Published in Hum Mol Genet on January 15, 2002
Air trapping and airflow obstruction in newborn cystic fibrosis piglets. Am J Respir Crit Care Med (2013) 1.65
An insulator element 3' to the CFTR gene binds CTCF and reveals an active chromatin hub in primary cells. Nucleic Acids Res (2009) 1.19
Lubiprostone activates non-CFTR-dependent respiratory epithelial chloride secretion in cystic fibrosis mice. Am J Physiol Lung Cell Mol Physiol (2008) 1.14
The "Goldilocks effect" in cystic fibrosis: identification of a lung phenotype in the cftr knockout and heterozygous mouse. BMC Genet (2004) 1.13
Addressing fluorogenic real-time qPCR inhibition using the novel custom Excel file system 'FocusField2-6GallupqPCRSet-upTool-001' to attain consistently high fidelity qPCR reactions. Biol Proced Online (2006) 1.10
New quick method for isolating RNA from laser captured cells stained by immunofluorescent immunohistochemistry; RNA suitable for direct use in fluorogenic TaqMan one-step real-time RT-PCR. Biol Proced Online (2005) 1.08
Novel regulatory mechanisms for the CFTR gene. Biochem Soc Trans (2009) 0.94
CFTR and Wnt/beta-catenin signaling in lung development. BMC Dev Biol (2008) 0.89
Pathophysiologic consequences following inhibition of a CFTR-dependent developmental cascade in the lung. BMC Dev Biol (2005) 0.88
The Peter Pan paradigm. Theor Biol Med Model (2008) 0.88
Dexamethasone regulates CFTR expression in Calu-3 cells with the involvement of chaperones HSP70 and HSP90. PLoS One (2012) 0.85
Cystic fibrosis transmembrane regulator fragments with the Phe508 deletion exert a dual allosteric control over the master kinase CK2. Biochem J (2010) 0.84
Multiple mechanisms influence regulation of the cystic fibrosis transmembrane conductance regulator gene promoter. Am J Respir Cell Mol Biol (2009) 0.83
The extracellular calcium-sensing receptor regulates human fetal lung development via CFTR. Sci Rep (2016) 0.79
Glucocorticoids Distinctively Modulate the CFTR Channel with Possible Implications in Lung Development and Transition into Extrauterine Life. PLoS One (2015) 0.78
Expression of ENaC subunits, chloride channels, and aquaporins in ovine fetal lung: ontogeny of expression and effects of altered fetal cortisol concentrations. Am J Physiol Regul Integr Comp Physiol (2009) 0.78
Chromatin Dynamics in the Regulation of CFTR Expression. Genes (Basel) (2015) 0.78
A balance between activating and repressive histone modifications regulates cystic fibrosis transmembrane conductance regulator (CFTR) expression in vivo. Epigenetics (2014) 0.77
Cystic fibrosis: more questions than answers. Ochsner J (2003) 0.76
Transient in utero disruption of cystic fibrosis transmembrane conductance regulator causes phenotypic changes in alveolar type II cells in adult rats. BMC Cell Biol (2009) 0.75
Deep resequencing of CFTR in 762 F508del homozygotes reveals clusters of non-coding variants associated with cystic fibrosis disease traits. Hum Genome Var (2016) 0.75
Dynamics of short- and long-term association between a bacterial plant pathogen and its arthropod vector. Sci Rep (2014) 0.75
Postnatal Airway Growth in Cystic Fibrosis Piglets. J Appl Physiol (1985) (2017) 0.75
Alternative splicing of the ovine CFTR gene. Mamm Genome (2003) 0.75
Extended lung cancer incidence follow-up in the Mayo Lung Project and overdiagnosis. J Natl Cancer Inst (2006) 4.39
The phenotypic consequences of CFTR mutations. Ann Hum Genet (2003) 2.09
Do peer-tutors perform better in examinations? An analysis of medical school final examination results. Med Educ (2014) 1.50
Peer-assisted learning--beyond teaching: How can medical students contribute to the undergraduate curriculum? Med Teach (2014) 1.37
Intronic enhancers coordinate epithelial-specific looping of the active CFTR locus. Proc Natl Acad Sci U S A (2009) 1.29
HNF1alpha is involved in tissue-specific regulation of CFTR gene expression. Biochem J (2004) 1.25
A complex intronic enhancer regulates expression of the CFTR gene by direct interaction with the promoter. J Cell Mol Med (2009) 1.23
An insulator element 3' to the CFTR gene binds CTCF and reveals an active chromatin hub in primary cells. Nucleic Acids Res (2009) 1.19
CTCF mediates insulator function at the CFTR locus. Biochem J (2007) 1.16
MicroRNA regulation of expression of the cystic fibrosis transmembrane conductance regulator gene. Biochem J (2011) 1.15
Evaluation of potential regulatory elements identified as DNase I hypersensitive sites in the CFTR gene. Eur J Biochem (2002) 1.14
The CFTR gene and regulation of its expression. Pediatr Pulmonol (2005) 1.07
Alternative 5' exons of the CFTR gene show developmental regulation. Hum Mol Genet (2003) 1.00
Transcriptional networks driving enhancer function in the CFTR gene. Biochem J (2012) 1.00
MUC6 mucin expression inhibits tumor cell invasion. Exp Cell Res (2011) 0.99
The role of the SEA (sea urchin sperm protein, enterokinase and agrin) module in cleavage of membrane-tethered mucins. FEBS J (2005) 0.98
The effect of a brief social intervention on the examination results of UK medical students: a cluster randomised controlled trial. BMC Med Educ (2009) 0.97
Molecular mechanisms controlling CFTR gene expression in the airway. J Cell Mol Med (2012) 0.97
N-Glycosylation of the MUC1 mucin in epithelial cells and secretions. Glycobiology (2006) 0.95
A T3 allele in the CFTR gene exacerbates exon 9 skipping in vas deferens and epididymal cell lines and is associated with Congenital Bilateral Absence of Vas Deferens (CBAVD). Hum Mutat (2005) 0.95
Novel regulatory mechanisms for the CFTR gene. Biochem Soc Trans (2009) 0.94
130-nm albumin-bound paclitaxel enhances tumor radiocurability and therapeutic gain. Clin Cancer Res (2007) 0.93
The characterization of the first anti-mouse Muc6 antibody shows an increased expression of the mucin in pancreatic tissue of Cftr-knockout mice. Histochem Cell Biol (2010) 0.93
Nucleosome mapping across the CFTR locus identifies novel regulatory factors. Nucleic Acids Res (2013) 0.92
Mucin variable number tandem repeat polymorphisms and severity of cystic fibrosis lung disease: significant association with MUC5AC. PLoS One (2011) 0.92
Coating of adeno-associated virus with reactive polymers can ablate virus tropism, enable retargeting and provide resistance to neutralising antisera. J Gene Med (2008) 0.92
The mucin MUC4 and its membrane partner ErbB2 regulate biological properties of human CAPAN-2 pancreatic cancer cells via different signalling pathways. PLoS One (2012) 0.91
Deletion of CFTR translation start site reveals functional isoforms of the protein in CF patients. Cell Physiol Biochem (2009) 0.90
Methods for RNA extraction, cDNA preparation and analysis of CFTR transcripts. J Cyst Fibros (2004) 0.89
The contribution of tandem repeat number to the O-glycosylation of mucins. Glycobiology (2002) 0.89
Atypical 5' splice sites cause CFTR exon 9 to be vulnerable to skipping. Am J Hum Genet (2002) 0.88
Transcriptional regulation of CFTR gene expression. Front Biosci (Elite Ed) (2012) 0.88
A genome-wide analysis of open chromatin in human tracheal epithelial cells reveals novel candidate regulatory elements for lung function. Thorax (2011) 0.88
Evaluation of gene targeting by homologous recombination in ovine somatic cells. Mol Reprod Dev (2003) 0.87
DNA polymorphisms in potential regulatory elements of the CFTR gene alter transcription factor binding. Hum Genet (2002) 0.86
Quantitative methods for the analysis of CFTR transcripts/splicing variants. J Cyst Fibros (2004) 0.86
Beyond amphiphiles: coarse-grained simulations of star-polyphile liquid crystalline assemblies. Phys Chem Chem Phys (2009) 0.86
Immune mediators regulate CFTR expression through a bifunctional airway-selective enhancer. Mol Cell Biol (2013) 0.85
Working with words: exploring textual analysis in medical education research. Med Educ (2012) 0.85
A genome-wide analysis of open chromatin in human epididymis epithelial cells reveals candidate regulatory elements for genes coordinating epididymal function. Biol Reprod (2013) 0.85
Nucleosome occupancy reveals regulatory elements of the CFTR promoter. Nucleic Acids Res (2011) 0.85
Collagen XV inhibits epithelial to mesenchymal transition in pancreatic adenocarcinoma cells. PLoS One (2013) 0.85
Hispanic Infants with cystic fibrosis show low CFTR mutation detection rates in the Illinois newborn screening program. J Genet Couns (2012) 0.84
Interaction of intestinal and pancreatic transcription factors in the regulation of CFTR gene expression. Biochim Biophys Acta (2009) 0.84
Validation of an improved pediatric weight estimation strategy. J Pediatr Pharmacol Ther (2013) 0.84
Introducing peer-assisted learning into a veterinary curriculum: a trial with a simulator. J Vet Med Educ (2009) 0.84
Multiple mechanisms influence regulation of the cystic fibrosis transmembrane conductance regulator gene promoter. Am J Respir Cell Mol Biol (2009) 0.83
MZF-1 and DbpA interact with DNase I hypersensitive sites that correlate with expression of the human MUC1 mucin gene. Exp Cell Res (2005) 0.83
CFTR expression from a BAC carrying the complete human gene and associated regulatory elements. J Cell Mol Med (2008) 0.83
A comparative genomic analysis of the cow, pig, and human CFTR genes identifies potential intronic regulatory elements. Genomics (2003) 0.83
Tumor suppression by collagen XV is independent of the restin domain. Matrix Biol (2012) 0.82
Telephone follow-up to a mail survey: when to offer an interview compared to a reminder call. BMC Med Res Methodol (2012) 0.82
High resolution intra-operative two-dimensional specimen mammography and its impact on second operation for re-excision of positive margins at final pathology after breast conservation surgery. Am J Surg (2011) 0.82
Genomic approaches for the discovery of CFTR regulatory elements. Transcription (2012) 0.81
The effect of visual and auditory cues on seat preference in an opera theater. J Acoust Soc Am (2008) 0.81
Oxidative stress regulates CFTR gene expression in human airway epithelial cells through a distal antioxidant response element. Am J Respir Cell Mol Biol (2015) 0.79
The role of CTCF in coordinating the expression of single gene loci. Biochem Cell Biol (2011) 0.79
Non-PCR methods for the analysis of CFTR transcripts. J Cyst Fibros (2004) 0.78
RNA interference-mediated inhibition of hepatocyte nuclear factor 1alpha identifies target genes. Biochim Biophys Acta (2008) 0.78
Mucin glycosylation and sulphation in airway epithelial cells is not influenced by cystic fibrosis transmembrane conductance regulator expression. Am J Respir Cell Mol Biol (2005) 0.78
Coordinate regulation of the gel-forming mucin genes at chromosome 11p15.5. J Biol Chem (2013) 0.78
Cubic membranes: a structure-based design for DNA uptake. J R Soc Interface (2008) 0.78
Exploring the mechanisms of macrolides in cystic fibrosis. Respir Med (2005) 0.77
Collagen XV: exploring its structure and role within the tumor microenvironment. Mol Cancer Res (2013) 0.77
Control of vitellogenin genes expression by sequences derived from transposable elements in rainbow trout. Biochim Biophys Acta (2010) 0.77
Evaluation of MUC6 mucin tandem repeats. Biochim Biophys Acta (2004) 0.76
Characterization of a large human transgene following invasin-mediated delivery in a bacterial artificial chromosome. Chromosoma (2013) 0.76
In vivo glycosylation of MUC1 in airway epithelial cells. Glycoconj J (2002) 0.75
Alternative splicing of the ovine CFTR gene. Mamm Genome (2003) 0.75
Successful collaboration in education: the UMeP. Clin Teach (2014) 0.75
Applying the food safety objective and related standards to thermal inactivation of Salmonella in poultry meat. J Food Prot (2007) 0.75
Learning through work: clinical shadowing of junior doctors by first year medical students. Med Teach (2013) 0.75
Genomic approaches to studying CFTR transcriptional regulation. Methods Mol Biol (2011) 0.75
Analysis of genomic CFTR DNA. J Cyst Fibros (2004) 0.75
Identification of two novel elements involved in human MUCI gene expression in vivo. Mol Med (2002) 0.75