Published in Biochemistry on March 29, 2005
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Expression of cone-photoreceptor-specific antigens in a cell line derived from retinal tumors in transgenic mice. Invest Ophthalmol Vis Sci (2004) 1.92
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Retention of function without normal disc morphogenesis occurs in cone but not rod photoreceptors. J Cell Biol (2006) 1.70
The R172W mutation in peripherin/rds causes a cone-rod dystrophy in transgenic mice. Hum Mol Genet (2004) 1.48
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The Cys214-->Ser mutation in peripherin/rds causes a loss-of-function phenotype in transgenic mice. Biochem J (2005) 1.28
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Effect of Rds abundance on cone outer segment morphogenesis, photoreceptor gene expression, and outer limiting membrane integrity. J Comp Neurol (2007) 1.20
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Retinal stem cells transplanted into models of late stages of retinitis pigmentosa preferentially adopt a glial or a retinal ganglion cell fate. Invest Ophthalmol Vis Sci (2007) 1.16
Differential requirements for retinal degeneration slow intermolecular disulfide-linked oligomerization in rods versus cones. Hum Mol Genet (2008) 1.15
Outer segment oligomerization of Rds: evidence from mouse models and subcellular fractionation. Biochemistry (2008) 1.12
P2Y(2) receptor agonist INS37217 enhances functional recovery after detachment caused by subretinal injection in normal and rds mice. Invest Ophthalmol Vis Sci (2003) 1.10
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The role of Rds in outer segment morphogenesis and human retinal disease. Ophthalmic Genet (2006) 1.04
Differences in RDS trafficking, assembly and function in cones versus rods: insights from studies of C150S-RDS. Hum Mol Genet (2010) 1.03
Retinal angiogenesis in the Ins2(Akita) mouse model of diabetic retinopathy. Invest Ophthalmol Vis Sci (2013) 1.02
S/MAR-containing DNA nanoparticles promote persistent RPE gene expression and improvement in RPE65-associated LCA. Hum Mol Genet (2013) 0.97
Molecular characterization of the skate peripherin/rds gene: relationship to its orthologues and paralogues. Invest Ophthalmol Vis Sci (2003) 0.97
Nanoparticle-mediated gene transfer specific to retinal pigment epithelial cells. Biomaterials (2011) 0.96
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Nanoparticles for retinal gene therapy. Prog Retin Eye Res (2010) 0.95
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Direct gene transfer with compacted DNA nanoparticles in retinal pigment epithelial cells: expression, repeat delivery and lack of toxicity. Nanomedicine (Lond) (2012) 0.93
Expression profiling after retinal detachment and reattachment: a possible role for aquaporin-0. Invest Ophthalmol Vis Sci (2008) 0.92
Defects in the outer limiting membrane are associated with rosette development in the Nrl-/- retina. PLoS One (2012) 0.92
Increased cone sensitivity to ABCA4 deficiency provides insight into macular vision loss in Stargardt's dystrophy. Biochim Biophys Acta (2011) 0.91
Genetic supplementation of RDS alleviates a loss-of-function phenotype in C214S model of retinitis pigmentosa. Adv Exp Med Biol (2008) 0.90
Late-onset cone photoreceptor degeneration induced by R172W mutation in Rds and partial rescue by gene supplementation. Invest Ophthalmol Vis Sci (2007) 0.90
Biochemical analysis of phenotypic diversity associated with mutations in codon 244 of the retinal degeneration slow gene. Biochemistry (2010) 0.90
Structural and functional relationships between photoreceptor tetraspanins and other superfamily members. Cell Mol Life Sci (2011) 0.88
Differential distribution of proteins and lipids in detergent-resistant and detergent-soluble domains in rod outer segment plasma membranes and disks. J Neurochem (2007) 0.88
Absence of functional and structural abnormalities associated with expression of EGFP in the retina. Invest Ophthalmol Vis Sci (2004) 0.88
Gene therapy for Stargardt disease associated with ABCA4 gene. Adv Exp Med Biol (2014) 0.87
A review of therapeutic prospects of non-viral gene therapy in the retinal pigment epithelium. Biomaterials (2013) 0.85
Nonviral ocular gene therapy: assessment and future directions. Curr Opin Mol Ther (2008) 0.85
Differential developmental deficits in retinal function in the absence of either protein tyrosine sulfotransferase-1 or -2. PLoS One (2012) 0.83
Persistence of non-viral vector mediated RPE65 expression: case for viability as a gene transfer therapy for RPE-based diseases. J Control Release (2013) 0.83
RDS in cones does not interact with the beta subunit of the cyclic nucleotide gated channel. Adv Exp Med Biol (2010) 0.82
Mouse models of human retinal disease caused by expression of mutant rhodopsin. A valuable tool for the assessment of novel gene therapies. Adv Exp Med Biol (2003) 0.81
Annexin A2 interactions with Rab14 in alveolar type II cells. J Biol Chem (2008) 0.81
A perspective on the role of the extracellular matrix in progressive retinal degenerative disorders. Invest Ophthalmol Vis Sci (2013) 0.80
Fibulin 2, a tyrosine O-sulfated protein, is up-regulated following retinal detachment. J Biol Chem (2014) 0.80
AAV and compacted DNA nanoparticles for the treatment of retinal disorders: challenges and future prospects. Invest Ophthalmol Vis Sci (2011) 0.80
Synthesis and characterization of glycol chitosan DNA nanoparticles for retinal gene delivery. ChemMedChem (2013) 0.80
A 350 bp region of the proximal promoter of Rds drives cell-type specific gene expression. Exp Eye Res (2010) 0.79
Episomal maintenance of S/MAR-containing non-viral vectors for RPE-based diseases. Adv Exp Med Biol (2014) 0.79
Focus on molecules: RDS. Exp Eye Res (2009) 0.78
Gene therapy in the Retinal Degeneration Slow model of retinitis pigmentosa. Adv Exp Med Biol (2010) 0.78
The function of oligomerization-incompetent RDS in rods. Adv Exp Med Biol (2010) 0.78
Structural characterization of the second intra-discal loop of the photoreceptor tetraspanin RDS. FEBS J (2012) 0.77
Mislocalization of oligomerization-incompetent RDS is associated with mislocalization of cone opsins and cone transducin. Adv Exp Med Biol (2012) 0.77
Transgenic animal studies of human retinal disease caused by mutations in peripherin/rds. Adv Exp Med Biol (2006) 0.76
In vitro analysis of ribozyme-mediated knockdown of an ADRP associated rhodopsin mutation. Adv Exp Med Biol (2008) 0.76
Overexpression of retinal degeneration slow (RDS) protein adversely affects rods in the rd7 model of enhanced S-cone syndrome. PLoS One (2013) 0.75
Overexpression of ROM-1 in the cone-dominant retina. Adv Exp Med Biol (2012) 0.75
Light/dark translocation of alphatransducin in mouse photoreceptor cells expressing G90D mutant opsin. Adv Exp Med Biol (2006) 0.75
Electrophysiological characterization of rod and cone responses in the baboon nonhuman primate model. Adv Exp Med Biol (2014) 0.75
Retinal degenerations: genetics, mechanisms, and therapies. J Ophthalmol (2011) 0.75