ADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly.

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Published in J Biol Chem on August 31, 2011

Authors

Masahiro Saito1, Misaki Kurokawa, Masahito Oda, Masamitsu Oshima, Ko Tsutsui, Kazutaka Kosaka, Kazuhisa Nakao, Miho Ogawa, Ri-ichiroh Manabe, Naoto Suda, Ganburged Ganjargal, Yasunobu Hada, Toshihide Noguchi, Toshio Teranaka, Kiyotoshi Sekiguchi, Toshiyuki Yoneda, Takashi Tsuji

Author Affiliations

1: Department of Biological Science and Technology, Faculty of Industrial Science, Tokyo University of Science, Noda, Chiba 278-8510, Japan. mssaito@rs.noda.tus.ac.jp

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