Published in Acta Neuropathol on January 01, 1987
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A rapid and efficient method to enrich SAF-protein from scrapie brains of hamsters. Biosci Rep (1984) 1.94
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Creutzfeldt-Jakob disease in a young adult with idiopathic hypopituitarism. Possible relation to the administration of cadaveric human growth hormone. N Engl J Med (1985) 1.92
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Characterization of antisera against scrapie-associated fibrils (SAF) from affected hamster and cross-reactivity with SAF from scrapie-affected mice and from patients with Creutzfeldt-Jakob disease. J Gen Virol (1985) 1.38
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Some speculations about prions, amyloid, and Alzheimer's disease. N Engl J Med (1984) 1.35
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Cloning of a gene whose expression is increased in scrapie and in senile plaques in human brain. Science (1985) 1.13
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Eight prion strains have PrP(Sc) molecules with different conformations. Nat Med (1998) 9.01
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Scrapie prions aggregate to form amyloid-like birefringent rods. Cell (1983) 7.92
Identification of a protein that purifies with the scrapie prion. Science (1982) 7.00
A protease-resistant protein is a structural component of the scrapie prion. Cell (1983) 6.72
Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science (1996) 6.71
Purification and structural studies of a major scrapie prion protein. Cell (1984) 5.98
Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein. Cell (1995) 5.16
Scrapie prion protein contains a phosphatidylinositol glycolipid. Cell (1987) 5.12
Formic acid pretreatment enhances immunostaining of cerebral and systemic amyloids. Lab Invest (1987) 4.98
Scrapie and cellular PrP isoforms are encoded by the same chromosomal gene. Cell (1986) 4.82
Transgenic mice expressing hamster prion protein produce species-specific scrapie infectivity and amyloid plaques. Cell (1989) 4.73
Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome. Nature (1989) 4.69
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Measurement of the scrapie agent using an incubation time interval assay. Ann Neurol (1982) 3.68
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Structural studies of the scrapie prion protein using mass spectrometry and amino acid sequencing. Biochemistry (1993) 3.54
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Complete genomic sequence and analysis of the prion protein gene region from three mammalian species. Genome Res (1998) 3.44
Structural clues to prion replication. Science (1994) 3.43
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Solution structure of a 142-residue recombinant prion protein corresponding to the infectious fragment of the scrapie isoform. Proc Natl Acad Sci U S A (1997) 3.42
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