A common mechanism of PLP/DM20 misfolding causes cysteine-mediated endoplasmic reticulum retention in oligodendrocytes and Pelizaeus-Merzbacher disease.

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Published in Proc Natl Acad Sci U S A on October 25, 2007

Authors

Ajit-Singh Dhaunchak1, Klaus-Armin Nave

Author Affiliations

1: Department of Neurogenetics, Max Planck Institute of Experimental Medicine, D-37075 Göttingen, Germany.

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