpha 2 dimer. Cell (1992) 2.39

Yeast repressor alpha 2 binds to its operator cooperatively with yeast protein Mcm1. Mol Cell Biol (1989) 2.33

Rfg1, a protein related to the Saccharomyces cerevisiae hypoxic regulator Rox1, controls filamentous growth and virulence in Candida albicans. Mol Cell Biol (2001) 2.22

Identification of genes required for alpha 2 repression in Saccharomyces cerevisiae. Genetics (1995) 2.19

Transcriptional repression in eukaryotes. Annu Rev Cell Biol (1993) 2.17

A short, disordered protein region mediates interactions between the homeodomain of the yeast alpha 2 protein and the MCM1 protein. Cell (1993) 2.14

Mating in Candida albicans and the search for a sexual cycle. Annu Rev Microbiol (2005) 2.06

A complex composed of tup1 and ssn6 represses transcription in vitro. J Biol Chem (1997) 1.97

Transcriptional repression directed by the yeast alpha 2 protein in vitro. Nature (1994) 1.94

Meiotic induction of the yeast HOP1 gene is controlled by positive and negative regulatory sites. Mol Cell Biol (1992) 1.92

Successful treatment of juvenile hemangiomas with prednisone. J Pediatr (1968) 1.91

Juvenile xanthogranuloma. J Am Acad Dermatol (1997) 1.90

Phenotypic switching in Candida albicans is controlled by a SIR2 gene. EMBO J (1999) 1.90

Guidelines of care for hemangiomas of infancy. American Academy of Dermatology Guidelines/Outcomes Committee. J Am Acad Dermatol (1997) 1.85

Optic gliomas in children with neurofibromatosis type 1. J Pediatr (1989) 1.76

Purpura in infants and children. J Am Acad Dermatol (1997) 1.72

The tetratricopeptide repeats of Ssn6 interact with the homeo domain of alpha 2. Genes Dev (1995) 1.71

Rapid solid-phase radioimmunoassay for staphylococcal enterotoxin A. Appl Microbiol (1973) 1.70

Homeo domain of the yeast repressor alpha 2 is a sequence-specific DNA-binding domain but is not sufficient for repression. Science (1987) 1.69

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Cutis marmorata telangiectatica congenita: report of 22 cases. J Am Acad Dermatol (1989) 1.63

Structure of the C-terminal domain of Tup1, a corepressor of transcription in yeast. EMBO J (2000) 1.62

Epidermal and other congenital organoid nevi. Curr Probl Pediatr (1975) 1.58

Phenytoin therapy of recessive dystrophic epidermolysis bullosa. Clinical trial and proposed mechanism of action on collagenase. N Engl J Med (1980) 1.58

The effect of antimicrobial agents on leukocyte chemotaxis. J Invest Dermatol (1978) 1.56

A rapid solid phase radioimmunoassay for staphylococcal B enterotoxin. J Immunol (1972) 1.54

Intraepidermal type VII collagen. Evidence for abnormal intracytoplasmic processing of a major basement membrane protein in rare patients with dominant and possibly localized recessive forms of dystrophic epidermolysis bullosa. J Am Acad Dermatol (1990) 1.54

Progressive osseous heteroplasia. Arch Dermatol (1996) 1.51

The effect of salicylate on the metabolism of normal and stimulated human lymphocytes in vitro. J Clin Invest (1971) 1.50

Myocyte enhancer binding factor-2 expression and activity in vascular smooth muscle cells. Association with the activated phenotype. Circ Res (1996) 1.48

Perianal pseudoverrucous papules and nodules in children. Arch Dermatol (1992) 1.48

Development of Streptococcus thermophilus lacZ as a reporter gene for Candida albicans. Microbiology (2001) 1.45

Production, purification, and chemical characterization of Staphylococcus aureus exfoliative toxin. Infect Immun (1975) 1.44

False aneurysms of the left ventricle. Identification of distinctive clinical, radiographic, and angiographic features. Radiology (1978) 1.43

Acrally occurring dermatofibrosarcoma protuberans in children and adults. J Dermatol Surg Oncol (1994) 1.42

Antimalarials for children: indications, toxicities, and guidelines. J Am Acad Dermatol (1993) 1.40

Effect of growth hormone therapy on melanocytic nevi in survivors of childhood neoplasia. Arch Dermatol (1997) 1.40

Yeast a1 and alpha 2 homeodomain proteins form a DNA-binding activity with properties distinct from those of either protein. J Mol Biol (1993) 1.40

Urticarial vasculitis and Lyme disease. J Am Acad Dermatol (1990) 1.40

Nonprogressive scrotal hair growth in two infants. Pediatr Dermatol (1993) 1.40

A homeo domain protein lacking specific side chains of helix 3 can still bind DNA and direct transcriptional repression. Genes Dev (1995) 1.39

Two sisters with telangiectases [corrected], spondyloepiphyseal dysplasia, hypothyroidism, neovascularization and tractional retinal detachments: a new entity? Pediatr Dermatol (1989) 1.39

Cold panniculitis in a neonate. J Am Acad Dermatol (1995) 1.39

A conditional allele of the Saccharomyces cerevisiae HOP1 gene is suppressed by overexpression of two other meiosis-specific genes: RED1 and REC104. Genetics (1993) 1.38

Residues in the WD repeats of Tup1 required for interaction with alpha2. Mol Cell Biol (1997) 1.36

Serum antibody titers to Candida albicans utilizing an immunofluorescent technic. Am J Clin Pathol (1968) 1.34

Comparison of growth and toxin production in two vaccine strains of Bacillus anthracis. Appl Environ Microbiol (1981) 1.33

Drug-induced hypersensitivity syndrome in pediatric patients. Pediatrics (2001) 1.29

A genetic switch in a bacterial virus. Sci Am (1982) 1.28

The carboxy-terminal tail of the homeo domain protein alpha 2 is required for function with a second homeo domain protein. Genes Dev (1993) 1.28

Gene regulation by the yeast Ssn6-Tup1 corepressor. Cold Spring Harb Symp Quant Biol (1998) 1.26

Purification and characterization of different types of exfoliative toxin from Staphylococcus aureus. Infect Immun (1979) 1.24

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Pyoderma gangrenosum in infants and children. Pediatr Dermatol (1994) 1.19

Diazepam and paraldehyde for treatment of severe delirium tremens. A controlled trial. Ann Intern Med (1975) 1.19

Increased skin permeability in preterm infants. J Pediatr (1971) 1.18

Interaction between two homeodomain proteins is specified by a short C-terminal tail. Nature (1994) 1.17

'Membranous aplasia cutis' with hair collars. Congenital absence of skin or neuroectodermal defect? Arch Dermatol (1995) 1.17

The spectrum of pathogenic mutations in SPINK5 in 19 families with Netherton syndrome: implications for mutation detection and first case of prenatal diagnosis. J Invest Dermatol (2001) 1.16

Staphylococcus aureus enterotoxin B release (excretion) under controlled conditions of fermentation. Appl Microbiol (1973) 1.15

Pharmacogenomics of the RNA world: structural RNA polymorphisms in drug therapy. Clin Pharmacol Ther (2011) 1.15

Mutations in chromatin components suppress a defect of Gcn5 protein in Saccharomyces cerevisiae. Mol Cell Biol (1998) 1.14

Trichostasis spinulosa. Int J Dermatol (1985) 1.13

Nucleotide sequence analysis of the recombinant joints in 16 naturally arising deletion mutants of simian virus 40. Virology (1982) 1.13

Relationship between follicular cysts and milk production in dairy cattle. J Dairy Sci (1966) 1.12

Report of an infant with GM1 gangliosidosis type I and extensive and unusual mongolian spots. Br J Dermatol (1981) 1.11

Hydroa vacciniforme. Diagnosis by repetitive ultraviolet-A phototesting. Arch Dermatol (1986) 1.10

Tissue expansion in a patient with extensive nevus comedonicus. Ann Plast Surg (1992) 1.10

Nontraumatic determination of left ventricular ejection fraction by radionuclide angiocardiography. Circulation (1975) 1.10

Functional and physical characterization of transcription initiation complexes in the bacteriophage lambda OR region. J Biol Chem (1985) 1.10

Recognition of a DNA operator by a dimer composed of two different homeodomain proteins. EMBO J (1994) 1.09

Intrinsic and chemically produced microheterogeneity of Staphylococcus aureus enterotoxin type C. Infect Immun (1975) 1.09