Published in J Biol Chem on October 25, 1980
Endocytosis and the recycling of plasma membrane. J Cell Biol (1983) 10.24
Intracellular movement of two mannose 6-phosphate receptors: return to the Golgi apparatus. J Cell Biol (1988) 3.05
Mannose-6-phosphate receptors for lysosomal enzymes cycle between the Golgi complex and endosomes. J Cell Biol (1986) 2.89
Receptor-mediated endocytosis. Biochem J (1985) 2.73
Identification and characterization of cells deficient in the mannose 6-phosphate receptor: evidence for an alternate pathway for lysosomal enzyme targeting. Proc Natl Acad Sci U S A (1983) 2.67
The role of intermediate vesicles in the adsorptive endocytosis and transport of ligand to lysosomes by human fibroblasts. J Cell Biol (1983) 2.45
Yeast mannans inhibit binding and phagocytosis of zymosan by mouse peritoneal macrophages. J Cell Biol (1983) 2.45
Dendritic cell and macrophage staining by monoclonal antibodies in tissue sections and epidermal sheets. Am J Pathol (1983) 2.38
Characterization of a membrane-associated receptor from bovine liver that binds phosphomannosyl residues of bovine testicular beta-galactosidase. Proc Natl Acad Sci U S A (1981) 2.32
Ultrastructural localization of the mannose 6-phosphate receptor in rat liver. J Cell Biol (1984) 2.08
Redistribution of mannose-6-phosphate receptors induced by tunicamycin and chloroquine. J Cell Biol (1984) 1.87
Morphologic study of the internalization of a lysosomal enzyme by the mannose 6-phosphate receptor in cultured Chinese hamster ovary cells. Proc Natl Acad Sci U S A (1981) 1.81
Synthesis of beta-hexosaminidase in cell-free translation and in intact fibroblasts: an insoluble precursor alpha chain in a rare form of Tay-Sachs disease. Proc Natl Acad Sci U S A (1982) 1.61
Antibodies against lysosomal membranes reveal a 100,000-mol-wt protein that cross-reacts with purified H+,K+ ATPase from gastric mucosa. J Cell Biol (1984) 1.59
Monensin inhibits recycling of macrophage mannose-glycoprotein receptors and ligand delivery to lysosomes. Biochem J (1984) 1.45
Demonstration and partial characterization of the interferon-gamma receptor on human mononuclear phagocytes. J Clin Invest (1985) 1.40
Subfractionation of rat liver Golgi apparatus: separation of enzyme activities involved in the biosynthesis of the phosphomannosyl recognition marker in lysosomal enzymes. Proc Natl Acad Sci U S A (1983) 1.35
A cycloheximide-resistant pool of receptors for asialoglycoproteins and mannose 6-phosphate residues in the Golgi complex of hepatocytes. EMBO J (1984) 1.29
Studies of the biosynthesis of the mannose 6-phosphate receptor in receptor-positive and -deficient cell lines. J Cell Biol (1983) 1.28
Lysosomal enzyme oligosaccharide phosphorylation in mouse lymphoma cells: specificity and kinetics of binding to the mannose 6-phosphate receptor in vivo. J Cell Biol (1982) 1.27
Transformation by the v-fms oncogene product: role of glycosylational processing and cell surface expression. Mol Cell Biol (1985) 1.22
Biosynthesis and turnover of the phosphomannosyl receptor in human fibroblasts. Biochem J (1983) 1.21
Isolation and characterization of membranes from bovine liver which are highly enriched in mannose 6-phosphate receptors. J Cell Biol (1989) 1.17
Polarized secretion of lysosomal enzymes: co-distribution of cation-independent mannose-6-phosphate receptors and lysosomal enzymes along the osteoclast exocytic pathway. J Cell Biol (1988) 1.16
Pathways involved in targeting and secretion of a lysosomal enzyme in Dictyostelium discoideum. J Cell Biol (1985) 1.06
Mucolipidosis II and III. The genetic relationships between two disorders of lysosomal enzyme biosynthesis. J Clin Invest (1983) 1.05
Mannose 6-, fructose 1-, and fructose 6-phosphates inhibit human natural cell-mediated cytotoxicity. Proc Natl Acad Sci U S A (1981) 1.04
Identification of asparagine-linked oligosaccharides involved in tumor cell adhesion to laminin and type IV collagen. J Cell Biol (1984) 1.01
Mannose 6-phosphate receptor-mediated endocytosis of acid hydrolases: internalization of beta-glucuronidase is accompanied by a limited dephosphorylation. J Cell Biol (1986) 0.99
The role of lysosomal enzymes in killing of mammalian cells by the lysosomotropic detergent N-dodecylimidazole. J Cell Biol (1987) 0.97
Carbohydrate modifications of the high mobility group proteins. Proc Natl Acad Sci U S A (1981) 0.96
Cellular and lysosomal uptake of methylamine in isolated rat hepatocytes. Biochem J (1983) 0.94
alpha-L-iduronidase therapy for mucopolysaccharidosis type I. Biologics (2008) 0.87
Low rate of procollagen conversion in dermatosparactic sheep fibroblasts is paralleled by increased synthesis of type I and type III collagens. EMBO J (1982) 0.86
A calcium-binding, asparagine-linked oligosaccharide is involved in skeleton formation in the sea urchin embryo. J Cell Biol (1989) 0.82
The effect of chloroquine on the distribution of newly synthesized and old beta-hexosaminidase in fibroblasts. Biochem J (1982) 0.81
Properties of the Syrian hamster phosphomannosyl receptor: an aggregate of low molecular weight proteins. Proc Natl Acad Sci U S A (1985) 0.79
Specific binding of leukotriene C4 to ileal segments and subcellular fractions of ileal smooth muscle cells. Proc Natl Acad Sci U S A (1984) 0.77
Protein bodies and vacuoles as lysosomes : investigations into the role of mannose-6-phosphate in intracellular transport of glycosidases in pea cotyledons. Plant Physiol (1984) 0.76
Structural analysis of the carbohydrate chains of beta-N-acetylhexosaminidases from bovine brain. Biochem J (1985) 0.75
Incorporation of mannose 6-phosphate receptors into liposomes. Receptor topography and binding of alpha-mannosidase. Biochem J (1983) 0.75
Association of newly synthesized islet prohormones with intracellular membranes. J Cell Biol (1984) 0.75
Chloroquine inhibits lysosomal enzyme pinocytosis and enhances lysosomal enzyme secretion by impairing receptor recycling. J Cell Biol (1980) 5.99
Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts. Proc Natl Acad Sci U S A (1977) 5.97
The phosphomannosyl recognition system for intracellular and intercellular transport of lysosomal enzymes. J Cell Biochem (1982) 4.50
beta-Glucan Synthetases of Plasma Membrane and Golgi Apparatus from Onion Stem. Plant Physiol (1974) 3.74
The ribosome binding sites recognized by E. coli ribosomes have regions with signal character in both the leader and protein coding segments. Nucleic Acids Res (1980) 3.74
Beta glucuronidase deficiency: report of clinical, radiologic, and biochemical features of a new mucopolysaccharidosis. J Pediatr (1973) 3.44
Phosphotungstic acid-chromic acid as a selective electron-dense stain for plasma membranes of plant cells. Stain Technol (1972) 3.42
HFE gene knockout produces mouse model of hereditary hemochromatosis. Proc Natl Acad Sci U S A (1998) 3.35
Enhancement of RNA polymerase activity by a factor released by auxin from plasma membrane. Proc Natl Acad Sci U S A (1972) 3.15
Alteration of intracellular traffic by monensin; mechanism, specificity and relationship to toxicity. Biochim Biophys Acta (1990) 2.93
DNA replication and messenger RNA production after induction of wild-type lambda bacteriophage and lambda mutants. J Mol Biol (1966) 2.90
Carbonic anhydrase II deficiency identified as the primary defect in the autosomal recessive syndrome of osteopetrosis with renal tubular acidosis and cerebral calcification. Proc Natl Acad Sci U S A (1983) 2.73
Beta-glucuronidase deficiency mucopolysaccharidosis: methods for enzymatic diagnosis. J Lab Clin Med (1973) 2.67
The hemochromatosis founder mutation in HLA-H disrupts beta2-microglobulin interaction and cell surface expression. J Biol Chem (1997) 2.62
Membrane flow and differentiation: origin of Golgi apparatus membranes from endoplasmic reticulum. Adv Cytopharmacol (1974) 2.58
Cloning, expression, and sequence homologies of cDNA for human carbonic anhydrase II. Genomics (1987) 2.57
Structure of isolated plant Golgi apparatus revealed by negative staining. J Cell Biol (1966) 2.56
Human beta-glucuronidase: in vivo clearance and in vitro uptake by a glycoprotein recognition system on reticuloendothelial cells. Cell (1978) 2.50
The role of intermediate vesicles in the adsorptive endocytosis and transport of ligand to lysosomes by human fibroblasts. J Cell Biol (1983) 2.45
Phospholipid class and fatty acid composition of golgi apparatus isolated from rat liver and comparison with other cell fractions. Biochemistry (1970) 2.42
Defective acidification of endosomes in Chinese hamster ovary cell mutants "cross-resistant" to toxins and viruses. Proc Natl Acad Sci U S A (1983) 2.39
Cytomembrane differentiation in the endoplasmic reticulum-Golgi apparatus-vesicle complex. Science (1968) 2.29
Enzymatic identification of mannose 6-phosphate on the recognition marker for receptor-mediated pinocytosis of beta-glucuronidase by human fibroblasts. Proc Natl Acad Sci U S A (1979) 2.28
Membrane flow and intercoversions among endomembranes. Biochim Biophys Acta (1979) 2.11
Beta-glucuronidase binding to human fibroblast membrane receptors. J Biol Chem (1980) 2.08
Association of the transferrin receptor in human placenta with HFE, the protein defective in hereditary hemochromatosis. Proc Natl Acad Sci U S A (1997) 2.06
Hereditary hemochromatosis: effects of C282Y and H63D mutations on association with beta2-microglobulin, intracellular processing, and cell surface expression of the HFE protein in COS-7 cells. Proc Natl Acad Sci U S A (1997) 2.03
Auxin-Stimulated NADH Oxidase Purified from Plasma Membrane of Soybean. Plant Physiol (1988) 1.98
Auxin (2,4-D) stimulation (in vivo and in vitro) of polysaccharide synthesis in plasma membrane fragments isolated from onion stems. Biochem Biophys Res Commun (1972) 1.94
Isolation and characterization of secretory vesicles in germinated pollen of Lilium longiflorum. J Cell Sci (1971) 1.93
Cloning, sequencing, and expression of cDNA for human beta-glucuronidase. Proc Natl Acad Sci U S A (1987) 1.92
Human carbonic anhydrase XII: cDNA cloning, expression, and chromosomal localization of a carbonic anhydrase gene that is overexpressed in some renal cell cancers. Proc Natl Acad Sci U S A (1998) 1.92
The human cation-independent mannose 6-phosphate receptor. Cloning and sequence of the full-length cDNA and expression of functional receptor in COS cells. J Biol Chem (1988) 1.91
Multiple isoelectric and recognition forms of human beta-glucuronidase activity. Arch Biochem Biophys (1975) 1.88
Carbonic anhydrase IV from human lung. Purification, characterization, and comparison with membrane carbonic anhydrase from human kidney. J Biol Chem (1990) 1.81
Treatment of murine mucopolysaccharidosis type VII by syngeneic bone marrow transplantation in neonates. Lab Invest (1993) 1.81
In vitro correction of deficient human fibroblasts by beta-glucuronidase from different human sources. Biochem Biophys Res Commun (1974) 1.81
Isolation of a Golgi apparatus-rich fraction from rat liver. I. Method and morphology. J Cell Biol (1970) 1.80
Enzyme replacement therapy for murine mucopolysaccharidosis type VII. J Clin Invest (1994) 1.73
The co-occurrence of Reiter's syndrome and acquired immunodeficiency. Ann Intern Med (1987) 1.73
Expression of the hypoxia-inducible and tumor-associated carbonic anhydrases in ductal carcinoma in situ of the breast. Am J Pathol (2001) 1.71
Hepcidin: a putative iron-regulatory hormone relevant to hereditary hemochromatosis and the anemia of chronic disease. Proc Natl Acad Sci U S A (2001) 1.71
Mechanism of increased iron absorption in murine model of hereditary hemochromatosis: increased duodenal expression of the iron transporter DMT1. Proc Natl Acad Sci U S A (1999) 1.66
Mouse strain differences determine severity of iron accumulation in Hfe knockout model of hereditary hemochromatosis. Proc Natl Acad Sci U S A (2001) 1.65
Immunohistochemistry of HLA-H, the protein defective in patients with hereditary hemochromatosis, reveals unique pattern of expression in gastrointestinal tract. Proc Natl Acad Sci U S A (1997) 1.61
Structure of human beta-glucuronidase reveals candidate lysosomal targeting and active-site motifs. Nat Struct Biol (1996) 1.61
Increased life span and correction of metabolic defects in murine mucopolysaccharidosis type VII after syngeneic bone marrow transplantation. Blood (1991) 1.61
Association of HFE protein with transferrin receptor in crypt enterocytes of human duodenum. Proc Natl Acad Sci U S A (1999) 1.60
Insulin-like growth factor receptor expression and function in human breast cancer. Cancer Res (1990) 1.57
Immunohistochemistry of carbonic anhydrase isozyme IX (MN/CA IX) in human gut reveals polarized expression in the epithelial cells with the highest proliferative capacity. J Histochem Cytochem (1998) 1.57
Carbonic anhydrase inhibitor suppresses invasion of renal cancer cells in vitro. Proc Natl Acad Sci U S A (2000) 1.55
Transferrin receptor 2: continued expression in mouse liver in the face of iron overload and in hereditary hemochromatosis. Proc Natl Acad Sci U S A (2000) 1.54
Constitutive lambda DNA replication by lambda-C17, a regulatory mutant related to virulence. Virology (1968) 1.53
A murine model of mucopolysaccharidosis VII. Gross and microscopic findings in beta-glucuronidase-deficient mice. Am J Pathol (1990) 1.53
Action and Inhibition of Endogenous Phospholipases during Isolation of Plant Membranes. Plant Physiol (1978) 1.51
Connections between mitochondria and endoplasmic reticulum in rat liver and onion stem. Protoplasma (1971) 1.48
Permanent lymphoid lines from genetically marked lymphocytes: success with lymphocytes recovered from frozen storage. Tissue Antigens (1976) 1.48
Mucolipidosis III (pseudo-Hurler polydystrophy): Clinical and laboratory studies in a series of 12 patients. Johns Hopkins Med J (1975) 1.48
Evidence for an increase in microviscosity of plasma membranes from soybean hypocotyls induced by the plant hormone, indole-3-acetic Acid. Plant Physiol (1976) 1.47
Carbonic anhydrase II deficiency: diagnosis and carrier detection using differential enzyme inhibition and inactivation. Am J Hum Genet (1986) 1.44
Human beta-glucuronidase. II. Fate of infused human placental beta-glucuronidase in the rat. Pediatr Res (1977) 1.42
Localization of membrane-associated carbonic anhydrase type IV in kidney epithelial cells. Proc Natl Acad Sci U S A (1990) 1.39
Inhibition of the rat clearance system for agalacto-orosomucoid by yeast mannans and by mannose. Biochem Biophys Res Commun (1977) 1.39
Isolation of highly purified fractions of plasma membrane and tonoplast from the same homogenate of soybean hypocotyls by free-flow electrophoresis. Plant Physiol (1986) 1.39
Carbonic anhydrase II deficiency in 12 families with the autosomal recessive syndrome of osteopetrosis with renal tubular acidosis and cerebral calcification. N Engl J Med (1985) 1.39
A light-responsive and periodic NADH oxidase activity of the cell surface of Tetrahymena and of human buffy coat cells. Antioxid Redox Signal (2000) 1.39
Crystal structure of the dimeric extracellular domain of human carbonic anhydrase XII, a bitopic membrane protein overexpressed in certain cancer tumor cells. Proc Natl Acad Sci U S A (2001) 1.39
Purification and properties of beta-glucuronidase from human placenta. Biochemistry (1978) 1.37
Ganglioside biosynthesis. Concentration of glycosphingolipid glycosyltransferases in Golgi apparatus from rat liver. J Biol Chem (1974) 1.36
Role of p97 and syntaxin 5 in the assembly of transitional endoplasmic reticulum. Mol Biol Cell (2000) 1.34
Murine mucopolysaccharidosis type VII: long term therapeutic effects of enzyme replacement and enzyme replacement followed by bone marrow transplantation. J Clin Invest (1997) 1.33
Enzyme replacement with recombinant beta-glucuronidase in murine mucopolysaccharidosis type VII: impact of therapy during the first six weeks of life on subsequent lysosomal storage, growth, and survival. Pediatr Res (1996) 1.33
Phosphatidylinositol turnover in isolated soybean membranes stimulated by the synthetic growth hormone 2,4-dichlorophenoxyacetic acid. J Biol Chem (1984) 1.33
Enzyme replacement in murine mucopolysaccharidosis type VII: neuronal and glial response to beta-glucuronidase requires early initiation of enzyme replacement therapy. Pediatr Res (1999) 1.31
Expression of a novel transmembrane carbonic anhydrase isozyme XII in normal human gut and colorectal tumors. Am J Pathol (2000) 1.30
Structural compartmentation of the cytosol: zones of exclusion, zones of adhesion, cytoskeletal and intercisternal elements. Subcell Biochem (1978) 1.26
Purification and characterization of human salivary carbonic anhydrase. J Biol Chem (1987) 1.26
The overexpressed human 46-kDa mannose 6-phosphate receptor mediates endocytosis and sorting of beta-glucuronidase. Proc Natl Acad Sci U S A (1990) 1.26
Localization of carbonic anhydrase IV in a specific capillary bed of the human eye. Proc Natl Acad Sci U S A (1991) 1.26
Carbonic anhydrase IV on brain capillary endothelial cells: a marker associated with the blood-brain barrier. Proc Natl Acad Sci U S A (1992) 1.25
Requirement for coenzyme Q in plasma membrane electron transport. Proc Natl Acad Sci U S A (1992) 1.25
B-type cytochromes in plasma membranes isolated from rat liver, in comparison with those of endomembranes. J Cell Biol (1979) 1.24
Membrane-associated carbonic anhydrase from rat lung. Purification, characterization, tissue distribution, and comparison with carbonic anhydrase IVs of other mammals. J Biol Chem (1992) 1.24
Biodistribution, kinetics, and efficacy of highly phosphorylated and non-phosphorylated beta-glucuronidase in the murine model of mucopolysaccharidosis VII. J Biol Chem (2001) 1.23
Distribution of phospholipid biosynthetic enzymes among cell components of rat liver. J Biol Chem (1978) 1.23
Enzyme replacement with recombinant beta-glucuronidase in the newborn mucopolysaccharidosis type VII mouse. Pediatr Res (1993) 1.23
Fibroblast receptor for lysosomal enzymes mediates pinocytosis of multivalent phosphomannan fragment. J Cell Biol (1980) 1.22
Expression of membrane-associated carbonic anhydrase XIV on neurons and axons in mouse and human brain. Proc Natl Acad Sci U S A (2001) 1.22
Osteopetrosis, renal tubular acidosis and basal ganglia calcification in three sisters. Am J Med (1980) 1.22
Correlation of structural features of phosphomannans with their ability to inhibit pinocytosis of human beta-glucuronidase by human fibroblasts. J Biol Chem (1978) 1.21
Biosynthesis and turnover of the phosphomannosyl receptor in human fibroblasts. Biochem J (1983) 1.21
Biochemical and morphological comparison of plasma membrane and milk fat globule membrane from bovine mammary gland. J Cell Biol (1970) 1.20
Enzyme replacement therapy for murine mucopolysaccharidosis type VII leads to improvements in behavior and auditory function. J Clin Invest (1998) 1.20
Isolation of a vesicular intermediate in the cell-free transfer of membrane from transitional elements of the endoplasmic reticulum to Golgi apparatus cisternae of rat liver. J Biol Chem (1988) 1.20
Tubular connections between dictyosomes and forming secretory vesicles in plant Golgi apparatus. J Cell Biol (1966) 1.19